Surveillance of multiple congenital anomalies; searching for new associations.


Journal

European journal of human genetics : EJHG
ISSN: 1476-5438
Titre abrégé: Eur J Hum Genet
Pays: England
ID NLM: 9302235

Informations de publication

Date de publication:
05 Dec 2023
Historique:
received: 08 02 2023
accepted: 16 11 2023
revised: 09 10 2023
medline: 6 12 2023
pubmed: 6 12 2023
entrez: 5 12 2023
Statut: aheadofprint

Résumé

Many human teratogens are associated with a spectrum of congenital anomalies rather than a single defect, and therefore the identification of congenital anomalies occurring together more frequently than expected may improve the detection of teratogens. Thirty-two EUROCAT congenital anomaly registries covering 6,599,765 births provided 123,566 cases with one or more major congenital anomalies (excluding chromosomal and genetic syndromes) for the birth years 2008-2016. The EUROCAT multiple congenital anomaly algorithm identified 8804 cases with two or more major congenital anomalies in different organ systems, that were not recognized as part of a syndrome or sequence. For each pair of anomalies, the odds of a case having both anomalies relative to having only one anomaly was calculated and the p value was estimated using a two-sided Fisher's exact test. The Benjamini-Hochberg procedure adjusted p values to control the false discovery rate and pairs of anomalies with adjusted p values < 0.05 were identified. A total of 1386 combinations of two anomalies were analyzed. Out of the 31 statistically significant positive associations identified, 20 were found to be known associations or sequences already described in the literature and 11 were considered "potential new associations" by the EUROCAT Coding and Classification Committee. After a review of the literature and a detailed examination of the individual cases with the anomaly pairs, six pairs remained classified as new associations. In summary, systematically searching for congenital anomalies occurring together more frequently than expected using the EUROCAT database is worthwhile and has identified six new associations that merit further investigation.

Identifiants

pubmed: 38052905
doi: 10.1038/s41431-023-01502-w
pii: 10.1038/s41431-023-01502-w
doi:

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Informations de copyright

© 2023. The Author(s).

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Auteurs

Joan K Morris (JK)

Population Health Research Institute, St George's, University of London, London, UK. jmorris@sgul.ac.uk.

Jorieke E H Bergman (JEH)

Department of Genetics, University Medical Center Groningen, University of Groningen, Groningen, The Netherlands.

Ingeborg Barisic (I)

Children's Hospital Zagreb, Centre of Excellence for Reproductive and Regenerative Medicine, Medical School University of Zagreb, Zagreb, Croatia.

Diana Wellesley (D)

Clinical Genetics, University of Southampton and Wessex Clinical Genetics Service, Princess Anne Hospital, Southampton, UK.

David Tucker (D)

Congenital Anomaly Register & Information Service for Wales (CARIS) Public Health Knowledge and Research, Public Health Wales, Swansea, Wales, UK.

Elizabeth Limb (E)

Population Health Research Institute, St George's, University of London, London, UK.

Marie-Claude Addor (MC)

Department of Woman-Mother-Child, University Medical Center CHUV, Lausanne, Switzerland.

Clara Cavero-Carbonell (C)

Rare Diseases Research Unit, Foundation for the Promotion of Health and Biomedical Research in the Valencian Region, Valencia, Spain.

Carlos Matias Dias (C)

Epidemiology Department, National Institute of Health Doutor Ricardo Jorge, Lisboa, Portugal.

Elisabeth S Draper (ES)

Department of Population Health Sciences, Georg Davies Centre, University of Leicester, Leicester, UK.

Luis Javier Echevarría-González-de-Garibay (LJ)

Department of Health of the Basque Government, Vitoria-Gasteiz, Spain.

Miriam Gatt (M)

Malta Congenital Anomalies Registry, Directorate for Health Information and Research, Guardamangia, Malta.

Kari Klungsøyr (K)

Department of Global Public Health and Primary Care, University of Bergen, Bergen, Norway.
Division of Mental and Physical Health, Norwegian Institute of Public Health, Bergen, Norway.

Nathalie Lelong (N)

Université Paris Cité, CRESS, Équipe de recherche en épidémiologie obstétricale périnatale et pédiatrique (EPOPé), INSERM, INRA, Paris, France.

Karen Luyt (K)

South West Congenital Anomaly Register, Bristol Medical School, University of Bristol, Bristol, UK.

Anna Materna-Kiryluk (A)

Polish Registry of Congenital Malformations, Chair and Department of Medical Genetics, University of Medical Sciences, 61-701, Poznan, Poland.

Vera Nelen (V)

Provincial Institute for Hygiene, Antwerp, Belgium.

Amanda Neville (A)

Center for Clinical and Epidemiological Research, University of Ferrara, Ferrara, Italy.

Isabelle Perthus (I)

Auvergne Registry of Congenital Anomalies (CEMC-Auvergne), Department of Clinical Genetics, Centre de Référence des Maladies Rares, University Hospital of Clermont-Ferrand, Clermont-Ferrand, France.

Anna Pierini (A)

Unit of Epidemiology of Rare diseases and Congenital anomalies, Institute of Clinical Physiology, National Research Council, Pisa, Italy.

Hanitra Randrianaivo-Ranjatoelina (H)

Service de Génétique Médicale et d'oncogénétique, Registre des Malformations Congénitales, Saint Pierre, La Réunion, France.

Judith Rankin (J)

Population Health Sciences Institute, Faculty of Medical Sciences, Newcastle University, Newcastle upon Tyne, UK.

Anke Rissmann (A)

Malformation Monitoring Centre Saxony-Anhalt, Medical Faculty Otto-von-Guericke University-Magdeburg, Magdeburg, Germany.

Florence Rouget (F)

Brittany Registry of Congenital Anomalies, CHU Rennes, Univ Rennes, Inserm, EHESP, Irset (Institut de recherche en santé, environnement et travail) - UMR_S 1085, F-35000, Rennes, France.

Geraldine Sayers (G)

Health Intelligence, Research and Development Health Service Executive, Dublin, Ireland.

Wladimir Wertelecki (W)

OMNI-Net Ukraine Programs, Rivne, Ukraine.

Agnieszka Kinsner-Ovaskainen (A)

European Commission, Joint Research Centre, Ispra, Italy.

Ester Garne (E)

Department of Paediatrics and Adolescent Medicine, Lillebaelt Hospital, University Hospital of Southern Denmark, Kolding, Denmark.

Classifications MeSH