'Hot phase' non-dilated left ventricular cardiomyopathy with atypical onset and recurrence: a case report.

Cardiac magnetic resonance Cardiomyopathy Endomyocardial biopsy Multimodality imaging

Journal

ESC heart failure
ISSN: 2055-5822
Titre abrégé: ESC Heart Fail
Pays: England
ID NLM: 101669191

Informations de publication

Date de publication:
12 Jul 2024
Historique:
revised: 18 03 2024
received: 21 10 2023
accepted: 02 04 2024
medline: 13 7 2024
pubmed: 13 7 2024
entrez: 13 7 2024
Statut: aheadofprint

Résumé

Non-dilated left ventricular cardiomyopathy (NDLVC) is a newly categorized cardiomyopathy phenotype includingseveral aetiologies with a linking characteristic represented by the normal left ventricular volume. Inflammatory heart disease (InHD) is a heterogeneous process with variegate clinical manifestations, sometimes in overlap with NDLVC. A 26-year-old woman was admitted forcomplete heart block (CHB) and persistently raised troponin. Echocardiography and coronary angiography were normal. Extensive oedema and late gadolinium enhancement was found at cardiac magnetic resonance. Endomyocardial biopsy showed no signs of active myocarditis. Steroid therapy was started with restoration of atrioventricular conduction but subsequently the patient experienced a mild recurrence with a new troponin relapse. Genetic test was negative for mutations related with the clinical scenario. In this case of NDLVC with InHD the precise diagnostic work-up, including genetic test, was crucial for diagnostic, prognostic andtherapeutic purposes. Multimodality approach is crucial to detect and treat possible recurrences.

Identifiants

pubmed: 39001591
doi: 10.1002/ehf2.14822
doi:

Types de publication

Case Reports Journal Article

Langues

eng

Sous-ensembles de citation

IM

Informations de copyright

© 2024 The Authors. ESC Heart Failure published by John Wiley & Sons Ltd on behalf of European Society of Cardiology.

Références

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Auteurs

Nicola Gonano (N)

Department of Cardiothoracovascular, Azienda Sanitaria Universitaria Integrata Giuliana Isontina (ASUGI), University of Trieste, Trieste, Italy.
Department of Cardiology, Santa Maria degli Angeli Hospital, Azienda Sanitaria Friuli Orientale (ASFO), Pordenone, Italy.

Vincenzo Nuzzi (V)

Clinical Cardiology and Heart Failure Unit, Mediterranean Institute for Transplantation and Advanced Specialized Therapies (ISMETT), Palermo, Italy.

Daniela Pavan (D)

Department of Cardiology, Santa Maria degli Angeli Hospital, Azienda Sanitaria Friuli Orientale (ASFO), Pordenone, Italy.

Rita Piazza (R)

Department of Cardiology, Santa Maria degli Angeli Hospital, Azienda Sanitaria Friuli Orientale (ASFO), Pordenone, Italy.

Rosa Pecoraro (R)

Department of Cardiology, Santa Maria degli Angeli Hospital, Azienda Sanitaria Friuli Orientale (ASFO), Pordenone, Italy.

Alessandro Altinier (A)

Department of Cardiothoracovascular, Azienda Sanitaria Universitaria Integrata Giuliana Isontina (ASUGI), University of Trieste, Trieste, Italy.

Rossana Bussani (R)

Institute of Pathological Anatomy and Histology, Azienda Sanitaria Universitaria Giuliano-Isontina (ASUGI), University of Trieste, Trieste, Italy.

Gianfranco Sinagra (G)

Department of Cardiothoracovascular, Azienda Sanitaria Universitaria Integrata Giuliana Isontina (ASUGI), University of Trieste, Trieste, Italy.

Marco Merlo (M)

Department of Cardiothoracovascular, Azienda Sanitaria Universitaria Integrata Giuliana Isontina (ASUGI), University of Trieste, Trieste, Italy.

Classifications MeSH