Genetic Testing in Hereditary Pituitary Tumors.

AIP Carney complex GPR101 Genetic testing IGSF1 Lynch syndrome MEN1 PitNETs Pituitary adenomas XLAG

Journal

Archives of medical research
ISSN: 1873-5487
Titre abrégé: Arch Med Res
Pays: United States
ID NLM: 9312706

Informations de publication

Date de publication:
24 Nov 2023
Historique:
received: 11 08 2023
revised: 26 10 2023
accepted: 13 11 2023
medline: 26 11 2023
pubmed: 26 11 2023
entrez: 25 11 2023
Statut: aheadofprint

Résumé

Genetic testing is becoming part of mainstream endocrinology. An increasing number of rare and not-so-rare endocrine diseases have an identifiable genetic cause, either at the germline or at the somatic level. Here we summerise germline genetic alterations in patients with pituitary neuroendocrine tumors (pituitary adenomas). These may be disorders with isolated pituitary tumors, such as X-linked acrogigantism, or AIP-related pituitary tumors, or as part of syndromic diseases, such as multiple endocrine neoplasia type 1 or Carney complex. In some cases, this could be relevant for treatment choices and follow-up, as well as for family members, as cascade screening leads to early identification of affected relatives and improved clinical outcomes.

Identifiants

pubmed: 38007383
pii: S0188-4409(23)00158-3
doi: 10.1016/j.arcmed.2023.102920
pii:
doi:

Types de publication

Journal Article Review

Langues

eng

Sous-ensembles de citation

IM

Pagination

102920

Informations de copyright

Copyright © 2023 Instituto Mexicano del Seguro Social (IMSS). Published by Elsevier Inc. All rights reserved.

Auteurs

Gamze Akkuş (G)

Centre for Endocrinology, William Harvey Research Institute, Barts and the London School of Medicine and Dentistry, Queen Mary University of London, London, UK.

Márta Korbonits (M)

Centre for Endocrinology, William Harvey Research Institute, Barts and the London School of Medicine and Dentistry, Queen Mary University of London, London, UK. Electronic address: m.korbonits@qmul.ac.uk.

Classifications MeSH