PRKD1-related Telangiectasia-ectodermal dysplasia-brachydactyly-cardiac anomaly syndrome: case report and review of the literature.

PRKD1 TEBC syndrome ectodermal dysplasia telangiectasia

Journal

European journal of medical genetics
ISSN: 1878-0849
Titre abrégé: Eur J Med Genet
Pays: Netherlands
ID NLM: 101247089

Informations de publication

Date de publication:
25 Apr 2024
Historique:
received: 20 04 2023
revised: 18 10 2023
accepted: 25 04 2024
medline: 28 4 2024
pubmed: 28 4 2024
entrez: 27 4 2024
Statut: aheadofprint

Résumé

Telangiectasia-ectodermal dysplasia-brachydactyly-cardiac anomaly (TEBC) syndrome is a rare autosomal dominant condition, recently linked to the protein kinase D1 (PRKD1) gene. The phenotype of TEBC remains incomplete at this point. Our aim is to improve the characterization of the clinical and molecular aspects of the TEBC syndrome. We report on the 8

Identifiants

pubmed: 38677542
pii: S1769-7212(24)00034-X
doi: 10.1016/j.ejmg.2024.104942
pii:
doi:

Types de publication

Case Reports

Langues

eng

Sous-ensembles de citation

IM

Pagination

104942

Informations de copyright

Copyright © 2024. Published by Elsevier Masson SAS.

Auteurs

Fiona Leduc (F)

CHU Lille, Univ. Lille, Clinique de génétique « Guy Fontaine », ULR7364 RADEME, F-59000 Lille, France. Electronic address: fiona.leduc@chu-lille.fr.

Thomas Smol (T)

CHU Lille, Univ. Lille, Institut de Génétique médicale, ULR7364 RADEME, F-59000 Lille, France.

Benoit Catteau (B)

CHU Lille, Service de dermatologie, F-59000 Lille, France.

Odile Boute (O)

CHU Lille, Univ. Lille, Clinique de génétique « Guy Fontaine », ULR7364 RADEME, F-59000 Lille, France.

Florence Petit (F)

CHU Lille, Univ. Lille, Clinique de génétique « Guy Fontaine », ULR7364 RADEME, F-59000 Lille, France.

Classifications MeSH