Vasculitis and vasculopathy associated with inborn errors of immunity: an overview.

Systemic autoinflammatory diseases (SAIDs) are disorders of innate immunity, which are characterized by unprovoked recurrent flares of systemic inflammation often characterized by fever associated with clinical manifestations mainly involving the musculoskeletal, mucocutaneous, gastrointestinal, and nervous systems. Several conditions also present with varied, sometimes prominent, involvement of the vascular system, with features of vasculitis characterized by variable target vessel involvement and organ damage. Here, we report a systematic review of vasculitis and vasculopathy associated with inborn errors of immunity.

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© 2024 Federici, Cinicola, La Torre, Castagnoli, Lougaris, Giardino, Volpi, Caorsi, Leonardi, Corrente, Soresina, Cancrini, Insalaco, Gattorno, De Benedetti, Marseglia, Del Giudice and Cardinale.

Déclaration de conflit d'intérêts

The authors declare that the research was conducted in the absence of any commercial or financial relationships that could be construed as a potential conflict of interest.