Comparative transcriptomic analysis of circulating endothelial cells in sickle cell stroke.

Endothelial colony-forming cells Ischemic stroke RNA-Seq Sickle cell anemia

Journal

Annals of hematology
ISSN: 1432-0584
Titre abrégé: Ann Hematol
Pays: Germany
ID NLM: 9107334

Informations de publication

Date de publication:
22 Feb 2024
Historique:
received: 11 10 2023
accepted: 08 02 2024
medline: 22 2 2024
pubmed: 22 2 2024
entrez: 22 2 2024
Statut: aheadofprint

Résumé

Ischemic stroke (IS) is one of the most impairing complications of sickle cell anemia (SCA), responsible for 20% of mortality in patients. Rheological alterations, adhesive properties of sickle reticulocytes, leukocyte adhesion, inflammation and endothelial dysfunction are related to the vasculopathy observed prior to ischemic events. The role of the vascular endothelium in this complex cascade of mechanisms is emphasized, as well as in the process of ischemia-induced repair and neovascularization. The aim of the present study was to perform a comparative transcriptomic analysis of endothelial colony-forming cells (ECFCs) from SCA patients with and without IS. Next, to gain further insights of the biological relevance of differentially expressed genes (DEGs), functional enrichment analysis, protein-protein interaction network (PPI) construction and in silico prediction of regulatory factors were performed. Among the 2469 DEGs, genes related to cell proliferation (AKT1, E2F1, CDCA5, EGFL7), migration (AKT1, HRAS), angiogenesis (AKT1, EGFL7) and defense response pathways (HRAS, IRF3, TGFB1), important endothelial cell molecular mechanisms in post ischemia repair were identified. Despite the severity of IS in SCA, widely accepted molecular targets are still lacking, especially related to stroke outcome. The comparative analysis of the gene expression profile of ECFCs from IS patients versus controls seems to indicate that there is a persistent angiogenic process even after a long time this complication has occurred. Thus, this is an original study which may lead to new insights into the molecular basis of SCA stroke and contribute to a better understanding of the role of endothelial cells in stroke recovery.

Identifiants

pubmed: 38386032
doi: 10.1007/s00277-024-05655-6
pii: 10.1007/s00277-024-05655-6
doi:

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Subventions

Organisme : Fundação de Amparo à Pesquisa do Estado de São Paulo
ID : 2021/14089-0
Organisme : Fundação de Amparo à Pesquisa do Estado de São Paulo
ID : 2014/00984-3
Organisme : Fundação de Amparo à Pesquisa do Estado de São Paulo
ID : 2019/18886-1
Organisme : Coordenação de Aperfeiçoamento de Pessoal de Nível Superior
ID : Finance code 001

Informations de copyright

© 2024. The Author(s), under exclusive licence to Springer-Verlag GmbH Germany, part of Springer Nature.

