Identification of potential disease-associated variants in idiopathic generalized epilepsy using targeted sequencing.


Journal

Journal of human genetics
ISSN: 1435-232X
Titre abrégé: J Hum Genet
Pays: England
ID NLM: 9808008

Informations de publication

Date de publication:
22 Nov 2023
Historique:
received: 31 08 2023
accepted: 07 11 2023
revised: 28 10 2023
medline: 23 11 2023
pubmed: 23 11 2023
entrez: 22 11 2023
Statut: aheadofprint

Résumé

Many questions remain regarding the genetics of idiopathic generalized epilepsy (IGE), a subset of genetic generalized epilepsy (GGE). We aimed to identify the candidate coding variants of epilepsy panel genes in a cohort of affected individuals, using variant frequency information from a control cohort of the same region. We performed whole-exome sequencing analysis of 121 individuals and 10 affected relatives, focusing on variants of 950 candidate genes associated with epilepsy according to the Genes4Epilepsy curated panel. We identified 168 candidate variants (CVs) in 137 of 950 candidate genes in 88 of 121 affected individuals with IGE, of which 61 were novel variants. Notably, we identified five CVs in known GGE-associated genes (CHD2, GABRA1, RORB, SCN1A, and SCN1B) in five individuals and CVs shared by affected individuals in each of four family cases for other epilepsy candidate genes. The results of this study demonstrate that IGE is a disease with high heterogeneity and provide IGE-associated CVs whose pathogenicity should be proven by future studies, including advanced functional analysis. The low detection rate of CVs in the GGE-associated genes (4.1%) in this study suggests the current incompleteness of the Genes4Epilepsy panel for the diagnosis of IGE in clinical practice.

Identifiants

pubmed: 37993639
doi: 10.1038/s10038-023-01208-3
pii: 10.1038/s10038-023-01208-3
doi:

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Informations de copyright

© 2023. The Author(s), under exclusive licence to The Japan Society of Human Genetics.

