Complement activation and cellular inflammation in Fabry disease patients despite enzyme replacement therapy.

C3a C5a Fabry disease complement enzyme replacement therapy

Journal

Frontiers in immunology
ISSN: 1664-3224
Titre abrégé: Front Immunol
Pays: Switzerland
ID NLM: 101560960

Informations de publication

Date de publication:
2024
Historique:
received: 04 10 2023
accepted: 03 01 2024
medline: 2 2 2024
pubmed: 2 2 2024
entrez: 2 2 2024
Statut: epublish

Résumé

Defective α-galactosidase A (AGAL/GLA) due to missense or nonsense mutations in the

Identifiants

pubmed: 38304433
doi: 10.3389/fimmu.2024.1307558
pmc: PMC10830671
doi:

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Pagination

1307558

Informations de copyright

Copyright © 2024 Laffer, Lenders, Ehlers-Jeske, Heidenreich, Brand and Köhl.

Déclaration de conflit d'intérêts

KH was employed by the company Eleva GmbH. JK received advisory fees from Eleva GmbH. ML received speaker honoraria, travel funding and research grants from Amicus Therapeutics, Sanofi Genzyme, Chiesi, and Shire/Takeda. EB received research grants and speaker honoraria from Sanofi Genzymem Shire/Takeda, Chiesi, Eleva GmbH and Amicus Therapeutics. The remaining authors declare that the research was conducted in the absence of any commercial or financial relationship that could be construed as a potential conflict of interest. The authors declare that this study received funding from Eleva GmbH. The funder was involved in the study design, review and editing of the manuscript.

Auteurs

Björn Laffer (B)

Institute for Systemic Inflammation Research, University of Lübeck, Lübeck, Germany.

Malte Lenders (M)

Department of Internal Medicine D, University Hospital Münster, Münster, Germany.

Elvira Ehlers-Jeske (E)

Institute for Systemic Inflammation Research, University of Lübeck, Lübeck, Germany.

Karin Heidenreich (K)

Eleva GmbH, Freiburg, Germany.

Eva Brand (E)

Department of Internal Medicine D, University Hospital Münster, Münster, Germany.

Jörg Köhl (J)

Institute for Systemic Inflammation Research, University of Lübeck, Lübeck, Germany.
Division of Immunobiology, Cincinnati Children's Hospital Medical Center, Cincinnati, OH, United States.

Classifications MeSH