Optimizing thiopurine therapy in autoimmune hepatitis: A multi-center study on monitoring metabolite profiles and co-therapy with allopurinol.


Journal

Hepatology (Baltimore, Md.)
ISSN: 1527-3350
Titre abrégé: Hepatology
Pays: United States
ID NLM: 8302946

Informations de publication

Date de publication:
29 May 2024
Historique:
received: 09 02 2024
accepted: 09 04 2024
medline: 20 8 2024
pubmed: 20 8 2024
entrez: 20 8 2024
Statut: aheadofprint

Résumé

In autoimmune hepatitis (AIH), achieving complete biochemical remission (CBR) with current weight-based thiopurine dosing is challenging. We investigated whether patients could be stratified regarding CBR according to a target range of thiopurine metabolites. Moreover, we explored the effects of azathioprine dosage increases and co-therapy of allopurinol with low-dose thiopurines on metabolite profiles and treatment response. The relation between metabolites and treatment response was assessed in 337 individuals from four European centers. In a global, cross-sectional analysis, active metabolites 6-thioguanin nucleotides (6TGN) were similar in those with and without CBR. However, analyzing patients with sequential measurements over 4 years (N=146) revealed higher average 6TGN levels in those with stable CBR (260 pmol/0.2 ml) compared to those failing to maintain CBR (181 pmol/0.2 ml;p=0.0014) or never achieving CBR (153 pmol/0.2 ml;p<0.0001), with an optimal 6TGN-cutoff of ≥223 pmol/0.2 ml (sensitivity: 76%, specificity: 78%). Only 42% exhibited 6TGN ≥223 pmol/0.2 ml following weight-based dosing, as doses weakly correlated with 6TGN but with 6-methylmercaptopurine (6MMP), a metabolite associated with toxicity. Azathioprine dose increases led to preferential 6MMP formation (+127% vs. 6TGN +34%;p<0.0001). Conversely, adding allopurinol to thiopurines in difficult-to-treat patients (N=36) raised 6TGN (168→321 pmol/0.2 ml;p<0.0001) and lowered 6MMP (2125→184 pmol/0.2 ml;p<0.0001), resulting in improved transaminases in all patients and long-term CBR in 75%. Maintaining CBR in AIH was associated with 6TGN ≥223 pmol/0.2 ml. For patients who fail to achieve CBR and therapeutic 6TGN levels despite thiopurine dose increase due to preferential 6MMP formation, co-medication of allopurinol alongside low-dose thiopurines represents an efficient alternative.

Sections du résumé

BACKGROUND AIMS UNASSIGNED
In autoimmune hepatitis (AIH), achieving complete biochemical remission (CBR) with current weight-based thiopurine dosing is challenging. We investigated whether patients could be stratified regarding CBR according to a target range of thiopurine metabolites. Moreover, we explored the effects of azathioprine dosage increases and co-therapy of allopurinol with low-dose thiopurines on metabolite profiles and treatment response.
APPROACH RESULTS UNASSIGNED
The relation between metabolites and treatment response was assessed in 337 individuals from four European centers. In a global, cross-sectional analysis, active metabolites 6-thioguanin nucleotides (6TGN) were similar in those with and without CBR. However, analyzing patients with sequential measurements over 4 years (N=146) revealed higher average 6TGN levels in those with stable CBR (260 pmol/0.2 ml) compared to those failing to maintain CBR (181 pmol/0.2 ml;p=0.0014) or never achieving CBR (153 pmol/0.2 ml;p<0.0001), with an optimal 6TGN-cutoff of ≥223 pmol/0.2 ml (sensitivity: 76%, specificity: 78%). Only 42% exhibited 6TGN ≥223 pmol/0.2 ml following weight-based dosing, as doses weakly correlated with 6TGN but with 6-methylmercaptopurine (6MMP), a metabolite associated with toxicity. Azathioprine dose increases led to preferential 6MMP formation (+127% vs. 6TGN +34%;p<0.0001). Conversely, adding allopurinol to thiopurines in difficult-to-treat patients (N=36) raised 6TGN (168→321 pmol/0.2 ml;p<0.0001) and lowered 6MMP (2125→184 pmol/0.2 ml;p<0.0001), resulting in improved transaminases in all patients and long-term CBR in 75%.
CONCLUSIONS CONCLUSIONS
Maintaining CBR in AIH was associated with 6TGN ≥223 pmol/0.2 ml. For patients who fail to achieve CBR and therapeutic 6TGN levels despite thiopurine dose increase due to preferential 6MMP formation, co-medication of allopurinol alongside low-dose thiopurines represents an efficient alternative.