Références

Jallon P, Latour P. Epidemiology of idiopathic generalized epilepsies. Epilepsia. 2005;46:10–4. https://doi.org/10.1111/j.1528-1167.2005.00309.x
doi: 10.1111/j.1528-1167.2005.00309.x pubmed: 16302871
Hirsch E, French J, Scheffer IE, Bogacz A, Alsaadi T, Sperling MR, et al. ILAE definition of the idiopathic generalized epilepsy syndromes: position statement by the ILAE task force on nosology and definitions. Epilepsia 2022;63:1475–99. https://doi.org/10.1111/epi.17236
doi: 10.1111/epi.17236 pubmed: 35503716
Sadleir LG, Vears D, Regan B, Redshaw N, Bleasel A, Scheffer IE. Family studies of individuals with eyelid myoclonia with absences. Epilepsia. 2012;53:2141–8. https://doi.org/10.1111/j.1528-1167.2012.03692.x
doi: 10.1111/j.1528-1167.2012.03692.x pubmed: 23205932
Zhang YH, Burgess R, Malone JP, Glubb GC, Helbig KL, Vadlamudi L, et al. Genetic epilepsy with febrile seizures plus: Refining the spectrum. Neurology. 2017;89:1210–9. https://doi.org/10.1212/WNL.0000000000004384
doi: 10.1212/WNL.0000000000004384 pubmed: 28842445
Mullen SA, Berkovic SF, ILAE Genetics Commission, Berkovic SF, Lowenstein DH, Kato M, et al. Genetic generalized epilepsies. Epilepsia. 2018;59:1148–53. https://doi.org/10.1111/epi.14042
doi: 10.1111/epi.14042 pubmed: 29741207
Hempelmann A, Taylor KP, Heils A, Lorenz S, Prud’Homme JF, Nabbout R, et al. Exploration of the genetic architecture of idiopathic generalized epilepsies. Epilepsia. 2006;47:1682–90. https://doi.org/10.1111/j.1528-1167.2006.00677.x
doi: 10.1111/j.1528-1167.2006.00677.x pubmed: 17054691
Marini C, Scheffer IE, Crossland KM, Grinton BE, Phillips FL, McMahon JM, et al. Genetic architecture of idiopathic generalized epilepsy: clinical genetic analysis of 55 multiplex families. Epilepsia. 2004;45:467–78. https://doi.org/10.1111/j.0013-9580.2004.46803.x
doi: 10.1111/j.0013-9580.2004.46803.x pubmed: 15101828
Delgado-Escueta AV, Koeleman BP, Bailey JN, Medina MT, Durón RM. The quest for juvenile myoclonic epilepsy genes. Epilepsy Behav. 2013;28:S52–7. https://doi.org/10.1016/j.yebeh.2012.06.033
doi: 10.1016/j.yebeh.2012.06.033 pubmed: 23756480
Greenberg DA, Durner M, Delgado-Escueta AV. Evidence for multiple gene loci in the expression of the common generalized epilepsies. Neurology 1992;42:56–62.
pubmed: 1574177
Qaiser F, Yuen RK, Andrade DM. Genetics of epileptic networks: From focal to generalized genetic epilepsies. Curr Neurol Neurosci Rep. 2020;20:46 https://doi.org/10.1007/s11910-020-01059-x
doi: 10.1007/s11910-020-01059-x pubmed: 32789700
Epi25 Collaborative. Ultra-rare genetic variation in the epilepsies: a whole-exome sequencing study of 17,606 individuals. Am J Hum Genet. 2019;105:267–82. https://doi.org/10.1016/j.ajhg.2019.05.020
doi: 10.1016/j.ajhg.2019.05.020
Johannesen K, Marini C, Pfeffer S, Møller RS, Dorn T, Niturad CE, et al. Phenotypic spectrum of GABRA1: From generalized epilepsies to severe epileptic encephalopathies. Neurology. 2016;87:1140–51. https://doi.org/10.1212/WNL.0000000000003087
doi: 10.1212/WNL.0000000000003087 pubmed: 27521439
Nicita F, De Liso P, Danti FR, Papetti L, Ursitti F, Castronovo A, et al. The genetics of monogenic idiopathic epilepsies and epileptic encephalopathies. Seizure. 2012;21:3–11. https://doi.org/10.1016/j.seizure.2011.08.007
doi: 10.1016/j.seizure.2011.08.007 pubmed: 21917483
Koko M, Motelow JE, Stanley KE, Bobbili DR, Dhindsa RS, May P, et al. Association of ultra‐rare coding variants with genetic generalized epilepsy: A case–control whole exome sequencing study. Epilepsia. 2022;63:723–35. https://doi.org/10.1111/epi.17166
doi: 10.1111/epi.17166 pubmed: 35032048 pmcid: 8891088
Stosser MB, Lindy AS, Butler E, Retterer K, Piccirillo-Stosser CM, Richard G, et al. High frequency of mosaic pathogenic variants in genes causing epilepsy-related neurodevelopmental disorders. Genet Med. 2018;20:403–10. https://doi.org/10.1038/gim.2017.114
doi: 10.1038/gim.2017.114 pubmed: 28837158
International League Against Epilepsy Consortium on Complex Epilepsies. GWAS meta-analysis of over 29,000 people with epilepsy identifies 26 risk loci and subtype-specific genetic architecture. Nat Genet. 2023;55:1471–82. https://doi.org/10.1038/s41588-023-01485-w
International League Against Epilepsy Consortium on Complex Epilepsies. Genome-wide mega-analysis identifies 16 loci and highlights diverse biological mechanisms in the common epilepsies. Nat Commun. 2018;9:5269 https://doi.org/10.1038/s41467-018-07524-z
doi: 10.1038/s41467-018-07524-z
Lee CG, Lee J, Lee M. Multi-gene panel testing in Korean patients with common genetic generalized epilepsy syndromes. PLoS One. 2018;13:e0199321 https://doi.org/10.1371/journal.pone.0199321
doi: 10.1371/journal.pone.0199321 pubmed: 29924869 pmcid: 6010271
May P, Girard S, Harrer M, Bobbili DR, Schubert J, Wolking S, et al. Rare coding variants in genes encoding GABAA receptors in genetic generalised epilepsies: an exome-based case-control study. Lancet Neurol. 2018;17:699–708. https://doi.org/10.1016/S1474-4422(18)30215-1
doi: 10.1016/S1474-4422(18)30215-1 pubmed: 30033060
Allen AS, Bellows ST, Berkovic SF, Bridgers J, Burgess R, Cavalleri G, et al. Ultra-rare genetic variation in common epilepsies: a case-control sequencing study. Lancet Neurol. 2017;16:135–43. https://doi.org/10.1016/S1474-4422(16)30359-3
doi: 10.1016/S1474-4422(16)30359-3
Durner M, Pal D, Greenberg D. Genetics of juvenile myoclonic epilepsy: faulty components and faulty wiring? Adv Neurol. 2005;95:245–54.
pubmed: 15508927
Van der Auwera GA, Carneiro MO, Hartl C, Poplin R, Del Angel G, Levy‐Moonshine A, et al. From FastQ data to high‐confidence variant calls: the genome analysis toolkit best practices pipeline. Curr Protoc Bioinforma. 2013;43:11–0. https://doi.org/10.1002/0471250953.bi1110s43
