Assessing joint health in haemophilia patients: The combined value of physical examination and ultrasound imaging.

haemophilia haemophilic arthropathy joint diseases physical examination synovitis ultrasonography

Journal

Haemophilia : the official journal of the World Federation of Hemophilia
ISSN: 1365-2516
Titre abrégé: Haemophilia
Pays: England
ID NLM: 9442916

Informations de publication

Date de publication:
08 May 2024
Historique:
revised: 12 04 2024
received: 02 10 2023
accepted: 16 04 2024
medline: 8 5 2024
pubmed: 8 5 2024
entrez: 8 5 2024
Statut: aheadofprint

Résumé

Early diagnosis of joint damage is pivotal in haemophilia to prevent the occurrence and progression of haemophilic arthropathy thus providing optimal personalised management. The haemophilia joint health score version 2.1 (HJHS) is based on a physical examination of the mainly affected joints. Musculoskeletal ultrasound has demonstrated the capability to detect early changes in terms of synovitis and osteochondral damage. The haemophilia early detection with ultrasound (HEAD-US) score has been proposed as a simple and reliable evaluation tool. This study aims to investigate the correlation between the HJHS and the HEAD-US scores performed by two independent operators (physical therapist and musculoskeletal ultrasound expert) for the evaluation of the joint health status of patients with haemophilia. Consecutive adult patients independent of the severity degree were included. Elbows, knees and ankles were evaluated by a physical therapist by HJHS and by a musculoskeletal ultrasound expert following the HEAD-US protocol. We observed a good positive correlation between HJHS and HEAD-US (Spearman's rho 0.72). The main discrepancy in conceptually similar domains was found between the HJHS swelling and the HEAD-US synovitis (rho 0.17), as ultrasound was able to detect even mild synovitis when HJHS swelling was scored 0 in up to 40% of cases. The HJHS and HEAD-US correlate well even when performed by two independent operators. Musculoskeletal ultrasound is particularly useful for the early detection of synovitis. The routine assessment of both scores helps clinicians define the stage and extension of joint involvement and set up a personalised treatment.

Identifiants

pubmed: 38717319
doi: 10.1111/hae.15030
doi:

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Subventions

Organisme : Italian Ministry of Health-Bando Ricerca Corrente
Organisme : Ministero della Salute
Organisme : Bando ricerca corrente
ID : RC2023

Informations de copyright

© 2024 The Authors. Haemophilia published by John Wiley & Sons Ltd.

Références

Bolton‐Maggs PH, Pasi KJ. Haemophilias A and B. Lancet. 2003;361(9371):1801‐1809.
Di Minno MN, Ambrosino P, Franchini M, Coppola A, Di Minno G. Arthropathy in patients with moderate hemophilia a: a systematic review of the literature. Semin Thromb Hemost. 2013;39(7):723‐731.
Gualtierotti R, Solimeno LP, Peyvandi F. Hemophilic arthropathy: current knowledge and future perspectives. J Thromb Haemost. 2021;19(9):2112‐2121.
De la Corte‐Rodriguez H, Rodriguez‐Merchan EC, Alvarez‐Roman MT, Martin‐Salces M, Martinoli C, Jimenez‐Yuste V. HJHS 2.1 and HEAD‐US assessment in the hemophilic joints: how do their findings compare? Blood Coagul Fibrinolysis. 2020;31(6):387‐392.
Srivastava A, Santagostino E, Dougall A, et al. WFH Guidelines for the management of hemophilia. Haemophilia. 2020;26(suppl 6):1‐158.
Nguyen S, Lu X, Ma Y, Du J, Chang EY, von Drygalski A. Musculoskeletal ultrasound for intra‐articular bleed detection: a highly sensitive imaging modality compared with conventional magnetic resonance imaging. J Thromb Haemost. 2018;16(3):490‐499.
Hooiveld MJ, Roosendaal G, Vianen ME, van den Berg HM, Bijlsma JW, Lafeber FP. Immature articular cartilage is more susceptible to blood‐induced damage than mature articular cartilage: an in vivo animal study. Arthritis Rheum. 2003;48(2):396‐403.
Manco‐Johnson MJ, Abshire TC, Shapiro AD, et al. Prophylaxis versus episodic treatment to prevent joint disease in boys with severe hemophilia. N Engl J Med. 2007;357(6):535‐544.
Rubak P, Nissen PH, Kristensen SD, Hvas AM. Investigation of platelet function and platelet disorders using flow cytometry. Platelets. 2016;27(1):66‐74.
Feldman BM, Funk SM, Bergstrom BM, et al. Validation of a new pediatric joint scoring system from the International Hemophilia Prophylaxis Study Group: validity of the hemophilia joint health score. Arthritis Care Res (Hoboken). 2011;63(2):223‐230.
St‐Louis J, Abad A, Funk S, et al. The Hemophilia Joint Health Score version 2.1 Validation in Adult Patients Study: a multicenter international study. Res Pract Thromb Haemost. 2022;6(2):e12690.
Martinoli C, Della Casa Alberighi O, Di Minno G, et al. Development and definition of a simplified scanning procedure and scoring method for Haemophilia Early Arthropathy Detection with Ultrasound (HEAD‐US). Thromb Haemost. 2013;109(6):1170‐1179.
Foppen W, van der Schaaf IC, Fischer K. Value of routine ultrasound in detecting early joint changes in children with haemophilia using the ‘Haemophilia Early Arthropathy Detection with UltraSound’ protocol. Haemophilia. 2016;22(1):121‐125.
Fischer K, Poonnoose P, Dunn AL, et al. Choosing outcome assessment tools in haemophilia care and research: a multidisciplinary perspective. Haemophilia. 2017;23(1):11‐24.
Vandenbroucke JP, von Elm E, Altman DG, et al. Strengthening the Reporting of Observational Studies in Epidemiology (STROBE): explanation and elaboration. PLoS Medicine. 2007;4(10):e297.
Blanchette VS, Key NS, Ljung LR, Manco‐Johnson MJ, van den Berg HM, Srivastava A. Definitions in hemophilia: communication from the SSC of the ISTH. J Thromb Haemost. 2014;12(11):1935‐1939.
Wang M, Batt K, Kessler C, et al. Internal consistency and item‐total correlation of patient‐reported outcome instruments and hemophilia joint health score v2.1 in US adult people with hemophilia: results from the Pain, Functional Impairment, and Quality of life (P‐FiQ) study. Patient Prefer Adherence. 2017;11:1831‐1839.
O'Hara J, Walsh S, Camp C, et al. The impact of severe haemophilia and the presence of target joints on health‐related quality‐of‐life. Health Qual Life Outcomes. 2018;16(1):84.
Guha A, Rai A, Nandy A, et al. Joint scores in hemophilic arthropathy in children: developing country perspectives. Eur J Rheumatol. 2020;7(1):26‐30.
Prasetyo M, Moniqa R, Tulaar A, Prihartono J, Setiawan SI. Correlation between Hemophilia Early Arthropathy Detection with Ultrasound (HEAD‐US) score and Hemophilia Joint Health Score (HJHS) in patients with hemophilic arthropathy. PLoS ONE. 2021;16(4):e0248952.
Timmer MA, Foppen W, Schutgens RE, Pisters MF, Fischer K. Comparing findings of routine Haemophilia Joint Health Score and Haemophlia Early Arthropathy Detection with UltraSound assessments in adults with haemophilia. Haemophilia. 2017;23(2):e141‐e143.

