Caught between pity, explicit bias, and discrimination: a qualitative study on the impact of stigma on the quality of life of persons living with sickle cell disease in three African countries.

Africa Cameroon Discrimination Explicit bias Ghana Pity Quality of life Sickle cell disease Stigma Tanzania

Journal

Quality of life research : an international journal of quality of life aspects of treatment, care and rehabilitation
ISSN: 1573-2649
Titre abrégé: Qual Life Res
Pays: Netherlands
ID NLM: 9210257

Informations de publication

Date de publication:
27 Oct 2023
Historique:
accepted: 28 09 2023
medline: 27 10 2023
pubmed: 27 10 2023
entrez: 27 10 2023
Statut: aheadofprint

Résumé

Sickle cell disease (SCD) is an inherited blood disorder characterized by unpredictable episodes of acute pain and numerous health complications. Individuals with SCD often face stigma from the public, including perceptions that they are lazy or weak tending to exaggerate their pain crisis, which can profoundly impact their quality of life (QoL). In a qualitative phenomenological study conducted in Cameroon, Ghana, and Tanzania, we explored stakeholders' perceptions of SCD-related stigma using three analytical frameworks: Bronfenbrenner's Ecological Systems Theory; The Health Stigma and Discriminatory Framework; and A Public Health Framework for Reducing Stigma. The study reveals that SCD-related stigma is marked by prejudice, negative labelling and social discrimination, with derogatory terms such as sickler, ogbanje (one who comes and goes), sika besa (money will finish), ene mewu (I can die today, I can die tomorrow), vampire (one who consumes human blood), and Efiewura (landlord-of the hospital), commonly used to refer to individuals living with SCD. Drivers of stigma include frequent crises and hospitalizations, distinct physical features of individuals living with SCD, cultural misconceptions about SCD and its association with early mortality. Proposed strategies for mitigating stigma include public health education campaigns about SCD, integrating SCD into school curricula, healthcare worker training and community engagement. The results highlight the importance of challenging stigmatizing narratives on SCD and recognizing that stigmatization represents a social injustice that significantly diminishes the QoL of individuals living with SCD.

Identifiants

pubmed: 37889387
doi: 10.1007/s11136-023-03533-8
pii: 10.1007/s11136-023-03533-8
doi:

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Subventions

Organisme : NHGRI NIH HHS
ID : U01HG007459
Pays : United States
Organisme : NHLBI NIH HHS
ID : U24HL135600
Pays : United States

Informations de copyright

© 2023. The Author(s).

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Auteurs

Nchangwi Syntia Munung (NS)

Division of Human Genetics, Faculty of Health Sciences, University of Cape Town, Cape Town, South Africa. munung.nchangwi@uct.ac.za.

Marsha Treadwell (M)

Department of Pediatrics/Division of Hematology, University of California San Francisco, Oakland, CA, USA.

Karen Kengne Kamga (KK)

Division of Human Genetics, Faculty of Health Sciences, University of Cape Town, Cape Town, South Africa.
University of Yaoundé 1, Yaoundé, Cameroon.

Jemima Dennis-Antwi (J)

Sickle Cell Foundation of Ghana, Accra, Ghana.

Kofi Anie (K)

London Northwest University Healthcare (NHS) Trust, Harrow, UK.
Imperial College London, London, UK.

Daima Bukini (D)

Muhimbili University of Health and Allied Sciences, Dar Es Salaam, Tanzania.

Julie Makani (J)

Muhimbili University of Health and Allied Sciences, Dar Es Salaam, Tanzania.

Ambroise Wonkam (A)

Division of Human Genetics, Faculty of Health Sciences, University of Cape Town, Cape Town, South Africa. awonkam1@jhmi.edu.
McKusick-Nathans Institute and Department of Genetic Medicine, Johns Hopkins University School of Medicine, Baltimore, USA. awonkam1@jhmi.edu.

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