A randomized double-blind clinical trial on safety and efficacy of tauroursodeoxycholic acid (TUDCA) as add-on treatment in patients affected by amyotrophic lateral sclerosis (ALS): the statistical analysis plan of TUDCA-ALS trial.


Journal

Trials
ISSN: 1745-6215
Titre abrégé: Trials
Pays: England
ID NLM: 101263253

Informations de publication

Date de publication:
05 Dec 2023
Historique:
received: 23 07 2023
accepted: 22 08 2023
medline: 7 12 2023
pubmed: 6 12 2023
entrez: 5 12 2023
Statut: epublish

Résumé

Amyotrophic lateral sclerosis (ALS) is a highly debilitating neurodegenerative condition. Despite recent advancements in understanding the molecular mechanisms underlying ALS, there have been no significant improvements in therapeutic options for ALS patients in recent years. Currently, there is no cure for ALS, and the only approved treatment in Europe is riluzole, which has been shown to slow the disease progression and prolong survival by approximately 3 months. Recently, tauroursodeoxycholic acid (TUDCA) has emerged as a promising and effective treatment for neurodegenerative diseases due to its neuroprotective activities. The ongoing TUDCA-ALS study is a double-blinded, parallel arms, placebo-controlled, randomized multicenter phase III trial with the aim to assess the efficacy and safety of TUDCA as add-on therapy to riluzole in patients with ALS. The primary outcome measure is the treatment response defined as a minimum of 20% improvement in the ALS Functional Rating Scale-Revised (ALSFRS-R) slope during the randomized treatment period (18 months) compared to the lead-in period (3 months). Randomization will be stratified by country. Primary analysis will be conducted based on the intention-to-treat principle through an unadjusted logistic regression model. Patient recruitment commenced on February 22, 2019, and was closed on December 23, 2021. The database will be locked in September 2023. This paper provides a comprehensive description of the statistical analysis plan in order to ensure the reproducibility of the analysis and avoid selective reporting of outcomes and data-driven analysis. Sensitivity analyses have been included in the protocol to assess the impact of intercurrent events related to the coronavirus disease 2019. By focusing on clinically meaningful and robust outcomes, this trial aims to determine whether TUDCA can be effective in slowing the disease progression in patients with ALS. ClinicalTrials.gov NCT03800524 . Registered on January 11, 2019.

Sections du résumé

BACKGROUND BACKGROUND
Amyotrophic lateral sclerosis (ALS) is a highly debilitating neurodegenerative condition. Despite recent advancements in understanding the molecular mechanisms underlying ALS, there have been no significant improvements in therapeutic options for ALS patients in recent years. Currently, there is no cure for ALS, and the only approved treatment in Europe is riluzole, which has been shown to slow the disease progression and prolong survival by approximately 3 months. Recently, tauroursodeoxycholic acid (TUDCA) has emerged as a promising and effective treatment for neurodegenerative diseases due to its neuroprotective activities.
METHODS METHODS
The ongoing TUDCA-ALS study is a double-blinded, parallel arms, placebo-controlled, randomized multicenter phase III trial with the aim to assess the efficacy and safety of TUDCA as add-on therapy to riluzole in patients with ALS. The primary outcome measure is the treatment response defined as a minimum of 20% improvement in the ALS Functional Rating Scale-Revised (ALSFRS-R) slope during the randomized treatment period (18 months) compared to the lead-in period (3 months). Randomization will be stratified by country. Primary analysis will be conducted based on the intention-to-treat principle through an unadjusted logistic regression model. Patient recruitment commenced on February 22, 2019, and was closed on December 23, 2021. The database will be locked in September 2023.
DISCUSSION CONCLUSIONS
This paper provides a comprehensive description of the statistical analysis plan in order to ensure the reproducibility of the analysis and avoid selective reporting of outcomes and data-driven analysis. Sensitivity analyses have been included in the protocol to assess the impact of intercurrent events related to the coronavirus disease 2019. By focusing on clinically meaningful and robust outcomes, this trial aims to determine whether TUDCA can be effective in slowing the disease progression in patients with ALS.
TRIAL REGISTRATION BACKGROUND
ClinicalTrials.gov NCT03800524 . Registered on January 11, 2019.

Identifiants

pubmed: 38053196
doi: 10.1186/s13063-023-07638-w
pii: 10.1186/s13063-023-07638-w
pmc: PMC10696667
doi:

Substances chimiques

Riluzole 7LJ087RS6F
ursodoxicoltaurine 60EUX8MN5X
Neuroprotective Agents 0

Banques de données

ClinicalTrials.gov
['NCT03800524']

Types de publication

Randomized Controlled Trial Multicenter Study Clinical Trial, Phase III Journal Article