Références

Kato GJ, Piel FB, Reid CD et al (2018) Sickle cell disease. Nat Rev Dis Primers 4:18010. https://doi.org/10.1038/nrdp.2018.10
doi: 10.1038/nrdp.2018.10 pubmed: 29542687
Balkaran B, Char G, Morris JS et al (1992) Stroke in a cohort of patients with homozygous sickle cell disease. J Pediatr 120:360–366. https://doi.org/10.1016/S0022-3476(05)80897-2
doi: 10.1016/S0022-3476(05)80897-2 pubmed: 1538280
Ohene-Frempong K, Weiner SJ, Sleeper LA et al (1998) Cerebrovascular accidents in sickle cell disease: rates and risk factors. Blood 91:288–294
pubmed: 9414296
Driscoll MC (2003) Stroke risk in siblings with sickle cell anemia. Blood 101:2401–2404. https://doi.org/10.1182/blood.V101.6.2401
doi: 10.1182/blood.V101.6.2401 pubmed: 12609963
Adams R, McKie V, Nichols F et al (1992) The use of transcranial ultrasonography to predict stroke in sickle cell disease. N Engl J Med 326:605–610. https://doi.org/10.1056/NEJM199202273260905
doi: 10.1056/NEJM199202273260905 pubmed: 1734251
Adams RJ (2013) Toward a stroke-free childhood in sickle cell disease. Stroke 44:2930–2934. https://doi.org/10.1161/STROKEAHA.113.001312
doi: 10.1161/STROKEAHA.113.001312 pubmed: 24008577
Adams RJ, McKie VC, Hsu L et al (1998) Prevention of a first stroke by transfusions in children with sickle cell anemia and abnormal results on transcranial doppler ultrasonography. N Engl J Med 339:5–11. https://doi.org/10.1056/NEJM199807023390102
doi: 10.1056/NEJM199807023390102 pubmed: 9647873
Ware RE, Davis BR, Schultz WH et al (2016) Hydroxycarbamide versus chronic transfusion for maintenance of transcranial doppler flow velocities in children with sickle cell anaemia—TCD with transfusions changing to hydroxyurea (TWiTCH): a multicentre, open-label, phase 3, non-inferiority trial. The Lancet 387:661–670. https://doi.org/10.1016/S0140-6736(15)01041-7
doi: 10.1016/S0140-6736(15)01041-7
Runge A, Brazel D, Pakbaz Z (2022) Stroke in sickle cell disease and the promise of recent disease modifying agents. J Neurol Sci 442:120412. https://doi.org/10.1016/j.jns.2022.120412
doi: 10.1016/j.jns.2022.120412 pubmed: 36150233
Liao S, Luo C, Cao B et al (2017) Endothelial progenitor cells for ischemic stroke: update on basic research and application. Stem Cells Int 2017:1–12. https://doi.org/10.1155/2017/2193432
doi: 10.1155/2017/2193432
Moubarik C, Guillet B, Youssef B et al (2011) Transplanted late outgrowth endothelial progenitor cells as cell therapy product for stroke. Stem Cell Rev Rep 7:208–220. https://doi.org/10.1007/s12015-010-9157-y
doi: 10.1007/s12015-010-9157-y pubmed: 20526754
Rakkar K, Othman O, Sprigg N et al (2020) Endothelial progenitor cells, potential biomarkers for diagnosis and prognosis of ischemic stroke: protocol for an observational case-control study. Neural Regen Res 15:1300. https://doi.org/10.4103/1673-5374.269028
doi: 10.4103/1673-5374.269028 pubmed: 31960816 pmcid: 7047808
Yan F, Liu X, Ding H, Zhang W (2022) Paracrine mechanisms of endothelial progenitor cells in vascular repair. Acta Histochem 124:151833. https://doi.org/10.1016/j.acthis.2021.151833
doi: 10.1016/j.acthis.2021.151833 pubmed: 34929523
Shirota T, He H, Yasui H, Matsuda T (2003) Human endothelial progenitor cell-seeded hybrid graft: proliferative and antithrombogenic potentials in vitro and fabrication processing. Tissue Eng 9:127–136. https://doi.org/10.1089/107632703762687609
doi: 10.1089/107632703762687609 pubmed: 12625961
Alwjwaj M, Kadir RA, Bayraktutan U (2021) The secretome of endothelial progenitor cells: a potential therapeutic strategy for ischemic stroke. Neural Regen Res 16:1483. https://doi.org/10.4103/1673-5374.303012
