Genomic and functional impact of Trp53 inactivation in JAK2V617F myeloproliferative neoplasms.


Journal

Blood cancer journal
ISSN: 2044-5385
Titre abrégé: Blood Cancer J
Pays: United States
ID NLM: 101568469

Informations de publication

Date de publication:
04 Jan 2024
Historique:
received: 29 06 2023
accepted: 08 12 2023
revised: 26 10 2023
medline: 5 1 2024
pubmed: 5 1 2024
entrez: 4 1 2024
Statut: epublish

Résumé

Classical myeloproliferative neoplasms (MPNs) are characterized by the proliferation of myeloid cells and the risk of transformation into myelofibrosis or acute myeloid leukemia (AML) and TP53 mutations in MPN patients are linked to AML. However, JAK2V617F has been reported to impact the TP53 response to DNA damage, suggesting potential overlapping role of TP53 inactivation in MPN. We established a mouse model showing that JAK2V617F/Vav-Cre/Trp53

Identifiants

pubmed: 38177095
doi: 10.1038/s41408-023-00969-6
pii: 10.1038/s41408-023-00969-6
doi:

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Pagination

1

Informations de copyright

© 2023. The Author(s).

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Auteurs

Panhong Gou (P)

Inserm UMR-S 1131, Hôpital Saint-Louis, Paris, France.
Université de Paris Cité, Paris, France.

Duanya Liu (D)

Inserm UMR-S 1131, Hôpital Saint-Louis, Paris, France.
Université de Paris Cité, Paris, France.

Saravanan Ganesan (S)

Inserm UMR-S 1131, Hôpital Saint-Louis, Paris, France.

Evelyne Lauret (E)

Université de Paris, Institut Cochin, Inserm U1016, CNRS UMR 8104, Paris, France.

Nabih Maslah (N)

Inserm UMR-S 1131, Hôpital Saint-Louis, Paris, France.
Université de Paris Cité, Paris, France.
Service de Biologie Cellulaire, Hôpital Saint-Louis, Assistance Publique-Hôpitaux de Paris, Paris, France.

Veronique Parietti (V)

Université de Paris Cité, Paris, France.
INSERM/CNRS US53/UAR2030, Institut de Recherche Saint-Louis, Paris, France.

Wenchao Zhang (W)

Université de Paris Cité, Paris, France.

Véronique Meignin (V)

Université de Paris Cité, Paris, France.
Histo-pathological Department, Hôpital Saint-Louis, Paris, France.

Jean-Jacques Kiladjian (JJ)

Inserm UMR-S 1131, Hôpital Saint-Louis, Paris, France.
Université de Paris Cité, Paris, France.
Centre Investigations Cliniques, Hôpital Saint-Louis, Paris, France.

Bruno Cassinat (B)

Inserm UMR-S 1131, Hôpital Saint-Louis, Paris, France.
Service de Biologie Cellulaire, Hôpital Saint-Louis, Assistance Publique-Hôpitaux de Paris, Paris, France.

Stephane Giraudier (S)

Inserm UMR-S 1131, Hôpital Saint-Louis, Paris, France. stephane.giraudier@aphp.fr.
Université de Paris Cité, Paris, France. stephane.giraudier@aphp.fr.
Service de Biologie Cellulaire, Hôpital Saint-Louis, Assistance Publique-Hôpitaux de Paris, Paris, France. stephane.giraudier@aphp.fr.

Classifications MeSH