Human Genetics of Ebstein Anomaly.


Journal

Advances in experimental medicine and biology
ISSN: 0065-2598
Titre abrégé: Adv Exp Med Biol
Pays: United States
ID NLM: 0121103

Informations de publication

Date de publication:
2024
Historique:
medline: 17 6 2024
pubmed: 17 6 2024
entrez: 17 6 2024
Statut: ppublish

Résumé

Ebstein anomaly (EA) is a rare, congenital cardiac defect of the tricuspid valve with a birth prevalence between 0.5 and 1 in 20,000 [1]. It is characterized by displacement of the tricuspid valve toward the apex of the right ventricle (RV) and "atrialization" of the RV (Fig. 57.1) [2]. EA accounts for about 0.5% of all congenital heart diseases (CHD) [2]. Depending on severity of the defect and due to heterogeneity of the disease, patient's presentation varies from severe heart failure symptoms and arrhythmia in neonatal life to asymptomatic adults.

Identifiants

pubmed: 38884759
doi: 10.1007/978-3-031-44087-8_57
doi:

Types de publication

Journal Article Review

Langues

eng

Sous-ensembles de citation

IM

Pagination

909-914

Informations de copyright

© 2024. The Author(s), under exclusive license to Springer Nature Switzerland AG.

Références

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Auteurs

Farbod Sedaghat-Hamedani (F)

Institute for Cardiomyopathies Heidelberg (ICH), University Hospital Heidelberg, Heidelberg, Germany.

Benjamin Meder (B)

Institute for Cardiomyopathies Heidelberg, Universitätsklinikum Heidelberg, Innere Medizin III - Kardiologie, Angiologie und Pneumologie, Heidelberg, Germany. benjamin.meder@med.uni-heidelberg.de.

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