doi: 10.4103/1673-5374.303012 pubmed: 33433461 pmcid: 8323700
Hur J, Yoon C-H, Kim H-S et al (2004) Characterization of two types of endothelial progenitor cells and their different contributions to neovasculogenesis. Arterioscler Thromb Vasc Biol 24:288–293. https://doi.org/10.1161/01.ATV.0000114236.77009.06
doi: 10.1161/01.ATV.0000114236.77009.06 pubmed: 14699017
Ito MT, da Silva Costa SM, Baptista LC, et al (2020) Angiogenesis-related genes in endothelial progenitor cells may be involved in sickle cell stroke. J Am Heart Assoc 9(3):e014143. https://doi.org/10.1161/JAHA.119.014143
de Bertozzo VHE, da Silva Costa SM, Ito MT et al (2023) Comparative transcriptome analysis of endothelial progenitor cells of HbSS patients with and without proliferative retinopathy. Exp Biol Med 248:677–684. https://doi.org/10.1177/15353702231157927
doi: 10.1177/15353702231157927
Banno K, Yoder MC (2018) Tissue regeneration using endothelial colony-forming cells: promising cells for vascular repair. Pediatr Res 83:283–290. https://doi.org/10.1038/pr.2017.231
doi: 10.1038/pr.2017.231 pubmed: 28915234
Flanagan JM, Frohlich DM, Howard TA et al (2011) Genetic predictors for stroke in children with sickle cell anemia. Blood 117:6681–6684. https://doi.org/10.1182/blood-2011-01-332205
doi: 10.1182/blood-2011-01-332205 pubmed: 21515823 pmcid: 3123027
Amlie-Lefond C, Flanagan J, Kanter J, Dobyns WB (2018) The genetic landscape of cerebral steno-occlusive arteriopathy and stroke in sickle cell anemia. J Stroke Cerebrovasc Dis 27:2897–2904. https://doi.org/10.1016/j.jstrokecerebrovasdis.2018.06.004
doi: 10.1016/j.jstrokecerebrovasdis.2018.06.004 pubmed: 30076115
Flanagan JM, Sheehan V, Linder H et al (2013) Genetic mapping and exome sequencing identify 2 mutations associated with stroke protection in pediatric patients with sickle cell anemia. Blood 121:3237–3245. https://doi.org/10.1182/blood-2012-10-464156
doi: 10.1182/blood-2012-10-464156 pubmed: 23422753 pmcid: 3630835
Lee J-M, Fernandez-Cadenas I, Lindgren AG (2021) Using human genetics to understand mechanisms in ischemic stroke outcome: from early brain injury to long-term recovery. Stroke 52:3013–3024. https://doi.org/10.1161/STROKEAHA.121.032622
doi: 10.1161/STROKEAHA.121.032622 pubmed: 34399587 pmcid: 8938679
Manzoni C, Kia DA, Vandrovcova J et al (2018) Genome, transcriptome and proteome: the rise of omics data and their integration in biomedical sciences. Brief Bioinform 19:286–302. https://doi.org/10.1093/bib/bbw114
doi: 10.1093/bib/bbw114 pubmed: 27881428
Sakamoto TM, Lanaro C, Ozelo MC et al (2013) Increased adhesive and inflammatory properties in blood outgrowth endothelial cells from sickle cell anemia patients. Microvasc Res 90:173–179. https://doi.org/10.1016/j.mvr.2013.10.002
doi: 10.1016/j.mvr.2013.10.002 pubmed: 24144783
Lin Y, Weisdorf DJ, Solovey A, Hebbel RP (2000) Origins of circulating endothelial cells and endothelial outgrowth from blood. J Clin Investig 105:71–77. https://doi.org/10.1172/JCI8071
doi: 10.1172/JCI8071 pubmed: 10619863 pmcid: 382587
Andrews S (2010) FastQC: a quality control tool for high throughput sequence data. In: http://www.bioinformatics.babraham.ac.uk/projects/fastqc/ . Accessed 15 Oct 2021
Dobin A, Davis CA, Schlesinger F et al (2013) STAR: ultrafast universal RNA-seq aligner. Bioinformatics 29:15–21. https://doi.org/10.1093/bioinformatics/bts635
doi: 10.1093/bioinformatics/bts635 pubmed: 23104886
Liao Y, Smyth GK, Shi W (2014) featureCounts: an efficient general purpose program for assigning sequence reads to genomic features. Bioinformatics 30:923–930. https://doi.org/10.1093/bioinformatics/btt656
