Benefits for children with suspected cancer from routine whole-genome sequencing.


Journal

Nature medicine
ISSN: 1546-170X
Titre abrégé: Nat Med
Pays: United States
ID NLM: 9502015

Informations de publication

Date de publication:
02 Jul 2024
Historique:
received: 20 11 2023
accepted: 08 05 2024
medline: 3 7 2024
pubmed: 3 7 2024
entrez: 2 7 2024
Statut: aheadofprint

Résumé

Clinical whole-genome sequencing (WGS) has been shown to deliver potential benefits to children with cancer and to alter treatment in high-risk patient groups. It remains unknown whether offering WGS to every child with suspected cancer can change patient management. We collected WGS variant calls and clinical and diagnostic information from 281 children (282 tumors) across two English units (n = 152 from a hematology center, n = 130 from a solid tumor center) where WGS had become a routine test. Our key finding was that variants uniquely attributable to WGS changed the management in ~7% (20 out of 282) of cases while providing additional disease-relevant findings, beyond standard-of-care molecular tests, in 108 instances for 83 (29%) cases. Furthermore, WGS faithfully reproduced every standard-of-care molecular test (n = 738) and revealed several previously unknown genomic features of childhood tumors. We show that WGS can be delivered as part of routine clinical care to children with suspected cancer and can change clinical management by delivering unexpected genomic insights. Our experience portrays WGS as a clinically impactful assay for routine practice, providing opportunities for assay consolidation and for delivery of molecularly informed patient care.

Identifiants

pubmed: 38956197
doi: 10.1038/s41591-024-03056-w
pii: 10.1038/s41591-024-03056-w
doi:

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Subventions

Organisme : Wellcome Trust (Wellcome)
ID : 220540/Z/20/A and 223135/Z/21/Z

Informations de copyright

© 2024. The Author(s).

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Auteurs

Angus Hodder (A)

Great Ormond Street Hospital NHS Foundation Trust, London, UK.

Sarah M Leiter (SM)

Wellcome Sanger Institute, Hinxton, UK.
Cambridge University Hospitals NHS Foundation Trust, Cambridge, UK.
Department of Paediatrics, University of Cambridge, Cambridge, UK.

Jonathan Kennedy (J)

Great Ormond Street Hospital NHS Foundation Trust, London, UK.
Wellcome Sanger Institute, Hinxton, UK.
Cambridge University Hospitals NHS Foundation Trust, Cambridge, UK.
Department of Paediatrics, University of Cambridge, Cambridge, UK.

Dilys Addy (D)

Great Ormond Street Hospital NHS Foundation Trust, London, UK.

Munaza Ahmed (M)

Great Ormond Street Hospital NHS Foundation Trust, London, UK.

Thankamma Ajithkumar (T)

Cambridge University Hospitals NHS Foundation Trust, Cambridge, UK.

Kieren Allinson (K)

Cambridge University Hospitals NHS Foundation Trust, Cambridge, UK.

Phil Ancliff (P)

Great Ormond Street Hospital NHS Foundation Trust, London, UK.

Shivani Bailey (S)

Cambridge University Hospitals NHS Foundation Trust, Cambridge, UK.

Gemma Barnard (G)

Cambridge University Hospitals NHS Foundation Trust, Cambridge, UK.
Department of Paediatrics, University of Cambridge, Cambridge, UK.

G A Amos Burke (GAA)

Cambridge University Hospitals NHS Foundation Trust, Cambridge, UK.
Department of Paediatrics, University of Cambridge, Cambridge, UK.

Charlotte Burns (C)

Cambridge University Hospitals NHS Foundation Trust, Cambridge, UK.

Julian Cano-Flanagan (J)

Great Ormond Street Hospital NHS Foundation Trust, London, UK.

Jane Chalker (J)

North Thames Genomic Laboratory Hub, London, UK.

Nicholas Coleman (N)

Cambridge University Hospitals NHS Foundation Trust, Cambridge, UK.
Department of Pathology, University of Cambridge, Cambridge, UK.

Danny Cheng (D)

Great Ormond Street Hospital NHS Foundation Trust, London, UK.

Yasmin Clinch (Y)

North Thames Genomic Laboratory Hub, London, UK.

Caryl Dryden (C)

Great Ormond Street Hospital NHS Foundation Trust, London, UK.

Sara Ghorashian (S)

Great Ormond Street Hospital NHS Foundation Trust, London, UK.
UCL Great Ormond Street Institute of Child Health, London, UK.

Blanche Griffin (B)

Great Ormond Street Hospital NHS Foundation Trust, London, UK.
North Thames Genomic Laboratory Hub, London, UK.

