Determinants of health status in older patients with transthyretin cardiac amyloidosis: a prospective cohort study.

ATTR-CA Frailty KCCQ Quality of life Social environment

Journal

Aging clinical and experimental research
ISSN: 1720-8319
Titre abrégé: Aging Clin Exp Res
Pays: Germany
ID NLM: 101132995

Informations de publication

Date de publication:
10 Apr 2024
Historique:
received: 12 03 2024
accepted: 27 03 2024
medline: 10 4 2024
pubmed: 10 4 2024
entrez: 10 4 2024
Statut: epublish

Résumé

Whether, and to what extent, frailty and other geriatric domains are linked to health status in patients with transthyretin cardiac amyloidosis (ATTR-CA) is unknown. To determine the association of frailty with health status [defined by the Kansas City Cardiomyopathy Questionnaire (KCCQ)] in patients with ATTR-CA. Consecutive ATTR-CA patients undergoing cardiovascular assessment at a tertiary care clinic from September 2021 to September 2023 were invited to participate. KCCQ, frailty and social environment were recorded. Frailty was assessed using the modified Frailty Index (mFI), mapping 11 variables from the Canadian Study of Health and Aging (frailty ≥0.36). Of 168 screened ATTR-CA patients, 138 [83% men, median age of 79 (75-84) years] were enrolled in the study. Median KCCQ was 66 (50-75). wtATTR-CA was the most prevalent form (N = 113, 81.9%). The most frequent cardiac variant was Ile68Leu (17/25 individuals with vATTR-CA). Twenty (14.5%) patients were considered frail, and prevalence of overt disability was 6.5%. At multivariable linear regression analysis, factors associated with worsening KCCQ were age at evaluation, the mFI, NYHA Class, and NAC Score. Gender, ATTR-CA type, phenotype, and LVEF were not associated with health status. In older patients diagnosed with ATTR-CA, frailty, symptoms, and disease severity were associated with KCCQ. Functional status is a determinant of quality of life and health status in older individuals with a main diagnosis of ATTR-CA. Future research may provide more in-depth knowledge on the association of frailty in patients with ATTR-CA with respect to quality of life and prognosis.

Sections du résumé

BACKGROUND BACKGROUND
Whether, and to what extent, frailty and other geriatric domains are linked to health status in patients with transthyretin cardiac amyloidosis (ATTR-CA) is unknown.
AIMS OBJECTIVE
To determine the association of frailty with health status [defined by the Kansas City Cardiomyopathy Questionnaire (KCCQ)] in patients with ATTR-CA.
METHODS METHODS
Consecutive ATTR-CA patients undergoing cardiovascular assessment at a tertiary care clinic from September 2021 to September 2023 were invited to participate. KCCQ, frailty and social environment were recorded. Frailty was assessed using the modified Frailty Index (mFI), mapping 11 variables from the Canadian Study of Health and Aging (frailty ≥0.36).
RESULTS RESULTS
Of 168 screened ATTR-CA patients, 138 [83% men, median age of 79 (75-84) years] were enrolled in the study. Median KCCQ was 66 (50-75). wtATTR-CA was the most prevalent form (N = 113, 81.9%). The most frequent cardiac variant was Ile68Leu (17/25 individuals with vATTR-CA). Twenty (14.5%) patients were considered frail, and prevalence of overt disability was 6.5%. At multivariable linear regression analysis, factors associated with worsening KCCQ were age at evaluation, the mFI, NYHA Class, and NAC Score. Gender, ATTR-CA type, phenotype, and LVEF were not associated with health status.
DISCUSSION CONCLUSIONS
In older patients diagnosed with ATTR-CA, frailty, symptoms, and disease severity were associated with KCCQ.
CONCLUSIONS CONCLUSIONS
Functional status is a determinant of quality of life and health status in older individuals with a main diagnosis of ATTR-CA. Future research may provide more in-depth knowledge on the association of frailty in patients with ATTR-CA with respect to quality of life and prognosis.

Identifiants

pubmed: 38598143
doi: 10.1007/s40520-024-02750-6
pii: 10.1007/s40520-024-02750-6
doi:

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Pagination

89

Informations de copyright

© 2024. The Author(s).

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Auteurs

Carlo Fumagalli (C)

Department of Advanced Medical and Surgical Sciences, University of Campania "Luigi Vanvitelli", Naples, Italy. carlo.fumagalli@unicampania.it.
Cardiomyopathy Unit, Careggi University Hospital, Florence, Italy. carlo.fumagalli@unicampania.it.
Tuscan Regional Amyloidosis Centre, Careggi University Hospital, Florence, Italy. carlo.fumagalli@unicampania.it.

Lucia Ponti (L)

Tuscan Regional Amyloidosis Centre, Careggi University Hospital, Florence, Italy.
Department of Humanities, University of Urbino, Urbino, Italy.

Martina Smorti (M)

Department of Surgical, Medical and Molecular Pathology and Critical Care Medicine, University of Pisa, Pisa, Italy.

Francesca Pozza (F)

Tuscan Regional Amyloidosis Centre, Careggi University Hospital, Florence, Italy.

Alessia Argirò (A)

Cardiomyopathy Unit, Careggi University Hospital, Florence, Italy.
Department of Surgical, Medical and Molecular Pathology and Critical Care Medicine, University of Pisa, Pisa, Italy.

Mattia Zampieri (M)

Department of Humanities, University of Urbino, Urbino, Italy.

Carlo Di Mario (C)

Division of Interventional Structural Cardiology, Cardiothoracovascular Department, Careggi University Hospital, Florence, Italy.

Raffaele Marfella (R)

Department of Advanced Medical and Surgical Sciences, University of Campania "Luigi Vanvitelli", Naples, Italy.

Celestino Sardu (C)

Department of Advanced Medical and Surgical Sciences, University of Campania "Luigi Vanvitelli", Naples, Italy.

Giuseppe Paolisso (G)

Department of Advanced Medical and Surgical Sciences, University of Campania "Luigi Vanvitelli", Naples, Italy.

Iacopo Olivotto (I)

Cardiomyopathy Unit, Careggi University Hospital, Florence, Italy.
Meyer Children Hospital, Florence, Italy.

Federico Perfetto (F)

Department of Surgical, Medical and Molecular Pathology and Critical Care Medicine, University of Pisa, Pisa, Italy.
IV Internal Medicine Division, Careggi University Hospital, Florence, Italy.

Andrea Ungar (A)

Geriatric Intensive Care Unit, University of Florence, Florence, Italy.

Niccolò Marchionni (N)

Department of Experimental and Clinical Medicine, University of Florence, Florence, Italy.

Francesco Cappelli (F)

Cardiomyopathy Unit, Careggi University Hospital, Florence, Italy.
Division of Interventional Structural Cardiology, Cardiothoracovascular Department, Careggi University Hospital, Florence, Italy.
Department of Experimental and Clinical Medicine, University of Florence, Florence, Italy.

Classifications MeSH