doi: 10.1093/bioinformatics/btt656 pubmed: 24227677
RStudio Team (2021) RStudio: Integrated Development Environment for R. RStudio, PBC, Boston, MA.  https://www.rstudio.com/
Robinson MD, McCarthy DJ, Smyth GK (2010) <tt>edgeR</tt> : a Bioconductor package for differential expression analysis of digital gene expression data. Bioinformatics 26:139–140. https://doi.org/10.1093/bioinformatics/btp616
doi: 10.1093/bioinformatics/btp616 pubmed: 19910308
Kolde R (2019) Pheatmap: pretty heatmaps. R package version 1.0.12. In: https://CRAN.Rproject.org/package=pheatmap . Accessed 28 Jul 2023
Blighe K, Lun A (2021) PCAtools: PCAtools: everything principal components analysis. R package version 2.4.0. In: https://github.com/kevinblighe/PCAtools . Accessed 28 Jul 2023
Blighe K, Rana S, Lewis M (2021) EnhancedVolcano: publication-ready volcano plots with enhanced colouring and labeling. R package version 1.10.0. In: https://github.com/kevinblighe/EnhancedVolcano . Accessed 28 Jul 2023
Dennis G, Sherman BT, Hosack DA et al (2003) DAVID: database for annotation, visualization, and integrated discovery. Genome Biol 4:P3
doi: 10.1186/gb-2003-4-5-p3 pubmed: 12734009
Doncheva NT, Morris JH, Gorodkin J, Jensen LJ (2019) Cytoscape StringApp: network analysis and visualization of proteomics data. J Proteome Res 18:623–632. https://doi.org/10.1021/acs.jproteome.8b00702
doi: 10.1021/acs.jproteome.8b00702 pubmed: 30450911
Shannon P, Markiel A, Ozier O et al (2003) Cytoscape: a software environment for integrated models of biomolecular interaction networks. Genome Res 13:2498–2504. https://doi.org/10.1101/gr.1239303
doi: 10.1101/gr.1239303 pubmed: 14597658 pmcid: 403769
Chin C-H, Chen S-H, Wu H-H et al (2014) cytoHubba: identifying hub objects and sub-networks from complex interactome. BMC Syst Biol 8:S11. https://doi.org/10.1186/1752-0509-8-S4-S11
doi: 10.1186/1752-0509-8-S4-S11 pubmed: 25521941 pmcid: 4290687
SankeyMATIC tool SankeyMATIC: a Sankey diagram builder for everyone. In: http://sankeymatic.com/ . Accessed 3 Aug 2023
Clarke DJB, Kuleshov MV, Schilder BM et al (2018) eXpression2Kinases (X2K) Web: linking expression signatures to upstream cell signaling networks. Nucleic Acids Res 46:W171–W179. https://doi.org/10.1093/nar/gky458
doi: 10.1093/nar/gky458 pubmed: 29800326 pmcid: 6030863
Zhang ZG, Zhang L, Jiang Q, Chopp M (2002) Bone marrow-derived endothelial progenitor cells participate in cerebral neovascularization after focal cerebral ischemia in the adult mouse. Circ Res 90:284–288. https://doi.org/10.1161/hh0302.104460
doi: 10.1161/hh0302.104460 pubmed: 11861416
Li J, Ma Y, Miao X-H et al (2021) Neovascularization and tissue regeneration by endothelial progenitor cells in ischemic stroke. Neurol Sci 42:3585–3593. https://doi.org/10.1007/s10072-021-05428-3
doi: 10.1007/s10072-021-05428-3 pubmed: 34216308
Somanath PR, Razorenova OV, Chen J, Byzova TV (2006) Akt1 in endothelial cell and angiogenesis. Cell Cycle 5:512–518. https://doi.org/10.4161/cc.5.5.2538
doi: 10.4161/cc.5.5.2538 pubmed: 16552185
Hallstrom TC, Mori S, Nevins JR (2008) An E2F1-dependent gene expression program that determines the balance between proliferation and cell death. Cancer Cell 13:11–22. https://doi.org/10.1016/j.ccr.2007.11.031
doi: 10.1016/j.ccr.2007.11.031 pubmed: 18167336 pmcid: 2243238
Ladu S, Calvisi DF, Conner EA et al (2008) E2F1 inhibits c-Myc-driven apoptosis via PIK3CA/Akt/mTOR and COX-2 in a mouse model of human liver cancer. Gastroenterology 135:1322–1332. https://doi.org/10.1053/j.gastro.2008.07.012
