Pregnancy and childbirth in patients with Glanzmann Thrombasthenia.

bleeding disorders platelet disorders pregnancy

Journal

British journal of haematology
ISSN: 1365-2141
Titre abrégé: Br J Haematol
Pays: England
ID NLM: 0372544

Informations de publication

Date de publication:
14 May 2024
Historique:
received: 03 03 2024
accepted: 03 05 2024
medline: 15 5 2024
pubmed: 15 5 2024
entrez: 14 5 2024
Statut: aheadofprint

Résumé

Glanzmann thrombasthenia (GT) is a rare inherited platelet bleeding disorder caused by a quantitative and/or qualitative defect of the αIIbβ3 integrin. Pregnancy and delivery pose special challenges as they entail increased risks of both maternal and foetal bleeding that may be life-threatening. Multidisciplinary management throughout the preconception, intrapartum and peripartum periods is vital to optimize pregnancy outcomes. This Nutshell review focuses on the challenging management of pregnancy and childbirth in patients with GT.

Identifiants

pubmed: 38744450
doi: 10.1111/bjh.19528
doi:

Types de publication

Journal Article Review

Langues

eng

Sous-ensembles de citation

IM

Informations de copyright

© 2024 British Society for Haematology and John Wiley & Sons Ltd.

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Auteurs

Amihai Rottenstreich (A)

Laboratory of Blood and Vascular Biology, Rockefeller University, New York City, New York, USA.
Division of Maternal-Fetal Medicine, Department of Obstetrics and Gynecology, Zucker School of Medicine at Hofstra/Northwell, New York City, New York, USA.
Department of Obstetrics and Gynecology, Hadassah-Hebrew University Medical Center, Jerusalem, Israel.
Faculty of Medicine, Hebrew University of Jerusalem, Jerusalem, Israel.

Barry S Coller (BS)

Laboratory of Blood and Vascular Biology, Rockefeller University, New York City, New York, USA.

Classifications MeSH