Identifiants

pubmed: 39162583
doi: 10.1097/HEP.0000000000000940
pii: 01515467-990000000-00895
doi:

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Informations de copyright

Copyright © 2024 American Association for the Study of Liver Diseases.

Auteurs

Jan Philipp Weltzsch (JP)

I. Department of Medicine, University Medical Centre Hamburg-Eppendorf (UKE), Hamburg, Germany.
European Reference Network on Hepatological Diseases (ERN RARE-LIVER) Hamburg, Germany.

Claudius F Bartel (CF)

I. Department of Medicine, University Medical Centre Hamburg-Eppendorf (UKE), Hamburg, Germany.

Moritz Waldmann (M)

Institute for Clinical Chemistry and Laboratory Medicine, University Medical Centre Hamburg-Eppendorf (UKE), Hamburg, Germany.

Thomas Renné (T)

Institute for Clinical Chemistry and Laboratory Medicine, University Medical Centre Hamburg-Eppendorf (UKE), Hamburg, Germany.

Stephanie Schulze (S)

I. Department of Medicine, University Medical Centre Hamburg-Eppendorf (UKE), Hamburg, Germany.

Benedetta Terziroli Beretta-Piccoli (B)

Epatocentro Ticino, Lugano, Switzerland.
Faculty of Biochemical Sciences, Università della Svizzera Italiana, Lugano, Switzerland.
Mowat Labs, Faculty of Life Sciences & Medicine, King's College London, King's College Hospital, London, UK.

Maria Papp (M)

University of Debrecen, Faculty of Medicine, Institute of Medicine, Department of Gastroenterology, Debrecen, Hungary.

Oo Ye (O)

European Reference Network on Hepatological Diseases (ERN RARE-LIVER) Hamburg, Germany.
Liver Transplant Unit, Centre for Rare Disease, Birmingham & Centre for Liver and Gastro Research, Institute of Immunology and Immunotherapy, Queen Elizabeth Hospital, University Hospital of Birmingham, University of Birmingham, Birmingham, UK.

Vincenzo Ronca (V)

Liver Transplant Unit, Centre for Rare Disease, Birmingham & Centre for Liver and Gastro Research, Institute of Immunology and Immunotherapy, Queen Elizabeth Hospital, University Hospital of Birmingham, University of Birmingham, Birmingham, UK.

Marcial Sebode (M)

I. Department of Medicine, University Medical Centre Hamburg-Eppendorf (UKE), Hamburg, Germany.
European Reference Network on Hepatological Diseases (ERN RARE-LIVER) Hamburg, Germany.

Ansgar W Lohse (AW)

I. Department of Medicine, University Medical Centre Hamburg-Eppendorf (UKE), Hamburg, Germany.
European Reference Network on Hepatological Diseases (ERN RARE-LIVER) Hamburg, Germany.

Christoph Schramm (C)

I. Department of Medicine, University Medical Centre Hamburg-Eppendorf (UKE), Hamburg, Germany.
European Reference Network on Hepatological Diseases (ERN RARE-LIVER) Hamburg, Germany.
Hamburg Centre for Translational Immunology (HCTI), University Medical Centre Hamburg-Eppendorf, Hamburg, Germany.
Martin Zeitz Centre for Rare Diseases, University Medical Centre Hamburg-Eppendorf, Hamburg, Germany.

Johannes Hartl (J)

I. Department of Medicine, University Medical Centre Hamburg-Eppendorf (UKE), Hamburg, Germany.
European Reference Network on Hepatological Diseases (ERN RARE-LIVER) Hamburg, Germany.

Classifications MeSH