doi: 10.1053/j.gastro.2008.07.012 pubmed: 18722373
Chang L, Xi L, Liu Y et al (2018) SIRT5 promotes cell proliferation and invasion in hepatocellular carcinoma by targeting E2F1. Mol Med Rep 17:342–349. https://doi.org/10.3892/MMR.2017.7875
doi: 10.3892/MMR.2017.7875 pubmed: 29115436
Chaussepied M, Ginsberg D (2004) Transcriptional regulation of AKT activation by E2F. Mol Cell 16:831–837. https://doi.org/10.1016/j.molcel.2004.11.003
doi: 10.1016/j.molcel.2004.11.003 pubmed: 15574337
Meng P, Ghosh R (2014) Transcription addiction: can we garner the Yin and Yang functions of E2F1 for cancer therapy? Cell Death Dis 5(8):e1360–e1360. https://doi.org/10.1038/cddis.2014.326
doi: 10.1038/cddis.2014.326 pubmed: 25101673 pmcid: 4454301
Nishiyama T, Ladurner R, Schmitz J et al (2010) Sororin mediates sister chromatid cohesion by antagonizing Wapl. Cell 143:737–749. https://doi.org/10.1016/j.cell.2010.10.031
doi: 10.1016/j.cell.2010.10.031 pubmed: 21111234
Nguyen M-H, Koinuma J, Ueda K et al (2010) Phosphorylation and activation of cell division cycle associated 5 by mitogen-activated protein kinase play a crucial role in human lung carcinogenesis. Cancer Res 70:5337–5347. https://doi.org/10.1158/0008-5472.CAN-09-4372
doi: 10.1158/0008-5472.CAN-09-4372 pubmed: 20551060
Xu J, Zhu C, Yu Y et al (2019) Systematic cancer-testis gene expression analysis identified CDCA5 as a potential therapeutic target in esophageal squamous cell carcinoma. EBioMedicine 46:54–65. https://doi.org/10.1016/j.ebiom.2019.07.030
doi: 10.1016/j.ebiom.2019.07.030 pubmed: 31324603 pmcid: 6710982
Shen A, Liu L, Chen H et al (2019) Cell division cycle associated 5 promotes colorectal cancer progression by activating the ERK signaling pathway. Oncogenesis 8:19. https://doi.org/10.1038/s41389-019-0123-5
doi: 10.1038/s41389-019-0123-5 pubmed: 30808873 pmcid: 6391450
Chen H, Chen J, Zhao L et al (2019) CDCA5, transcribed by E2F1, promotes Oncogenesis by enhancing cell proliferation and inhibiting apoptosis via the AKT pathway in hepatocellular carcinoma. J Cancer 10:1846–1854. https://doi.org/10.7150/jca.28809
doi: 10.7150/jca.28809 pubmed: 31205541 pmcid: 6547986
Parker LH, Schmidt M, Jin S-W et al (2004) The endothelial-cell-derived secreted factor Egfl7 regulates vascular tube formation. Nature 428:754–758. https://doi.org/10.1038/nature02416
doi: 10.1038/nature02416 pubmed: 15085134
Campagnolo L, Leahy A, Chitnis S et al (2005) EGFL7 is a chemoattractant for endothelial cells and is up-regulated in angiogenesis and arterial injury. Am J Pathol 167:275–284. https://doi.org/10.1016/S0002-9440(10)62972-0
doi: 10.1016/S0002-9440(10)62972-0 pubmed: 15972971 pmcid: 1451775
Badiwala MV, Tumiati LC, Joseph JM, et al (2010) Epidermal growth factor-like domain 7 suppresses intercellular adhesion molecule 1 expression in response to hypoxia/reoxygenation injury in human coronary artery endothelial cells. Circulation 122(11 Suppl):S156–61. https://doi.org/10.1161/CIRCULATIONAHA.109.927715
Gustavsson M, Mallard C, Vannucci SJ et al (2007) Vascular response to hypoxic preconditioning in the immature brain. J Cereb Blood Flow Metab 27:928–938. https://doi.org/10.1038/sj.jcbfm.9600408
doi: 10.1038/sj.jcbfm.9600408 pubmed: 17033689
Li Q, Cheng K, Wang A-Y et al (2019) microRNA-126 inhibits tube formation of HUVECs by interacting with EGFL7 and down-regulating PI3K/AKT signaling pathway. Biomed Pharmacother 116:109007. https://doi.org/10.1016/j.biopha.2019.109007
doi: 10.1016/j.biopha.2019.109007 pubmed: 31170663
