Coinheritance of hereditary spherocytosis with haemochromatosis: next-generation sequencing reveals.

Haematology (incl blood transfusion) Nonalcoholic steatosis

Journal

BMJ case reports
ISSN: 1757-790X
Titre abrégé: BMJ Case Rep
Pays: England
ID NLM: 101526291

Informations de publication

Date de publication:
09 Jan 2024
Historique:
medline: 10 1 2024
pubmed: 10 1 2024
entrez: 9 1 2024
Statut: epublish

Résumé

We report the case of a man in his 50s with extravascular haemolysis, fluctuating indirect hyperbilirubinaemia, elevated transferrin saturation with hyperferritinaemia and normal liver enzymes. Spherocytes were detected in a blood smear and a mutation of unknown significance, c.1626+1G>A p.?, in intron 13 of the

Identifiants

pubmed: 38195192
pii: 17/1/e256891
doi: 10.1136/bcr-2023-256891
pii:
doi:

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Informations de copyright

© BMJ Publishing Group Limited 2024. No commercial re-use. See rights and permissions. Published by BMJ.

Déclaration de conflit d'intérêts

Competing interests: None declared.

Auteurs

Inês Hilário Soldin (IH)

Internal Medicine Department, Hospital Pedro Hispano, Matosinhos, Portugal ineshsilva@gmail.com.
Portuguese Institute of Oncology of Porto, Francisco Gentil EPE, Porto, Portugal.

Ana Ferro (A)

Internal Medicine Department, Hospital Pedro Hispano, Matosinhos, Portugal.

Yuliana O Eremina (YO)

Clinical Pathology Department, Hospital Pedro Hispano, Matosinhos, Portugal.
University of Porto, Porto, Portugal.

Mário Sérgio Nascimento Bibi (MSN)

Internal Medicine Department, Hospital Pedro Hispano, Matosinhos, Portugal.

Classifications MeSH