REM sleep behavior disorder in Brunner syndrome.

Brunner syndrome MAOA Monoamine Oxidase-A REM sleep behavior disorder deficiency genetic disorder mutation

Journal

Journal of clinical sleep medicine : JCSM : official publication of the American Academy of Sleep Medicine
ISSN: 1550-9397
Titre abrégé: J Clin Sleep Med
Pays: United States
ID NLM: 101231977

Informations de publication

Date de publication:
17 Jun 2024
Historique:
medline: 17 6 2024
pubmed: 17 6 2024
entrez: 17 6 2024
Statut: aheadofprint

Résumé

Brunner syndrome is a recessive X-linked disorder characterized by intellectual disability and impulsive aggressiveness associated with Monoamine Oxidase-A (MAOA) deficiency leading to increased monoaminergic activity. We report the presence of REM sleep behavior disorder (RBD) in a 46-year-old patient with Brunner syndrome due to a c.1438A>G/iVS14-2 A>G mutation of the

Identifiants

pubmed: 38881510
doi: 10.5664/jcsm.11230
doi:

Types de publication

Case Reports Journal Article

Langues

eng

Sous-ensembles de citation

IM

Informations de copyright

© 2024 American Academy of Sleep Medicine.

Auteurs

Eduard Cesari (E)

Department of Psychiatry, Hospital Clínic de Barcelona, Barcelona, Spain.

Amaia Muñoz-Lopetegi (A)

Department of Neurology, Hospital Clínic de Barcelona, Barcelona, Spain.
Sleep Disorders Center, Hospital Clínic de Barcelona, Barcelona, Spain.

Joan Santamaria (J)

Department of Neurology, Hospital Clínic de Barcelona, Barcelona, Spain.
Sleep Disorders Center, Hospital Clínic de Barcelona, Barcelona, Spain.

Alex Iranzo (A)

Department of Neurology, Hospital Clínic de Barcelona, Barcelona, Spain.
Sleep Disorders Center, Hospital Clínic de Barcelona, Barcelona, Spain.

Carles Gaig (C)

Department of Neurology, Hospital Clínic de Barcelona, Barcelona, Spain.
Sleep Disorders Center, Hospital Clínic de Barcelona, Barcelona, Spain.

Classifications MeSH