Abdominal wall congenital infantile fibrosarcoma: A rare case report and literature review.
Abdominal wall mass
Ethiopia
Infantile fibrosarcoma
Pediatric soft tissue sarcoma
Journal
Radiology case reports
ISSN: 1930-0433
Titre abrégé: Radiol Case Rep
Pays: Netherlands
ID NLM: 101467888
Informations de publication
Date de publication:
Aug 2024
Aug 2024
Historique:
received:
15
09
2023
revised:
17
04
2024
accepted:
19
04
2024
medline:
23
5
2024
pubmed:
23
5
2024
entrez:
23
5
2024
Statut:
epublish
Résumé
Congenital infantile fibrosarcoma is a rare malignant soft tissue tumor, accounting for less than 1%-2% of childhood cancers. Although it can arise from any body part, an abdominal wall origin is exceptionally rare. This case report presents a case of congenital infantile fibrosarcoma originating from the abdominal wall. To the best of our knowledge, this is only the second reported case of abdominal wall congenital infantile fibrosarcoma. Unlike adult fibrosarcoma, infantile fibrosarcoma has a good prognosis with less metastasis. Early diagnosis and management are critical for improving outcomes in such rare cases.
Identifiants
pubmed: 38779193
doi: 10.1016/j.radcr.2024.04.047
pii: S1930-0433(24)00347-9
pmc: PMC11109291
doi:
Types de publication
Case Reports
Langues
eng
Pagination
3176-3179Informations de copyright
© 2024 The Authors. Published by Elsevier Inc. on behalf of University of Washington.