A Transoral Approach to Decompression Odontoidectomy With Posterior Wiring and Fusion for Pediatric Platybasia With Chiari Malformation.

atlantoaxial basilar chiari craniovertebral invagination osteogenesis

Journal

Cureus
ISSN: 2168-8184
Titre abrégé: Cureus
Pays: United States
ID NLM: 101596737

Informations de publication

Date de publication:
Jun 2024
Historique:
accepted: 19 06 2024
medline: 22 7 2024
pubmed: 22 7 2024
entrez: 22 7 2024
Statut: epublish

Résumé

Basilar invagination in a Chiari malformation associated with osteogenesis imperfecta in the pediatric population is a rare entity. We report a case of a seven-year-old female who presented with sudden-onset bilateral spastic quadriplegia and evidence of a basilar invagination on MRI. She underwent emergency decompression of the impinging odontoid via transoral approach followed by posterior wiring and fusion of the C1 and C2 vertebrae. Imaging modalities such as dynamic CT and MRI play a major role in delineating any craniovertebral anomalies and neural impingement not easily identified in plain radiographs. Understanding the complex craniovertebral junction (CVJ) anatomy and the possible causes of such deformities is vital for ensuring proper diagnosis and management of these patients.

Identifiants

pubmed: 39036121
doi: 10.7759/cureus.62754
pmc: PMC11259996
doi:

Types de publication

Case Reports Journal Article

Langues

eng

Pagination

e62754

Informations de copyright

Copyright © 2024, Zainudin et al.

Déclaration de conflit d'intérêts

Human subjects: Consent was obtained or waived by all participants in this study. Conflicts of interest: In compliance with the ICMJE uniform disclosure form, all authors declare the following: Payment/services info: All authors have declared that no financial support was received from any organization for the submitted work. Financial relationships: All authors have declared that they have no financial relationships at present or within the previous three years with any organizations that might have an interest in the submitted work. Other relationships: All authors have declared that there are no other relationships or activities that could appear to have influenced the submitted work.

Auteurs

Nur Aidurra Zainudin (NA)

Orthopaedics and Traumatology, Hospital Universiti Kebangsaan Malaysia, Kuala Lumpur, MYS.

Mohd Hisam Muhamad Ariffin (MH)

Spine Surgery, Universiti Kebangsaan Malaysia Medical Centre, Kuala Lumpur, MYS.

Classifications MeSH