NF1-dependent disruption of the blood-nerve-barrier is improved by blockade of P2RY14.

biological sciences molecular neuroscience neuroscience

Journal

iScience
ISSN: 2589-0042
Titre abrégé: iScience
Pays: United States
ID NLM: 101724038

Informations de publication

Date de publication:
19 Jul 2024
Historique:
received: 10 06 2022
revised: 17 12 2023
accepted: 14 06 2024
medline: 5 8 2024
pubmed: 5 8 2024
entrez: 5 8 2024
Statut: epublish

Résumé

The blood-nerve-barrier (BNB) that regulates peripheral nerve homeostasis is formed by endoneurial capillaries and perineurial cells surrounding the Schwann cell (SC)-rich endoneurium. Barrier dysfunction is common in human tumorigenesis, including in some nerve tumors. We identify barrier disruption in human

Identifiants

pubmed: 39100928
doi: 10.1016/j.isci.2024.110294
pii: S2589-0042(24)01519-0
pmc: PMC11294707
doi:

Types de publication

Journal Article

Langues

eng

Pagination

110294

Informations de copyright

© 2024 The Authors.

Déclaration de conflit d'intérêts

Some research in the N.R. lab is funded by Revolution Meidicines and Boehringer Ingelheim, unrelated to this study. D.A.L. is the co-founder and co-owner of NeoClone Biotechnologies, Inc., Discovery Genomics, Inc. (recently acquired by Immusoft, Inc.), B-MoGen Biotechnologies, Inc. (recently acquired by Bio-Techne Corporation), and Luminary Therapeutics, Inc. D.A.L. holds equity in, serves as a Senior Scientific Advisor for and Board of Director member for Recombinetics, a genome editing company. The business of all these companies is unrelated to the contents of this manuscript. D.A.L. consults for Styx Therapeutics, Inc. and 10.13039/100004328Genentech, Inc., which is funding some of his research.

Auteurs

Jennifer Patritti-Cram (J)

Division of Experimental Hematology and Cancer Biology, Cancer & Blood Diseases Institute, Cincinnati Children's Hospital Medical Center, Cincinnati, OH 45229, USA.
Neuroscience Graduate Program, University of Cincinnati College of Medicine, Cincinnati, OH 45267-0713, USA.

Eric P Rahrmann (EP)

Cancer Research UK Cambridge Institute, University of Cambridge, Cambridge, UK.

Tilat A Rizvi (TA)

Division of Experimental Hematology and Cancer Biology, Cancer & Blood Diseases Institute, Cincinnati Children's Hospital Medical Center, Cincinnati, OH 45229, USA.

Katherine C Scheffer (KC)

Division of Experimental Hematology and Cancer Biology, Cancer & Blood Diseases Institute, Cincinnati Children's Hospital Medical Center, Cincinnati, OH 45229, USA.

Timothy N Phoenix (TN)

Division of Pharmaceutical Sciences, James L. Wrinkle College of Pharmacy, University of Cincinnati, Cincinnati, OH 45229, USA.

David A Largaespada (DA)

Department of Pediatrics, Masonic Cancer Center, University of Minnesota, Minneapolis, MN 55455, USA.

Nancy Ratner (N)

Division of Experimental Hematology and Cancer Biology, Cancer & Blood Diseases Institute, Cincinnati Children's Hospital Medical Center, Cincinnati, OH 45229, USA.
Department of Pediatrics, University of Cincinnati College of Medicine, Cincinnati, OH 45267, USA.

Classifications MeSH