Incidental discovery of asymptomatic low-grade mucinous appendiceal tumor during paraumbilical hernia repair: A case report emphasizing intraoperative vigilance.

Asymptomatic Incidental Low-grade mucinous appendiceal tumor Mucinous appendiceal tumor Paraumbilical hernia

Journal

International journal of surgery case reports
ISSN: 2210-2612
Titre abrégé: Int J Surg Case Rep
Pays: Netherlands
ID NLM: 101529872

Informations de publication

Date de publication:
20 Sep 2024
Historique:
received: 14 08 2024
revised: 15 09 2024
accepted: 19 09 2024
medline: 23 9 2024
pubmed: 23 9 2024
entrez: 22 9 2024
Statut: aheadofprint

Résumé

Mucinous appendiceal tumor is an exceptionally rare and indolent epithelial neoplasm characterized by the production of mucin within the appendix. Here we present a rare case of a large, asymptomatic mucinous appendiceal tumor discovered incidentally during repair of a paraumbilical hernia. A 73-year-old man with a complex medical history presented with epigastric pain, nausea, vomiting, and constipation. Diagnosed with a strangulated paraumbilical hernia. During hernia repair surgery, a low-grade mucinous appendiceal tumor was accidentally discovered. Post-operative monitoring over 18 months, including colonoscopy and CT scans, showed no recurrence. Appendiceal primary tumors, though rare, can originate from neuroendocrine or epithelial cells. Epithelial tumors, including mucinous adenocarcinoma, produce mucin, potentially leading to pseudomyxoma peritonei, characterized by mucinous ascites and abdominal swelling. These tumors are often incidentally discovered during surgery, as symptoms are nonspecific, resembling acute appendicitis or causing abdominal distension. Diagnosis requires histopathology, revealing mucin accumulation and irregular glandular structures. Treatment typically involves cytoreductive surgery with hyperthermic intraperitoneal chemotherapy to manage the condition effectively. This case emphasizes the critical need for intraoperative vigilance and histopathological analysis in detecting appendiceal mucinous tumors during abdominal surgery, ensuring accurate diagnosis and favorable outcomes.

Identifiants

pubmed: 39307026
pii: S2210-2612(24)01110-6
doi: 10.1016/j.ijscr.2024.110329
pii:
doi:

Types de publication

Case Reports Journal Article

Langues

eng

Pagination

110329

Informations de copyright

Copyright © 2024 The Authors. Published by Elsevier Ltd.. All rights reserved.

Déclaration de conflit d'intérêts

Conflict of interest statement The authors disclose no conflicts.

Auteurs

Ahmad Alkheder (A)

Department of Otorhinolaryngology, Al Mouwasat University Hospital, Faculty of Medicine, Damascus University, Damascus, Syria; Faculty of Medicine, Syrian Private University, Damascus, Syria; Faculty of Medicine, Damascus University, Damascus, Syria. Electronic address: alkhederahmed@gmail.com.

Ibrahim Fathallah (I)

Faculty of Medicine, Al-Baath University, Homs, Syria.

Abd Alrhman Alajrd (AA)

Faculty of Medicine, Al-Baath University, Homs, Syria.

Zeina Alsodi (Z)

Faculty of Medicine, Damascus University, Damascus, Syria.

Majed Abdul Karim Rahal (MAK)

Faculty of Medicine, Aleppo Universit, Aleppo, Syria; Abha Private Hospital, Abha, Saudi Arabia.

Classifications MeSH