Cystic fibrosis in Europe: improved lung function & longevity: reasons for cautious optimism, but challenges remain.


Journal

The European respiratory journal
ISSN: 1399-3003
Titre abrégé: Eur Respir J
Pays: England
ID NLM: 8803460

Informations de publication

Date de publication:
01 Feb 2024
Historique:
received: 25 07 2023
accepted: 08 01 2024
medline: 2 2 2024
pubmed: 2 2 2024
entrez: 1 2 2024
Statut: aheadofprint

Résumé

Prognosis and disease severity in cystic fibrosis (CF) is linked to declining lung function. To characterize lung function by the number of adults in countries with different level of Gross National Income (GNI), data from the European Cystic Fibrosis Society Patient Registry was utilized. Annual data including age, forced expiratory volume in 1 s (FEV A consistent improvement in FEV This pan-European analysis demonstrates a consistent improvement in FEV

Sections du résumé

BACKGROUND BACKGROUND
Prognosis and disease severity in cystic fibrosis (CF) is linked to declining lung function. To characterize lung function by the number of adults in countries with different level of Gross National Income (GNI), data from the European Cystic Fibrosis Society Patient Registry was utilized.
METHODS METHODS
Annual data including age, forced expiratory volume in 1 s (FEV
FINDINGS RESULTS
A consistent improvement in FEV
INTERPRETATION CONCLUSIONS
This pan-European analysis demonstrates a consistent improvement in FEV

Identifiants

pubmed: 38302155
pii: 13993003.01241-2023
doi: 10.1183/13993003.01241-2023
pii:
doi:

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Informations de copyright

Copyright ©The authors 2024. For reproduction rights and permissions contact permissions@ersnet.org.

Auteurs

Eitan Kerem (E)

Department of Paediatrics and CF Center, Hebrew University Medical School, Hadassah Medical Center, Jerusalem, Israel kerem@hadassah.org.il.

Annalisa Orenti (A)

Department of Clinical Sciences and Community Health, Laboratory of Medical Statistics, Biometry and Epidemiology "G.A. Maccaccaro", University of Milan, Milan, Italy.

Arianna Adamoli (A)

Department of Clinical Sciences and Community Health, Laboratory of Medical Statistics, Biometry and Epidemiology "G.A. Maccaccaro", University of Milan, Milan, Italy.

Elpis Hatziagorou (E)

Paediatric Pulmonology and Cystic Fibrosis Unit, 3rd Paediatric Department, Hippokration Hospital, Aristotle University of Thessaloniki, Thessaloniki, Greece.
Equally contributed to the manuscript.

Lutz Naehrlich (L)

Department of Pediatrics, Justus-Liebig-University Giessen, Giessen, Germany.
Equally contributed to the manuscript.

Isabelle Sermet-Gaudelus (I)

Cystic Fibrosis National Pediatric Reference Center, Pneumo-Allergologie Pédiatrique, Hôpital Necker Enfants Malades, Assistance Publique Hôpitaux de Paris (AP-HP), Paris, France.
INSERM, CNRS, Institut Necker Enfants Malades, Paris, France.
Université Paris-Cité, Paris, France.
Equally contributed to the manuscript.

Classifications MeSH