Schmidt M, Paes K, De Mazière A et al (2007) EGFL7 regulates the collective migration of endothelial cells by restricting their spatial distribution. Development 134:2913–2923. https://doi.org/10.1242/dev.002576
doi: 10.1242/dev.002576 pubmed: 17626061
Soncin F (2003) VE-statin, an endothelial repressor of smooth muscle cell migration. EMBO J 22:5700–5711. https://doi.org/10.1093/emboj/cdg549
doi: 10.1093/emboj/cdg549 pubmed: 14592969 pmcid: 275406
Wu XY, Liu WT, Wu ZF et al (2016) Identification of HRAS as cancer-promoting gene in gastric carcinoma cell aggressiveness. Am J Cancer Res 6:1935–1948
pubmed: 27725900 pmcid: 5043104
Li Q, Decker-Rockefeller B, Bajaj A, Pumiglia K (2018) Activation of Ras in the vascular endothelium induces brain vascular malformations and hemorrhagic stroke. Cell Rep 24:2869–2882. https://doi.org/10.1016/j.celrep.2018.08.025
doi: 10.1016/j.celrep.2018.08.025 pubmed: 30208313
Montaner J, Ramiro L, Simats A et al (2020) Multilevel omics for the discovery of biomarkers and therapeutic targets for stroke. Nat Rev Neurol 16:247–264. https://doi.org/10.1038/s41582-020-0350-6
doi: 10.1038/s41582-020-0350-6 pubmed: 32322099
Pepper MS (1997) Transforming growth factor-beta: vasculogenesis, angiogenesis, and vessel wall integrity. Cytokine Growth Factor Rev 8:21–43. https://doi.org/10.1016/S1359-6101(96)00048-2
doi: 10.1016/S1359-6101(96)00048-2 pubmed: 9174661
Cheng X, Yang Y-L, Li W-H et al (2020) Cerebral ischemia-reperfusion aggravated cerebral infarction injury and possible differential genes identified by RNA-Seq in rats. Brain Res Bull 156:33–42. https://doi.org/10.1016/j.brainresbull.2019.12.014
doi: 10.1016/j.brainresbull.2019.12.014 pubmed: 31877338
Downward J (2009) A tumour gene’s fatal flaws. Nature 462:44–45. https://doi.org/10.1038/462044a
doi: 10.1038/462044a pubmed: 19890318
Tarassishin L, Suh H-S, Lee SC (2011) Interferon regulatory factor 3 plays an anti-inflammatory role in microglia by activating the PI3K/Akt pathway. J Neuroinflammation 8:187. https://doi.org/10.1186/1742-2094-8-187
doi: 10.1186/1742-2094-8-187 pubmed: 22208359 pmcid: 3259120
Vadas O, Burke JE, Zhang X, et al (2011) Structural basis for activation and inhibition of class I phosphoinositide 3-kinases. Sci Signal 4(195):re2. https://doi.org/10.1126/scisignal.2002165
Thorpe LM, Spangle JM, Ohlson CE et al (2017) PI3K-p110α mediates the oncogenic activity induced by loss of the novel tumor suppressor PI3K-p85α. Proc Natl Acad Sci 114:7095–7100. https://doi.org/10.1073/pnas.1704706114
doi: 10.1073/pnas.1704706114 pubmed: 28630349 pmcid: 5502636
Chang Milbauer L, Wei P, Enenstein J et al (2008) Genetic endothelial systems biology of sickle stroke risk. Blood 111:3872–3879. https://doi.org/10.1182/blood-2007-06-097188
doi: 10.1182/blood-2007-06-097188 pubmed: 18156497 pmcid: 2275038
Zhang SJ, Zhang H, Wei YJ et al (2006) Adult endothelial progenitor cells from human peripheral blood maintain monocyte/macrophage function throughout in vitro culture. Cell Res 16:577–584. https://doi.org/10.1038/sj.cr.7310075
doi: 10.1038/sj.cr.7310075 pubmed: 16775629
Mikirova NA, Jackson JA, Hunninghake R et al (2009) Circulating endothelial progenitor cells: a new approach to anti-aging medicine? J Transl Med 7:106. https://doi.org/10.1186/1479-5876-7-106
doi: 10.1186/1479-5876-7-106 pubmed: 20003528 pmcid: 2804590
Ding D-C, Shyu W-C, Lin S-Z, Li H (2007) The role of endothelial progenitor cells in ischemic cerebral and heart diseases. Cell Transplant 16:273–284. https://doi.org/10.3727/000000007783464777
doi: 10.3727/000000007783464777 pubmed: 17503738

