Abdominal wall congenital infantile fibrosarcoma: A rare case report and literature review.

Abdominal wall mass Ethiopia Infantile fibrosarcoma Pediatric soft tissue sarcoma

Journal

Radiology case reports
ISSN: 1930-0433
Titre abrégé: Radiol Case Rep
Pays: Netherlands
ID NLM: 101467888

Informations de publication

Date de publication:
Aug 2024
Historique:
received: 15 09 2023
revised: 17 04 2024
accepted: 19 04 2024
medline: 23 5 2024
pubmed: 23 5 2024
entrez: 23 5 2024
Statut: epublish

Résumé

Congenital infantile fibrosarcoma is a rare malignant soft tissue tumor, accounting for less than 1%-2% of childhood cancers. Although it can arise from any body part, an abdominal wall origin is exceptionally rare. This case report presents a case of congenital infantile fibrosarcoma originating from the abdominal wall. To the best of our knowledge, this is only the second reported case of abdominal wall congenital infantile fibrosarcoma. Unlike adult fibrosarcoma, infantile fibrosarcoma has a good prognosis with less metastasis. Early diagnosis and management are critical for improving outcomes in such rare cases.

Identifiants

pubmed: 38779193
doi: 10.1016/j.radcr.2024.04.047
pii: S1930-0433(24)00347-9
pmc: PMC11109291
doi:

Types de publication

Case Reports

Langues

eng

Pagination

3176-3179

Informations de copyright

© 2024 The Authors. Published by Elsevier Inc. on behalf of University of Washington.

Auteurs

Yodit Abraham Yaynishet (YA)

Addis Ababa University, College of Health Sciences, Department of Radiology, Addis Ababa, Ethiopia.

Fathia Omer Salah (FO)

Addis Ababa University, College of Health Sciences, Department of Radiology, Addis Ababa, Ethiopia.

Hermon Miliard Derbew (HM)

Addis Ababa University, College of Health Sciences, Department of Radiology, Addis Ababa, Ethiopia.
Childrens Hospital of Philadelphia, Department of Radiology, Philadelphia, PA, USA.

Abel Hailu (A)

Addis Ababa University, College of Health Sciences, Department of Pediatric Hematology/Oncology, Addis Ababa, Ethiopia.

Diriba Fufa (D)

Jimma University, Department of Pediatric and Child Health, Jimma, Ethiopia.

Abdo Kedir Abafogi (AK)

Jimma University, Department of Pathology, Jimma, Ethiopia.

Hailu Alemu (H)

Jimma University, Department of Pediatric and Child Health, Jimma, Ethiopia.

Classifications MeSH