Gail Horan (G)

Cambridge University Hospitals NHS Foundation Trust, Cambridge, UK.

Michael Hubank (M)

North Thames Genomic Laboratory Hub, London, UK.
The Institute of Cancer Research, London, UK.

Phillippa May (P)

Great Ormond Street Hospital NHS Foundation Trust, London, UK.

Joanna McDerra (J)

Great Ormond Street Hospital NHS Foundation Trust, London, UK.

Rajvi Nagrecha (R)

Great Ormond Street Hospital NHS Foundation Trust, London, UK.

James Nicholson (J)

Cambridge University Hospitals NHS Foundation Trust, Cambridge, UK.
Department of Paediatrics, University of Cambridge, Cambridge, UK.

David O'Connor (D)

Great Ormond Street Hospital NHS Foundation Trust, London, UK.
UCL Cancer Institute, University College London, London, UK.

Vesna Pavasovic (V)

Great Ormond Street Hospital NHS Foundation Trust, London, UK.

Annelies Quaegebeur (A)

Cambridge University Hospitals NHS Foundation Trust, Cambridge, UK.
Department of Clinical Neurosciences, University of Cambridge, Cambridge, UK.

Anupama Rao (A)

Great Ormond Street Hospital NHS Foundation Trust, London, UK.

Thomas Roberts (T)

Cambridge University Hospitals NHS Foundation Trust, Cambridge, UK.
East Genomics Laboratory Hub, Cambridge, UK.

Sujith Samarasinghe (S)

Great Ormond Street Hospital NHS Foundation Trust, London, UK.

Iryna Stasevich (I)

Great Ormond Street Hospital NHS Foundation Trust, London, UK.

John A Tadross (JA)

Cambridge University Hospitals NHS Foundation Trust, Cambridge, UK.
East Genomics Laboratory Hub, Cambridge, UK.
MRC Metabolic Diseases Unit, Wellcome Trust-Medical Research Council Institute of Metabolic Science, University of Cambridge, Cambridge, UK.

Claire Trayers (C)

Cambridge University Hospitals NHS Foundation Trust, Cambridge, UK.

Jamie Trotman (J)

Cambridge University Hospitals NHS Foundation Trust, Cambridge, UK.
East Genomics Laboratory Hub, Cambridge, UK.

Ajay Vora (A)

Great Ormond Street Hospital NHS Foundation Trust, London, UK.

James Watkins (J)

Cambridge University Hospitals NHS Foundation Trust, Cambridge, UK.
Department of Pathology, University of Cambridge, Cambridge, UK.
East Genomics Laboratory Hub, Cambridge, UK.

Lyn S Chitty (LS)

Great Ormond Street Hospital NHS Foundation Trust, London, UK.
North Thames Genomic Laboratory Hub, London, UK.
UCL Great Ormond Street Institute of Child Health, London, UK.

Sarah Bowdin (S)

Cambridge University Hospitals NHS Foundation Trust, Cambridge, UK.
East Genomics Laboratory Hub, Cambridge, UK.

Ruth Armstrong (R)

Cambridge University Hospitals NHS Foundation Trust, Cambridge, UK.

Matthew J Murray (MJ)

Cambridge University Hospitals NHS Foundation Trust, Cambridge, UK. mjm16@cam.ac.uk.
Department of Pathology, University of Cambridge, Cambridge, UK. mjm16@cam.ac.uk.

Catherine E Hook (CE)

Cambridge University Hospitals NHS Foundation Trust, Cambridge, UK. lizhook@nhs.net.
Department of Pathology, University of Cambridge, Cambridge, UK. lizhook@nhs.net.

Patrick Tarpey (P)

Cambridge University Hospitals NHS Foundation Trust, Cambridge, UK. patrick.tarpey1@nhs.net.
East Genomics Laboratory Hub, Cambridge, UK. patrick.tarpey1@nhs.net.

Aditi Vedi (A)

Cambridge University Hospitals NHS Foundation Trust, Cambridge, UK. a.vedi@nhs.net.
Department of Paediatrics, University of Cambridge, Cambridge, UK. a.vedi@nhs.net.

Jack Bartram (J)

Great Ormond Street Hospital NHS Foundation Trust, London, UK. jack.bartram@gosh.nhs.uk.
North Thames Genomic Laboratory Hub, London, UK. jack.bartram@gosh.nhs.uk.

Sam Behjati (S)

Wellcome Sanger Institute, Hinxton, UK. sb31@sanger.ac.uk.
Cambridge University Hospitals NHS Foundation Trust, Cambridge, UK. sb31@sanger.ac.uk.
Department of Paediatrics, University of Cambridge, Cambridge, UK. sb31@sanger.ac.uk.

Classifications MeSH