doi: 10.1002/0471250953.bi1110s43
Li H Aligning sequence reads, clone sequences and assembly contigs with BWA-MEM. arXiv preprint arXiv:1303.3997. (2013). https://doi.org/10.48550/arXiv.1303.3997
Okonechnikov K, Conesa A, García-Alcalde F. Qualimap 2: advanced multi-sample quality control for high-throughput sequencing data. Bioinformatics. 2016;32:292–4. https://doi.org/10.1093/bioinformatics/btv566
doi: 10.1093/bioinformatics/btv566 pubmed: 26428292
Chang CC, Chow CC, Tellier LC, Vattikuti S, Purcell SM, Lee JJ. Second-generation PLINK: rising to the challenge of larger and richer datasets. Gigascience. 2015;4:s13742–015. https://doi.org/10.1186/s13742-015-0047-8
doi: 10.1186/s13742-015-0047-8
Wang K, Li M, Hakonarson H. ANNOVAR: functional annotation of genetic variants from high-throughput sequencing data. Nucleic Acids Res. 2010;38:e164 https://doi.org/10.1093/nar/gkq603
doi: 10.1093/nar/gkq603 pubmed: 20601685 pmcid: 2938201
Richards S, Aziz N, Bale S, Bick D, Das S, Gastier-Foster J, et al. Standards and guidelines for the interpretation of sequence variants: a joint consensus recommendation of the American College of Medical Genetics and Genomics and the Association for Molecular Pathology. Genet Med. 2015;17:405–23 https://doi.org/10.1038/gim.2015.30
doi: 10.1038/gim.2015.30 pubmed: 25741868 pmcid: 4544753
Li Q, Wang K. InterVar: clinical interpretation of genetic variants by the 2015 ACMG-AMP guidelines. Am J Hum Genet. 2017;100:267–80. https://doi.org/10.1016/j.ajhg.2017.01.004
doi: 10.1016/j.ajhg.2017.01.004 pubmed: 28132688 pmcid: 5294755
Barbitoff YA, Khmelkova DN, Pomerantseva EA, Slepchenkov AV, Zubashenko NA, Mironova IV, et al. Expanding the Russian allele frequency reference via cross-laboratory data integration: Insights from 7,452 exome samples. MedRXiv. 2021.11.02.21265801. https://doi.org/10.1101/2021.11.02.21265801
Oliver KL, Scheffer IE, Bennett MF, Grinton BE, Bahlo M, Berkovic SF. Genes4Epilepsy: An epilepsy gene resource. Epilepsia. 2023;64:1368–75. https://doi.org/10.1111/epi.17547
doi: 10.1111/epi.17547 pubmed: 36808730
Pejaver V, Byrne AB, Feng BJ, Pagel KA, Mooney SD, Karchin R, et al. Calibration of computational tools for missense variant pathogenicity classification and ClinGen recommendations for PP3/BP4 criteria. Am J Hum Genet. 2022;109:2163–77. https://doi.org/10.1016/j.ajhg.2022.10.013
doi: 10.1016/j.ajhg.2022.10.013 pubmed: 36413997 pmcid: 9748256
Tian Y, Pesaran T, Chamberlin A, Fenwick RB, Li S, Gau CL, et al. REVEL and BayesDel outperform other in silico meta-predictors for clinical variant classification. Sci Rep. 2019;9:12752 https://doi.org/10.1038/s41598-019-49224-8
doi: 10.1038/s41598-019-49224-8 pubmed: 31484976 pmcid: 6726608
Karlsson M, Zhang C, Méar L, Zhong W, Digre A, Katona B, et al. A single–cell type transcriptomics map of human tissues. Sci Adv. 2021;7:eabh2169 https://doi.org/10.1126/sciadv.abh2169
doi: 10.1126/sciadv.abh2169 pubmed: 34321199 pmcid: 8318366
Biesecker LG, Shianna KV, Mullikin JC. Exome sequencing: the expert view. Genome Biol. 2011;12:1–3. https://doi.org/10.1186/gb-2011-12-9-128
doi: 10.1186/gb-2011-12-9-128
Tashkandi M, Baarma D, Tricco AC, Boelman C, Alkhater R, Minassian BA. EEG of asymptomatic first‐degree relatives of patients with juvenile myoclonic, childhood absence and rolandic epilepsy: a systematic review and meta‐analysis. Epileptic Disord. 2019;21:30–41. https://doi.org/10.1684/epd.2019.1024
doi: 10.1684/epd.2019.1024 pubmed: 30767897
Chowdhury FA, Woldman W, FitzGerald TH, Elwes RD, Nashef L, Terry JR, et al. Revealing a brain network endophenotype in families with idiopathic generalised epilepsy. PloS one. 2014;9:e110136 https://doi.org/10.1371/journal.pone.0110136
doi: 10.1371/journal.pone.0110136 pubmed: 25302690 pmcid: 4193864
Shen W, Pristov JB, Nobili P, Nikolić L. Can glial cells save neurons in epilepsy. Neural Regen Res. 2023;18:1417 https://doi.org/10.4103/1673-5374.360281
doi: 10.4103/1673-5374.360281 pubmed: 36571336
Knowles JK, Xu H, Soane C, Batra A, Saucedo T, Frost E, et al. Maladaptive myelination promotes generalized epilepsy progression. Nat Neurosci. 2022;25:596–606. https://doi.org/10.1038/s41593-022-01052-2
doi: 10.1038/s41593-022-01052-2 pubmed: 35501379 pmcid: 9076538
Tognatta R, Miller RH. Contribution of the oligodendrocyte lineage to CNS repair and neurodegenerative pathologies. Neuropharmacology. 2016;110:539–47. https://doi.org/10.1016/j.neuropharm.2016.04.026
doi: 10.1016/j.neuropharm.2016.04.026 pubmed: 27108096 pmcid: 5512544
Larson VA, Mironova Y, Vanderpool KG, Waisman A, Rash JE, Agarwal A, et al. Oligodendrocytes control potassium accumulation in white matter and seizure susceptibility. Elife. 2018;7:e34829 https://doi.org/10.7554/eLife.34829
doi: 10.7554/eLife.34829 pubmed: 29596047 pmcid: 5903864
Xin W, Mironova YA, Shen H, Marino RA, Waisman A, Lamers WH, et al. Oligodendrocytes support neuronal glutamatergic transmission via expression of glutamine synthetase. Cell Rep. 2019;27:2262–71. https://doi.org/10.1016/j.celrep.2019.04.094
doi: 10.1016/j.celrep.2019.04.094 pubmed: 31116973 pmcid: 6544175
Patel DC, Tewari BP, Chaunsali L, Sontheimer H. Neuron–glia interactions in the pathophysiology of epilepsy. Nat Rev Neurosci. 2019;20:282–97. https://doi.org/10.1038/s41583-019-0126-4
doi: 10.1038/s41583-019-0126-4 pubmed: 30792501 pmcid: 8558781
Timechko EE, Shilkina OS, Oreshkova NV, Kobanenko VO, Osipova EA, Shnayder NA, et al. Whole-exome sequencing of patients with juvenile myoclonic epilepsy. Epilepsy Paroxysmal Cond. 2022;14:254–66. https://doi.org/10.17749/2077-8333/epi.par.con.2022.119
doi: 10.17749/2077-8333/epi.par.con.2022.119

