The Beneficial Impact of Pulmonary Rehabilitation in Idiopathic Pulmonary Fibrosis: A Review of the Current Literature.

cardiovascular outcomes disability exercise health-related quality of life idiopathic pulmonary fibrosis occupational medicine outcome pulmonary rehabilitation

Journal

Journal of clinical medicine
ISSN: 2077-0383
Titre abrégé: J Clin Med
Pays: Switzerland
ID NLM: 101606588

Informations de publication

Date de publication:
30 Mar 2024
Historique:
received: 05 03 2024
revised: 20 03 2024
accepted: 28 03 2024
medline: 13 4 2024
pubmed: 13 4 2024
entrez: 13 4 2024
Statut: epublish

Résumé

Idiopathic pulmonary fibrosis (IPF) is a chronic and irreversible fibrotic disease whose natural history is characterised by a progressive worsening of the pulmonary function, exertional dyspnoea, exercise intolerance, reduced physical activity, and health-related quality of life (HRQOL) impairment. Pulmonary rehabilitation (PR) is a comprehensive, multi-disciplinary programme that uses a combination of strength training, teaching, counselling, and behaviour modification techniques to reduce symptoms and optimise functional capacity in patients with chronic lung disease. Based on the well-documented effectiveness of PR in chronic obstructive pulmonary disease (COPD), over the years supportive evidence of its benefits for other respiratory diseases has been emerging. Although the latest rehabilitation guidelines recognised PR's efficacy for interstitial lung disease (ILD) and IPF in particular, this comprehensive approach remains underused and under-resourced. In this review, we will discuss the advantages and beneficial effects of PR on IPF, analysing its impact on exercise capacity, disease-related symptoms, cardiovascular outcomes, body composition, and HRQOL.

Identifiants

pubmed: 38610791
pii: jcm13072026
doi: 10.3390/jcm13072026
pii:
doi:

Types de publication

Journal Article Review

Langues

eng

Subventions

Organisme : Ministero della Salute
ID : N/A

Auteurs

Stefano Sanduzzi Zamparelli (SS)

Division of Pneumology and Respiratory Physiopathology, A. Cardarelli Hospital, 80131 Naples, Italy.

Carmen Lombardi (C)

Istituti Clinici Scientifici Maugeri IRCCS, Pulmonary Rehabilitation Unit of Telese Terme Institute, 82037 Telese Terme, Italy.

Claudio Candia (C)

Department of Clinical Medicine and Surgery, University of Naples "Federico II", 80131 Naples, Italy.

Paola Rebecca Iovine (PR)

Department of Clinical Medicine and Surgery, University of Naples "Federico II", 80131 Naples, Italy.

Gaetano Rea (G)

Department of Radiology, Monaldi Hospital, Azienda Ospedaliera dei Colli, 80131 Naples, Italy.

Michele Vitacca (M)

Istituti Clinici Scientifici Maugeri IRCCS, Pulmonary Rehabilitation Unit of Lumezzane Institute, 25065 Lumezzane, Italy.

Pasquale Ambrosino (P)

Istituti Clinici Scientifici Maugeri IRCCS, Scientific Directorate of Telese Terme Institute, 82037 Telese Terme, Italy.

Marialuisa Bocchino (M)

Department of Clinical Medicine and Surgery, University of Naples "Federico II", 80131 Naples, Italy.

Mauro Maniscalco (M)

Istituti Clinici Scientifici Maugeri IRCCS, Pulmonary Rehabilitation Unit of Telese Terme Institute, 82037 Telese Terme, Italy.
Department of Clinical Medicine and Surgery, University of Naples "Federico II", 80131 Naples, Italy.

Classifications MeSH