Role of pediatric dentist in West syndrome rehabilitation: A case report.

West syndrome dental rehabilitation under general anesthesia hypsarrhythmia infantile spasms

Journal

Special care in dentistry : official publication of the American Association of Hospital Dentists, the Academy of Dentistry for the Handicapped, and the American Society for Geriatric Dentistry
ISSN: 1754-4505
Titre abrégé: Spec Care Dentist
Pays: United States
ID NLM: 8103755

Informations de publication

Date de publication:
29 Aug 2024
Historique:
revised: 17 08 2024
received: 01 04 2024
accepted: 21 08 2024
medline: 31 8 2024
pubmed: 31 8 2024
entrez: 30 8 2024
Statut: aheadofprint

Résumé

West syndrome is characterized by a triad of infantile spasms, arrested psychomotor development, and pronounced paroxysmal electroencephalogram (EEG) abnormalities, notably hypsarrhythmia. This case report aims to discuss the various considerations and strategies for the dental management of a child with West syndrome. This report focuses on a case of a 5-year-old girl diagnosed with West Syndrome who presented for her first dental visit with complaints of pain and swelling in the right posterior tooth region for the past three weeks. Due to frequent seizure episodes, neuropsychomotor delay, and multiple dental treatment needs, comprehensive full-mouth rehabilitation was performed under general anesthesia. Awareness of syndromes like West syndrome equips dentists to better manage children with complex conditions. Additionally, parental counselling and early preventive measures can significantly reduce the added burden of dental diseases in these patients.

Identifiants

pubmed: 39210530
doi: 10.1111/scd.13059
doi:

Types de publication

Case Reports Journal Article

Langues

eng

Sous-ensembles de citation

IM

Informations de copyright

© 2024 Special Care Dentistry Association and Wiley Periodicals LLC.

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Auteurs

Deepshikha Mehrotra (D)

Department of Pediatric and Preventive Dentistry, D.Y. Patil University School of Dentistry, Navi Mumbai, Maharashtra, India.

Prajna P Nayak (PP)

Department of Pediatric and Preventive Dentistry, AB Shetty Memorial Institute of Dental Sciences (ABSMIDS), NITTE (Deemed to be University), Mangalore, Karnataka, India.

Shilpa Shetty Naik (SS)

Department of Pediatric and Preventive Dentistry, D.Y. Patil University School of Dentistry, Navi Mumbai, Maharashtra, India.

Nidhish Krishna (N)

Department of Pediatric and Preventive Dentistry, AB Shetty Memorial Institute of Dental Sciences (ABSMIDS), NITTE (Deemed to be University), Mangalore, Karnataka, India.

Classifications MeSH