Auteurs

Júlia Nicoliello Pereira de Castro (JNP)

Laboratory of Human Genetics, Center for Molecular Biology and Genetic Engineering-CBMEG, Universidade Estadual de Campinas-UNICAMP, Campinas, São Paulo, 13083-875, Brazil.

Sueli Matilde da Silva Costa (SM)

Laboratory of Human Genetics, Center for Molecular Biology and Genetic Engineering-CBMEG, Universidade Estadual de Campinas-UNICAMP, Campinas, São Paulo, 13083-875, Brazil.

Ana Carolina Lima Camargo (ACL)

Laboratory of Human Genetics, Center for Molecular Biology and Genetic Engineering-CBMEG, Universidade Estadual de Campinas-UNICAMP, Campinas, São Paulo, 13083-875, Brazil.

Mirta Tomie Ito (MT)

Laboratory of Human Genetics, Center for Molecular Biology and Genetic Engineering-CBMEG, Universidade Estadual de Campinas-UNICAMP, Campinas, São Paulo, 13083-875, Brazil.

Bruno Batista de Souza (BB)

Laboratory of Human Genetics, Center for Molecular Biology and Genetic Engineering-CBMEG, Universidade Estadual de Campinas-UNICAMP, Campinas, São Paulo, 13083-875, Brazil.

Victor de Haidar E Bertozzo (V)

Laboratory of Human Genetics, Center for Molecular Biology and Genetic Engineering-CBMEG, Universidade Estadual de Campinas-UNICAMP, Campinas, São Paulo, 13083-875, Brazil.

Thiago Adalton Rosa Rodrigues (TAR)

Laboratory of Human Genetics, Center for Molecular Biology and Genetic Engineering-CBMEG, Universidade Estadual de Campinas-UNICAMP, Campinas, São Paulo, 13083-875, Brazil.

Carolina Lanaro (C)

Hematology and Hemotherapy Center, Universidade Estadual de Campinas-UNICAMP, Campinas, São Paulo, Brazil.

Dulcinéia Martins de Albuquerque (DM)

Hematology and Hemotherapy Center, Universidade Estadual de Campinas-UNICAMP, Campinas, São Paulo, Brazil.

Roberta Casagrande Saez (RC)

Hematology and Hemotherapy Center, Universidade Estadual de Campinas-UNICAMP, Campinas, São Paulo, Brazil.

Sara Teresinha Olalla Saad (STO)

Hematology and Hemotherapy Center, Universidade Estadual de Campinas-UNICAMP, Campinas, São Paulo, Brazil.

Margareth Castro Ozelo (MC)

Hematology and Hemotherapy Center, Universidade Estadual de Campinas-UNICAMP, Campinas, São Paulo, Brazil.

Fernando Cendes (F)

Neuroimaging Laboratory, Department of Neurology, Universidade Estadual de Campinas-UNICAMP, Campinas, São Paulo, Brazil.

Fernando Ferreira Costa (FF)

Hematology and Hemotherapy Center, Universidade Estadual de Campinas-UNICAMP, Campinas, São Paulo, Brazil.

Mônica Barbosa de Melo (MB)

Laboratory of Human Genetics, Center for Molecular Biology and Genetic Engineering-CBMEG, Universidade Estadual de Campinas-UNICAMP, Campinas, São Paulo, 13083-875, Brazil. melomb@unicamp.br.

Classifications MeSH