Efficacy and safety of a SOD1-targeting artificial miRNA delivered by AAV9 in mice are impacted by miRNA scaffold selection.

ALS MT: oligonucleotides: therapies RNAi SOD1 adeno-associated virus gene therapy preclinical primary miRNA scaffold

Journal

Molecular therapy. Nucleic acids
ISSN: 2162-2531
Titre abrégé: Mol Ther Nucleic Acids
Pays: United States
ID NLM: 101581621

Informations de publication

Date de publication:
12 Dec 2023
Historique:
received: 27 09 2022
accepted: 12 10 2023
medline: 6 11 2023
pubmed: 6 11 2023
entrez: 6 11 2023
Statut: epublish

Résumé

Toxic gain-of-function mutations in superoxide dismutase 1 (SOD1) contribute to approximately 2%-3% of all amyotrophic lateral sclerosis (ALS) cases. Artificial microRNAs (amiRs) delivered by adeno-associated virus (AAV) have been proposed as a potential treatment option to silence SOD1 expression and mitigate disease progression. Primary microRNA (pri-miRNA) scaffolds are used in amiRs to shuttle a hairpin RNA into the endogenous miRNA pathway, but it is unclear whether different primary miRNA (pri-miRNA) scaffolds impact the potency and safety profile of the expressed amiR

Identifiants

pubmed: 37928442
doi: 10.1016/j.omtn.2023.102057
pii: S2162-2531(23)00275-5
pmc: PMC10622307
doi:

Types de publication

Journal Article

Langues

eng

Pagination

102057

Informations de copyright

© 2023 The Author(s).

Déclaration de conflit d'intérêts

M.H. is a paid advisor from Charter Preclinical Services. All other authors are paid employees at Biogen.

