Polyostotic Fibrous Dysplasia: A Case Report.

facial distortion fibrous dysplasia ground glass matrix leontiasis ossea polyostotic

Journal

Cureus
ISSN: 2168-8184
Titre abrégé: Cureus
Pays: United States
ID NLM: 101596737

Informations de publication

Date de publication:
Jul 2024
Historique:
received: 08 04 2024
accepted: 29 07 2024
medline: 1 9 2024
pubmed: 1 9 2024
entrez: 30 8 2024
Statut: epublish

Résumé

Polyostotic fibrous dysplasia (PFD) is a scarce noncancerous bone condition characterized by the failure to form mature lamellar bone and arrest in the form of woven bone, resulting in deformities and functional limitations. Extreme forms of craniofacial fibrous dysplasia can lead to leontiasis ossea, an exceptionally uncommon presentation. We report a case of a 32-year-old man displaying facial abnormalities indicative of leontiasis ossea. Through radiographic and histopathological assessments, the diagnosis of PFD was confirmed. Surgical intervention was undertaken to address symptoms and enhance facial appearance. This case underscores the diagnostic and therapeutic complexities associated with PFD featuring leontiasis ossea and underscores the significance of a collaborative medical approach.

Identifiants

pubmed: 39211650
doi: 10.7759/cureus.65695
pmc: PMC11361471
doi:

Types de publication

Case Reports Journal Article

Langues

eng

Pagination

e65695

Informations de copyright

Copyright © 2024, Aram et al.

Déclaration de conflit d'intérêts

Human subjects: Consent was obtained or waived by all participants in this study. Conflicts of interest: In compliance with the ICMJE uniform disclosure form, all authors declare the following: Payment/services info: All authors have declared that no financial support was received from any organization for the submitted work. Financial relationships: All authors have declared that they have no financial relationships at present or within the previous three years with any organizations that might have an interest in the submitted work. Other relationships: All authors have declared that there are no other relationships or activities that could appear to have influenced the submitted work.

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Auteurs

Arun Aram (A)

Department of Radiology, Saveetha Medical College and Hospital, Saveetha Institute of Medical and Technical Sciences, Saveetha University, Chennai, IND.

Karthik Krishna Ramakrishnan (KK)

Department of Radiology, Saveetha Medical College and Hospital, Saveetha Institute of Medical and Technical Sciences, Saveetha University, Chennai, IND.

Evangeline P Christina (EP)

Department of Radiology, Saveetha Medical College and Hospital, Saveetha Institute of Medical and Technical Sciences, Saveetha University, Chennai, IND.

Paarthipan Natarajan (P)

Department of Radiology, Saveetha Medical College and Hospital, Saveetha Institute of Medical and Technical Sciences, Saveetha University, Chennai, IND.

Classifications MeSH