Transient inhibition of 53BP1 increases the frequency of targeted integration in human hematopoietic stem and progenitor cells.


Journal

Nature communications
ISSN: 2041-1723
Titre abrégé: Nat Commun
Pays: England
ID NLM: 101528555

Informations de publication

Date de publication:
02 Jan 2024
Historique:
received: 23 02 2023
accepted: 08 11 2023
medline: 4 1 2024
pubmed: 4 1 2024
entrez: 3 1 2024
Statut: epublish

Résumé

Genome editing by homology directed repair (HDR) is leveraged to precisely modify the genome of therapeutically relevant hematopoietic stem and progenitor cells (HSPCs). Here, we present a new approach to increasing the frequency of HDR in human HSPCs by the delivery of an inhibitor of 53BP1 (named "i53") as a recombinant peptide. We show that the use of i53 peptide effectively increases the frequency of HDR-mediated genome editing at a variety of therapeutically relevant loci in HSPCs as well as other primary human cell types. We show that incorporating the use of i53 recombinant protein allows high frequencies of HDR while lowering the amounts of AAV6 needed by 8-fold. HDR edited HSPCs were capable of long-term and bi-lineage hematopoietic reconstitution in NSG mice, suggesting that i53 recombinant protein might be safely integrated into the standard CRISPR/AAV6-mediated genome editing protocol to gain greater numbers of edited cells for transplantation of clinically meaningful cell populations.

Identifiants

pubmed: 38169468
doi: 10.1038/s41467-023-43413-w
pii: 10.1038/s41467-023-43413-w
doi:

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Pagination

111

Informations de copyright

© 2024. The Author(s).

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Auteurs

Ron Baik (R)

Institute for Stem Cell Biology and Regenerative Medicine, Stanford University School of Medicine, Lorry I. Lokey Stem Cell Research Building, 265 Campus Drive, Stanford, CA, USA.
Department of Pediatrics, Stanford University School of Medicine, Stanford, CA, USA.
Molecular Biology Program, Sloan Kettering Institute, Memorial Sloan Kettering Cancer Center, New York, NY, USA.

M Kyle Cromer (MK)

Institute for Stem Cell Biology and Regenerative Medicine, Stanford University School of Medicine, Lorry I. Lokey Stem Cell Research Building, 265 Campus Drive, Stanford, CA, USA.
Department of Pediatrics, Stanford University School of Medicine, Stanford, CA, USA.

Steve E Glenn (SE)

Integrated DNA Technologies, Inc., Coralville, IA, USA.

Christopher A Vakulskas (CA)

Integrated DNA Technologies, Inc., Coralville, IA, USA.

Kay O Chmielewski (KO)

Institute for Transfusion Medicine and Gene Therapy, Medical Center - University of Freiburg, 79106, Freiburg, Germany.
Center for Chronic Immunodeficiency, University of Freiburg, 79106, Freiburg, Germany.
Ph.D. Program, Faculty of Biology, University of Freiburg, 79104, Freiburg, Germany.

Amanda M Dudek (AM)

Institute for Stem Cell Biology and Regenerative Medicine, Stanford University School of Medicine, Lorry I. Lokey Stem Cell Research Building, 265 Campus Drive, Stanford, CA, USA.
Department of Pediatrics, Stanford University School of Medicine, Stanford, CA, USA.

William N Feist (WN)

Institute for Stem Cell Biology and Regenerative Medicine, Stanford University School of Medicine, Lorry I. Lokey Stem Cell Research Building, 265 Campus Drive, Stanford, CA, USA.
Department of Pediatrics, Stanford University School of Medicine, Stanford, CA, USA.

Julia Klermund (J)

Institute for Transfusion Medicine and Gene Therapy, Medical Center - University of Freiburg, 79106, Freiburg, Germany.
Center for Chronic Immunodeficiency, University of Freiburg, 79106, Freiburg, Germany.

Suzette Shipp (S)

Institute for Stem Cell Biology and Regenerative Medicine, Stanford University School of Medicine, Lorry I. Lokey Stem Cell Research Building, 265 Campus Drive, Stanford, CA, USA.
Department of Pediatrics, Stanford University School of Medicine, Stanford, CA, USA.

Toni Cathomen (T)

Institute for Transfusion Medicine and Gene Therapy, Medical Center - University of Freiburg, 79106, Freiburg, Germany.
Center for Chronic Immunodeficiency, University of Freiburg, 79106, Freiburg, Germany.

Daniel P Dever (DP)

Institute for Stem Cell Biology and Regenerative Medicine, Stanford University School of Medicine, Lorry I. Lokey Stem Cell Research Building, 265 Campus Drive, Stanford, CA, USA.
Department of Pediatrics, Stanford University School of Medicine, Stanford, CA, USA.

Matthew H Porteus (MH)

Institute for Stem Cell Biology and Regenerative Medicine, Stanford University School of Medicine, Lorry I. Lokey Stem Cell Research Building, 265 Campus Drive, Stanford, CA, USA. mporteus@stanford.edu.
Department of Pediatrics, Stanford University School of Medicine, Stanford, CA, USA. mporteus@stanford.edu.

Classifications MeSH