Both GEF domains of the autism and developmental epileptic encephalopathy-associated Trio protein are required for proper tangential migration of GABAergic interneurons.


Journal

Molecular psychiatry
ISSN: 1476-5578
Titre abrégé: Mol Psychiatry
Pays: England
ID NLM: 9607835

Informations de publication

Date de publication:
19 Sep 2024
Historique:
received: 23 12 2022
accepted: 02 09 2024
revised: 19 08 2024
medline: 20 9 2024
pubmed: 20 9 2024
entrez: 19 9 2024
Statut: aheadofprint

Résumé

Recessive and de novo mutations in the TRIO gene are associated with intellectual deficiency (ID), autism spectrum disorder (ASD) and developmental epileptic encephalopathies (DEE). TRIO is a dual guanine nucleotide exchange factor (GEF) that activates Rac1, Cdc42 and RhoA. Trio has been extensively studied in excitatory neurons, and has recently been found to regulate the switch from tangential to radial migration in GABAergic interneurons (INs) through GEFD1-Rac1-dependent SDF1α/CXCR4 signaling. Given the central role of Rho-GTPases during neuronal migration and the implication of IN pathologies in ASD and DEE, we investigated the relative roles of both Trio's GEF domains in regulating the dynamics of INs tangential migration. In Trio

Identifiants

pubmed: 39300136
doi: 10.1038/s41380-024-02742-y
pii: 10.1038/s41380-024-02742-y
doi:

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Informations de copyright

© 2024. The Author(s).

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Auteurs

Lara Eid (L)

Centre de recherche du CHU Sainte-Justine, 3175 Côte Ste-Catherine, Montréal, QC, H3T 1C5, Canada.
Département de neurosciences, Université de Montréal, Montréal, QC, Canada.

Ludmilla Lokmane (L)

Institut de Biologie de l'ENS (IBENS), École Normale Supérieure, CNRS, INSERM, Université PSL, 75005, Paris, France.

Praveen K Raju (PK)

Centre de recherche du CHU Sainte-Justine, 3175 Côte Ste-Catherine, Montréal, QC, H3T 1C5, Canada.
Département de neurosciences, Université de Montréal, Montréal, QC, Canada.

Samuel Boris Tene Tadoum (SB)

Centre de recherche du CHU Sainte-Justine, 3175 Côte Ste-Catherine, Montréal, QC, H3T 1C5, Canada.
Département de neurosciences, Université de Montréal, Montréal, QC, Canada.

Xiao Jiang (X)

Centre de recherche du CHU Sainte-Justine, 3175 Côte Ste-Catherine, Montréal, QC, H3T 1C5, Canada.

Karolanne Toulouse (K)

Centre de recherche du CHU Sainte-Justine, 3175 Côte Ste-Catherine, Montréal, QC, H3T 1C5, Canada.
Département de neurosciences, Université de Montréal, Montréal, QC, Canada.

Alexis Lupien-Meilleur (A)

Centre de recherche du CHU Sainte-Justine, 3175 Côte Ste-Catherine, Montréal, QC, H3T 1C5, Canada.
Département de neurosciences, Université de Montréal, Montréal, QC, Canada.

François Charron-Ligez (F)

Centre de recherche du CHU Sainte-Justine, 3175 Côte Ste-Catherine, Montréal, QC, H3T 1C5, Canada.

Asmaa Toumi (A)

Centre de recherche du CHU Sainte-Justine, 3175 Côte Ste-Catherine, Montréal, QC, H3T 1C5, Canada.

Stéphanie Backer (S)

Institut Cochin- INSERM, U1016-CNRS UMR 8104-Université Paris Cité -24, rue du Faubourg Saint-Jacques, 75014, Paris, France.

Mathieu Lachance (M)

Centre de recherche du CHU Sainte-Justine, 3175 Côte Ste-Catherine, Montréal, QC, H3T 1C5, Canada.

Marisol Lavertu-Jolin (M)

Centre de recherche du CHU Sainte-Justine, 3175 Côte Ste-Catherine, Montréal, QC, H3T 1C5, Canada.

Marie Montseny (M)

Institut Cochin- INSERM, U1016-CNRS UMR 8104-Université Paris Cité -24, rue du Faubourg Saint-Jacques, 75014, Paris, France.

Jean-Claude Lacaille (JC)

Département de neurosciences, Université de Montréal, Montréal, QC, Canada.
Centre interdisciplinaire de recherche sur le cerveau et l'apprentissage, Groupe de recherche sur la signalisation neurale et la circuiterie, Université de Montréal, Montréal, QC, Canada.

Evelyne Bloch-Gallego (E)

Institut Cochin- INSERM, U1016-CNRS UMR 8104-Université Paris Cité -24, rue du Faubourg Saint-Jacques, 75014, Paris, France. evelyne.bloch-gallego@inserm.fr.

Elsa Rossignol (E)

Centre de recherche du CHU Sainte-Justine, 3175 Côte Ste-Catherine, Montréal, QC, H3T 1C5, Canada. elsa.rossignol@umontreal.ca.
Département de neurosciences, Université de Montréal, Montréal, QC, Canada. elsa.rossignol@umontreal.ca.
Département de Pédiatrie, Université de Montréal, Montréal, QC, Canada. elsa.rossignol@umontreal.ca.

Classifications MeSH