[Fatal outcome of complete resection of undifferentiated pleomorphic cardiac sarcoma : About a case].
Évolution fatale d'une résection complète d'un sarcome cardiaque pléomorphe indifférencié : à propos d'un cas.
Complete resection of a pleomorphic undifferentiated cardiac sarcoma
Le sarcome cardiaque pléomorphe indifférencié
Malignant primary cardiac tumor
Résection complète d'un sarcome cardiaque pléomorphe indifférencié
The pleomorphic undifferentiated cardiac sarcoma
Tumeur cardiaque primitive maligne
Journal
Annales de cardiologie et d'angeiologie
ISSN: 1768-3181
Titre abrégé: Ann Cardiol Angeiol (Paris)
Pays: France
ID NLM: 0142167
Informations de publication
Date de publication:
08 Aug 2024
08 Aug 2024
Historique:
received:
02
04
2024
revised:
17
04
2024
accepted:
17
05
2024
medline:
10
8
2024
pubmed:
10
8
2024
entrez:
9
8
2024
Statut:
aheadofprint
Résumé
Undifferentiated pleomorphic sarcoma (UPS) is a very rare malignant primary cardiac tumor with a poor prognosis. A 34-year-old woman complained of dyspnea evolving in a febrile context with altered general condition: Transthoracic echocardiography (TTE) revealed a left intra-atrial mass measuring 51/26 mm in diameter. A thoracic computed tomography (CT) revealed a mass occupying the left atrium measuring 42/28/34 mm, associated with two pulmonary metastases. The cardiac mass was resected and the postoperative suites were fatal. Histological diagnosis was UPS. We present an atypical case of invasive UPS, which was surgically resected and scheduled for radio-chemotherapy with a fatal outcome.
Identifiants
pubmed: 39121517
pii: S0003-3928(24)00048-9
doi: 10.1016/j.ancard.2024.101769
pii:
doi:
Types de publication
English Abstract
Journal Article
Langues
fre
Sous-ensembles de citation
IM
Pagination
101769Informations de copyright
Copyright © 2024 Elsevier Masson SAS. All rights reserved.
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Déclaration de liens d'intérêts Les auteurs déclarent ne pas avoir le lien d'intérêts.