Conservative management by embolization of a ruptured renal arterio-venous malformation (AVM) in Hereditary Hemorrhagic Telangiectasia (HHT).

Arterio-Venous Malformation Embolization Hematuria Hereditary Hemorrhagic Telangiectasia Rendu-Osler-Weber disease

Journal

CVIR endovascular
ISSN: 2520-8934
Titre abrégé: CVIR Endovasc
Pays: Switzerland
ID NLM: 101738484

Informations de publication

Date de publication:
16 Mar 2024
Historique:
received: 02 02 2024
accepted: 07 03 2024
medline: 16 3 2024
pubmed: 16 3 2024
entrez: 16 3 2024
Statut: epublish

Résumé

Renal arteriovenous malformation (AVM) in Hereditary Hemorrhagic Telangiectasia (HHT) is uncommon and only few cases have been described, mainly with surgical management because of uncontrolled hematuria. We managed a 70-year-old patient with HHT who presented with hematuria and left flank pain. Computed Tomography and ultrasound showed left renal AVM of 18 mm with clotting in the urinary tract. An external ureteral catheter was placed during 3 days to allow rinsing and facilitate elimination of clots. Given the patient's hemodynamic stability, a non-surgical management was chosen. Treatment of the AVM was performed by trans-arterial embolization using micro-coils and ethylene-vinyl alcohol copolymer. Our case study shows a conservative management by embolization of ruptured left renal AVM revealed by hematuria in a 70-year-old patient with HHT.

Sections du résumé

BACKGROUND BACKGROUND
Renal arteriovenous malformation (AVM) in Hereditary Hemorrhagic Telangiectasia (HHT) is uncommon and only few cases have been described, mainly with surgical management because of uncontrolled hematuria.
CASE PRESENTATION METHODS
We managed a 70-year-old patient with HHT who presented with hematuria and left flank pain. Computed Tomography and ultrasound showed left renal AVM of 18 mm with clotting in the urinary tract. An external ureteral catheter was placed during 3 days to allow rinsing and facilitate elimination of clots. Given the patient's hemodynamic stability, a non-surgical management was chosen. Treatment of the AVM was performed by trans-arterial embolization using micro-coils and ethylene-vinyl alcohol copolymer.
CONCLUSIONS CONCLUSIONS
Our case study shows a conservative management by embolization of ruptured left renal AVM revealed by hematuria in a 70-year-old patient with HHT.

Identifiants

pubmed: 38492037
doi: 10.1186/s42155-024-00444-8
pii: 10.1186/s42155-024-00444-8
doi:

Types de publication

Journal Article

Langues

eng

Pagination

30

Informations de copyright

© 2024. The Author(s).

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Auteurs

Romain L'Huillier (R)

Department of Diagnostic and Interventional Radiology, Hospices Civils de Lyon, University of Lyon, Pavillon B, Hôpital Edouard Herriot, 5 Place D'Arsonval, Lyon, 69003, France. romain.lhuillier@chu-lyon.fr.
LabTAU - Inserm U1032, Lyon, 69003, France. romain.lhuillier@chu-lyon.fr.
The French Comprehensive Liver Center, Hospices Civils de Lyon, University of Lyon, Lyon, 69004, France. romain.lhuillier@chu-lyon.fr.

Gaële Pagnoux (G)

Department of Diagnostic and Interventional Radiology, Hospices Civils de Lyon, University of Lyon, Pavillon B, Hôpital Edouard Herriot, 5 Place D'Arsonval, Lyon, 69003, France.

Sophie Dupuis-Girod (S)

Genetics Department and National, Hospices Civils de Lyon, HHT Reference Center Hôpital Femme-Mère-Enfant, Bron, 69677, France.
Laboratory Biology of Cancer and Infection, Inserm, CEA, Université Grenoble Alpes, Grenoble, France.

Nicolas Stacoffe (N)

Department of Diagnostic and Interventional Radiology, Centre Hospitalier Lyon Sud, Hospices Civils de Lyon, University of Lyon, Pierre-Bénite, 69495, France.

Classifications MeSH