B-cell prolymphocytic leukemia: an enduring bona fide entity.

B-cell prolymphocytic leukemia Lymphoproliferative disorders Prolymphocytes

Journal

International journal of hematology
ISSN: 1865-3774
Titre abrégé: Int J Hematol
Pays: Japan
ID NLM: 9111627

Informations de publication

Date de publication:
26 May 2024
Historique:
received: 25 01 2024
accepted: 08 04 2024
revised: 03 04 2024
medline: 26 5 2024
pubmed: 26 5 2024
entrez: 26 5 2024
Statut: aheadofprint

Résumé

B-cell prolymphocytic leukemia (B-PLL) was recognized as a distinct entity in the fourth edition of the World Health Organization (WHO) classification for hematolymphoid neoplasms (WHO-HAEM4); however, its de novo presentation has been removed from the upcoming 5th edition classification (WHO-HAEM5). We present a case of a 65-year-old man with leukocytosis, fatigue, and no organomegaly by imaging. Bone marrow examination showed a prolymphocytoid population comprising 78% of the marrow elements. After thorough exclusion of other entities by clinical parameters and ancillary methods, we concluded that this case represents a de novo case of B-PLL.

Identifiants

pubmed: 38796826
doi: 10.1007/s12185-024-03774-4
pii: 10.1007/s12185-024-03774-4
doi:

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Informations de copyright

© 2024. Japanese Society of Hematology.

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Auteurs

Miguel S Gonzalez-Mancera (MS)

Department of Pathology and Laboratory Medicine, Cedars-Sinai Medical Center, 8700 Beverly Blvd, South Tower, Room 4707, Los Angeles, USA.

Jean Lopategui (J)

Department of Pathology and Laboratory Medicine, Cedars-Sinai Medical Center, 8700 Beverly Blvd, South Tower, Room 4707, Los Angeles, USA.

David Hoffman (D)

Tower Hematology Oncology Medical Group, Cedars-Sinai Medical Center, 9090 Wilshire Blvd #300, Beverly Hills, USA.

Sumire Kitahara (S)

Department of Pathology and Laboratory Medicine, Cedars-Sinai Medical Center, 8700 Beverly Blvd, South Tower, Room 4707, Los Angeles, USA.

Serhan Alkan (S)

Department of Pathology and Laboratory Medicine, Cedars-Sinai Medical Center, 8700 Beverly Blvd, South Tower, Room 4707, Los Angeles, USA. Serhan.alkan@cshs.org.

Classifications MeSH