Congenital and hereditary nail disease.

Patología ungueal congénita y hereditaria.
congenital congénito displasia ungueal distrofia ungueal genetic skin disorders nail dysplasia nail dystrophy onicodistrofia onychodystrophy trastornos genéticos de la piel

Journal

Actas dermo-sifiliograficas
ISSN: 1578-2190
Titre abrégé: Actas Dermosifiliogr
Pays: Spain
ID NLM: 0373062

Informations de publication

Date de publication:
23 Apr 2024
Historique:
received: 15 01 2024
revised: 30 03 2024
accepted: 08 04 2024
medline: 26 4 2024
pubmed: 26 4 2024
entrez: 25 4 2024
Statut: aheadofprint

Résumé

Nail disorders in newborns can show independently or as components of systemic illnesses or genodermatoses. The examination of these abnormalities is complex and sometimes challenging. However, familiarity with these disorders can significantly contribute to uncovering potential underlying conditions. This review includes the physiological nail changes seen within the first few months of life, such as Beau's lines, onychoschizia, koilonychia, congenital nail fold hypertrophy of the first digit, and onychocryptosis. This review also focuses on the most relevant congenital disorders reported and how to perform differential diagnosis. Finally, this review highlights those hereditary diseases in which nail involvement is crucial for diagnosis, such as nail-patella syndrome, congenital pachyonychia, or congenital dyskeratosis, among others.

Identifiants

pubmed: 38663727
pii: S0001-7310(24)00341-7
doi: 10.1016/j.ad.2024.04.002
pii:
doi:

Types de publication

Journal Article Review

Langues

eng spa

Sous-ensembles de citation

IM

Informations de copyright

Copyright © 2024 AEDV. Publicado por Elsevier España, S.L.U. All rights reserved.

Auteurs

L Bernal Masferrer (L)

Departamento de Dermatología, Hospital Miguel Servet, Zaragoza, Spain.

M Claudia Matei (M)

Departamento de Dermatología, Hospital Miguel Servet, Zaragoza, Spain. Electronic address: marimatei.96@gmail.com.

Y Gilaberte Calzada (Y)

Departamento de Dermatología, Hospital Miguel Servet, Zaragoza, Spain.

L Navarro Campoamor (L)

Departamento de Dermatología, Consulta Castellana 179, Madrid, Spain.

Classifications MeSH