Auteurs

Roberta Gualtierotti (R)

Fondazione IRCCS Ca' Granda Ospedale Maggiore Policlinico, Angelo Bianchi Bonomi Hemophilia and Thrombosis Center, Milan, Italy.
Department of Pathophysiology and Transplantation, Università degli Studi di Milano, Milan, Italy.

Andrea Giachi (A)

Department of Pathophysiology and Transplantation, Università degli Studi di Milano, Milan, Italy.

Addolorata Truma (A)

Department of Pathophysiology and Transplantation, Università degli Studi di Milano, Milan, Italy.

Sara Arcudi (S)

Fondazione IRCCS Ca' Granda Ospedale Maggiore Policlinico, Angelo Bianchi Bonomi Hemophilia and Thrombosis Center, Milan, Italy.
Department of Pathophysiology and Transplantation, Università degli Studi di Milano, Milan, Italy.

Alessandro Ciavarella (A)

Department of Biomedical Sciences for Health, Università degli Studi di Milano, Milan, Italy.

Paolo Bucciarelli (P)

Fondazione IRCCS Ca' Granda Ospedale Maggiore Policlinico, Angelo Bianchi Bonomi Hemophilia and Thrombosis Center, Milan, Italy.

Dario Consonni (D)

Fondazione IRCCS Ca' Granda Ospedale Maggiore Policlinico, Epidemiology Unit, Milan, Italy.

Elena Boccalandro (E)

Fondazione IRCCS Ca' Granda Ospedale Maggiore Policlinico, Angelo Bianchi Bonomi Hemophilia and Thrombosis Center, Milan, Italy.

Valentina Begnozzi (V)

Fondazione IRCCS Ca' Granda Ospedale Maggiore Policlinico, Angelo Bianchi Bonomi Hemophilia and Thrombosis Center, Milan, Italy.

Luigi Piero Solimeno (LP)

Fondazione IRCCS Ca' Granda Ospedale Maggiore Policlinico, Division of Orthopaedic Surgery and Traumatology, Milan, Italy.

Simona Maria Siboni (SM)

Fondazione IRCCS Ca' Granda Ospedale Maggiore Policlinico, Angelo Bianchi Bonomi Hemophilia and Thrombosis Center, Milan, Italy.

Flora Peyvandi (F)

Fondazione IRCCS Ca' Granda Ospedale Maggiore Policlinico, Angelo Bianchi Bonomi Hemophilia and Thrombosis Center, Milan, Italy.
Department of Pathophysiology and Transplantation, Università degli Studi di Milano, Milan, Italy.

Classifications MeSH