Langues

eng

Sous-ensembles de citation

IM

Pagination

792

Subventions

Organisme : Horizon 2020 Framework Programme
ID : 755094

Investigateurs

Paolo Tornese (P)
Antoniangela Cocco (A)
Michela Matteoli (M)
Eliana Lauranzano (E)
Maria Luisa Malosio (ML)
Chiara Adriana Elia (CA)
Adriano Chiò (A)
Umberto Manera (U)
Cristina Moglia (C)
Andrea Calvo (A)
Paolina Salamone (P)
Giuseppe Fuda (G)
Carlo Colosimo (C)
Cristina Spera (C)
Prabha Cristina Ranchicchio (PC)
Giuseppe Stipa (G)
Domenico Frondizi (D)
Christian Lunetta (C)
Valeria Sansone (V)
Claudia Tarlarini (C)
Francesca Gerardi (F)
Vincenzo Silani (V)
Alberto Doretti (A)
Eleonora Colombo (E)
Gianluca Demirtzidis (G)
Gioacchino Tedeschi (G)
Francesca Trojsi (F)
Carla Passaniti (C)
Stefania Ballestrero (S)
Johannes Dorst (J)
Ulrike Weiland (U)
Andrea Fromm (A)
Maximilian Wiesenfarth (M)
Katharina Kandler (K)
Simon Witzel (S)
Markus Otto (M)
Joachim Schuster (J)
Thomas Meyer (T)
André Maier (A)
Dagmar Kettemann (D)
Susanne Petri (S)
Lars Müschen (L)
Camilla Wohnrade (C)
Anastasia Sarikidi (A)
Alma Osmanovic (A)
Julian Grosskreutz (J)
Annekathrin Rödiger (A)
Robert Steinbach (R)
Benjamin Ilse (B)
Uta Smesny (U)
Robert Untucht (R)
René Günther (R)
Maximilian Vidovic (M)
Pamela Shaw (P)
Alexis Collins (A)
Helen Wollff (H)
Theresa Walsh (T)
Lee Tuddenham (L)
Mbombe Kazoka (M)
David White (D)
Stacy Young (S)
Benjamin Thompson (B)
Daniel Madarshahian (D)
Suresh K Chhetri (SK)
Amina Chaouch (A)
Carolyn A Young (CA)
Heike Arndt (H)
Coliver Hanemann (C)
Thomas Lambert (T)
Stephane Beltran (S)
Philippe Couratier (P)
Florence Esselin (F)
William Camu (W)
Elisa De La Cruz (E)
Gwendal Lemasson (G)
Pegah Masrori (P)
Sinead Maguire (S)
Liz Fogarty (L)
Toyosi Atoyebi (T)
Niamh Ní Obáin (NN)

Informations de copyright

© 2023. The Author(s).

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Auteurs

Flavia L Lombardo (FL)

National Centre for Disease Prevention and Health Promotion, Italian National Institute of Health, Rome, Italy. flavia.lombardo@iss.it.

Stefania Spila Alegiani (S)

National Center for Drug Research and Evaluation, Italian National Institute of Health, Rome, Italy.

Flavia Mayer (F)

National Center for Drug Research and Evaluation, Italian National Institute of Health, Rome, Italy.

Marta Cipriani (M)

Department of Statistical Sciences, Sapienza University of Rome, Rome, Italy.
Department of Neuroscience, Italian National Institute of Health, Rome, Italy.

Maria Lo Giudice (M)

Neurology Department, IRCCS Humanitas Research Hospital, Rozzano, Italy.

Albert Christian Ludolph (AC)

Neurology Department, University of Ulm, Ulm, Germany.
German Centre of Neurodegenerative Diseases, Site Ulm, Ulm, Germany.

Christopher J McDermott (CJ)

Department of Neuroscience, Sheffield Institute for Translational Neuroscience, University of Sheffield, Sheffield, UK.

Philippe Corcia (P)

Centre de Référence Maladie Rare (CRMR) SLA Et Les Autres Maladies du Neurone Moteur (FILSLAN), Tours, France.
CHU Bretonneau, Tours, France.
Federation des CRMR-SLA Tours-Limoges, LITORALS, Tours, France.
Faculté de Médecine, INSERM U1253, "iBrain," Université François-Rabelais de Tours, Tours, France.

Philip Van Damme (P)

Neurology Department, University Hospitals Leuven, Louvain, Belgium.
Neuroscience Department, KU Leuven, Louvain, Belgium.

Leonard H Van den Berg (LH)

Department of Neurology, UMC Utrecht Brain Center, University Medical Centre Utrecht, Utrecht, Netherlands.

Orla Hardiman (O)

Academic Unit of Neurology, Trinity Biomedical Sciences Institute, Dublin, Ireland.
Clinical Research Centre, Beaumont Hospital, Dublin, Ireland.

Gabriele Nicolini (G)

Medical Affairs, Bruschettini S.R.L, Genoa, Italy.

Nicola Vanacore (N)

National Centre for Disease Prevention and Health Promotion, Italian National Institute of Health, Rome, Italy.

Brian Dickie (B)

Motor Neurone Disease Association, Northampton, UK.

Alberto Albanese (A)

Neurology Department, IRCCS Humanitas Research Hospital, Rozzano, Italy.

Maria Puopolo (M)

Department of Neuroscience, Italian National Institute of Health, Rome, Italy.

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