Auteurs

Regina Gamirova (R)

Department of Bioinformatics and Genomics, Graduate School of Advanced Preventive Medical Sciences, Kanazawa University, Kanazawa, Japan.

Elena Shagimardanova (E)

Regulatory Genomics Research Cen-ter, Kazan Federal University, Kazan, Russia.

Takehiro Sato (T)

Department of Bioinformatics and Genomics, Graduate School of Advanced Preventive Medical Sciences, Kanazawa University, Kanazawa, Japan.
Department of Human Biology and Anatomy, Graduate School of Medicine, University of the Ryukyus, Nishihara, Japan.

Takayuki Kannon (T)

Department of Bioinformatics and Genomics, Graduate School of Advanced Preventive Medical Sciences, Kanazawa University, Kanazawa, Japan.
Department of Biomedical Data Science, Fujita Health University School of Medicine, Toyoake, Japan.

Rimma Gamirova (R)

Department of Neurology with Courses in Psychiatry, Clinical Psychology and Medical Genetics, Kazan Federal University, Kazan, Russia. r-gamirov@mail.ru.
Laboratory of Neurocognitive Investigations, Kazan Federal University, Kazan, Russia. r-gamirov@mail.ru.

Atsushi Tajima (A)

Department of Bioinformatics and Genomics, Graduate School of Advanced Preventive Medical Sciences, Kanazawa University, Kanazawa, Japan. atajima@med.kanazawa-u.ac.jp.

Classifications MeSH