Références

Nat Biotechnol. 2009 Jan;27(1):59-65
pubmed: 19098898
Ann Neurol. 2016 Apr;79(4):687-700
pubmed: 26891182
N Engl J Med. 2020 Jul 9;383(2):151-158
pubmed: 32640133
Nature. 1993 Mar 4;362(6415):59-62
pubmed: 8446170
Gene Ther. 2021 Aug;28(7-8):456-468
pubmed: 33612827
Nucleic Acids Res. 2012 Jul;40(13):5864-75
pubmed: 22434881
BMC Bioinformatics. 2017 Mar 20;18(1):180
pubmed: 28320324
J Neural Transm Suppl. 1997;49:219-33
pubmed: 9266431
Nat Med. 2021 Nov;27(11):1982-1989
pubmed: 34663988
JCI Insight. 2018 Jun 21;3(12):
pubmed: 29925692
Nucleic Acids Res. 2019 Jan 8;47(D1):D766-D773
pubmed: 30357393
Methods. 2001 Dec;25(4):402-8
pubmed: 11846609
Mol Ther Nucleic Acids. 2016 Mar 22;5:e297
pubmed: 27003755
Nature. 2006 May 25;441(7092):537-41
pubmed: 16724069
J Neurol Neurosurg Psychiatry. 2016 Jan;87(1):12-20
pubmed: 26296871
Nucleic Acids Res. 2019 Jan 8;47(D1):D155-D162
pubmed: 30423142
Sci Transl Med. 2020 Nov 11;12(569):
pubmed: 33177182
Muscle Nerve. 2014 Dec;50(6):943-9
pubmed: 24619579
Mol Ther. 2020 Feb 5;28(2):422-430
pubmed: 31843447
Genetics. 2017 Feb;205(2):707-723
pubmed: 27974499
J Clin Invest. 2015 Feb;125(2):870-80
pubmed: 25607839
Osteoarthr Cartil Open. 2021 Jun 10;3(3):100189
pubmed: 36474808
Aging Cell. 2009 Jun;8(3):277-87
pubmed: 19627267
Genome Biol. 2009;10(3):R25
pubmed: 19261174
Mayo Clin Proc. 2018 Nov;93(11):1617-1628
pubmed: 30401437
Methods Mol Biol. 2016;1415:245-62
pubmed: 27115637
Proc Natl Acad Sci U S A. 2008 Apr 15;105(15):5868-73
pubmed: 18398004
Mol Ther Nucleic Acids. 2017 Jun 16;7:324-334
pubmed: 28624208
Wiley Interdiscip Rev RNA. 2021 Jul;12(4):e1640
pubmed: 33386705
Genome Biol. 2014;15(12):550
pubmed: 25516281
Neuron. 2020 Dec 9;108(5):822-842
pubmed: 32931756
Hum Gene Ther. 2018 Mar;29(3):285-298
pubmed: 29378426
Hum Gene Ther. 2022 Jul;33(13-14):740-756
pubmed: 35331006
Cell Rep. 2019 Jan 8;26(2):447-459.e4
pubmed: 30625327
Nucleic Acids Res. 2020 Jan 8;48(D1):D682-D688
pubmed: 31691826
Hum Gene Ther. 2020 Aug;31(15-16):808-818
pubmed: 32845779
Biochim Biophys Acta. 2016 Apr;1859(4):639-49
pubmed: 26921501
BMC Bioinformatics. 2011 Aug 04;12:323
pubmed: 21816040
Mol Ther. 2014 Apr;22(4):692-701
pubmed: 24352214
J Neurol Sci. 2015;353(1-2):122-9
pubmed: 25958264
J Clin Invest. 2018 Aug 1;128(8):3558-3567
pubmed: 30010620
Mol Ther. 2009 Jan;17(1):169-75
pubmed: 19002161
Mol Cell. 2015 Oct 1;60(1):131-45
pubmed: 26412306
PLoS One. 2012;7(7):e40998
pubmed: 22815892
Hum Mol Genet. 2001 Sep 15;10(19):2013-23
pubmed: 11590119
Hum Mol Genet. 2014 Feb 1;23(3):668-81
pubmed: 24108104
Gene. 2013 Sep 25;527(2):624-9
pubmed: 23856130
J Neurosci. 1998 May 1;18(9):3241-50
pubmed: 9547233
Stem Cell Reports. 2017 Oct 10;9(4):1221-1233
pubmed: 28966121
N Engl J Med. 2020 Jul 9;383(2):109-119
pubmed: 32640130
Nucleic Acids Res. 2016 Jan 4;44(D1):D184-9
pubmed: 26673694
Mol Ther Methods Clin Dev. 2022 Mar 28;25:264-277
pubmed: 35505662
Neuroscience. 2017 Dec 4;365:192-205
pubmed: 29024785
Sci Rep. 2017 Sep 8;7(1):10943
pubmed: 28887500
Mol Cell. 2014 Dec 18;56(6):796-807
pubmed: 25435137

Auteurs

Shukkwan K Chen (SK)

Biogen, Cambridge, MA, USA.

Zachary C E Hawley (ZCE)

Biogen, Cambridge, MA, USA.

Maria I Zavodszky (MI)

Biogen, Cambridge, MA, USA.

Sam Hana (S)

Biogen, Cambridge, MA, USA.

Daniel Ferretti (D)

Biogen, Cambridge, MA, USA.

Branka Grubor (B)

Biogen, Cambridge, MA, USA.

Michael Hawes (M)

Charter Preclinical Services, Hudson, MA, USA.

Shanqin Xu (S)

Biogen, Cambridge, MA, USA.

Stefan Hamann (S)

Biogen, Cambridge, MA, USA.

Galina Marsh (G)

Biogen, Cambridge, MA, USA.

Patrick Cullen (P)

Biogen, Cambridge, MA, USA.

Ravi Challa (R)

Biogen, Cambridge, MA, USA.

Thomas M Carlile (TM)

Biogen, Cambridge, MA, USA.

Hang Zhang (H)

Biogen, Cambridge, MA, USA.

Wan-Hung Lee (WH)

Biogen, Cambridge, MA, USA.

Andrea Peralta (A)

Biogen, Cambridge, MA, USA.

Pete Clarner (P)

Biogen, Cambridge, MA, USA.

Cong Wei (C)

Biogen, Cambridge, MA, USA.

Kathryn Koszka (K)

Biogen, Cambridge, MA, USA.

Feng Gao (F)

Biogen, Cambridge, MA, USA.

Shih-Ching Lo (SC)

Biogen, Cambridge, MA, USA.

Classifications MeSH