Classification of

Genetic Predisposition to Disease Genetics, Medical Mutation, Missense

Journal

Journal of medical genetics
ISSN: 1468-6244
Titre abrégé: J Med Genet
Pays: England
ID NLM: 2985087R

Informations de publication

Date de publication:
02 Oct 2024
Historique:
received: 11 03 2024
accepted: 30 08 2024
medline: 3 10 2024
pubmed: 3 10 2024
entrez: 2 10 2024
Statut: aheadofprint

Résumé

PTEN hamartoma tumour syndrome (PHTS) encompasses distinct syndromes, including Cowden syndrome resulting from Between 2010 and 2020, the Bergonie Institute reference laboratory identified 76 different non-truncating This new method of classification is more discriminative and reclassifies 25 variants, including 8 variants of unknown significance. This report proposes a revision of the current

Sections du résumé

BACKGROUND BACKGROUND
PTEN hamartoma tumour syndrome (PHTS) encompasses distinct syndromes, including Cowden syndrome resulting from
METHODS METHODS
Between 2010 and 2020, the Bergonie Institute reference laboratory identified 76 different non-truncating
RESULTS RESULTS
This new method of classification is more discriminative and reclassifies 25 variants, including 8 variants of unknown significance.
CONCLUSION CONCLUSIONS
This report proposes a revision of the current

Identifiants

pubmed: 39358013
pii: jmg-2024-109982
doi: 10.1136/jmg-2024-109982
pii:
doi:

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Investigateurs

Stéphanie Arpin (S)
Eric Bieth (E)
Valérie Bonadona (V)
Simon Boussion (S)
Bruno Buecher (B)
Olivier Caron (O)
Gustave Roussy (G)
Jean Chiesa (J)
Carole Corsini (C)
Rodolphe Dard (R)
Benjamin Dauriat (B)
Capucine Delnatte (C)
Philippe Denizeau (P)
Florence Demurger (F)
Vincent des Portes (VD)
Anne Dieux-Coeslier (A)
Berenice Doray (B)
Valérie Drouin Garraud (VD)
Nelly Durand (N)
Charles Patrick Edery (CP)
Laurence Faivre (L)
Christine Francannet (C)
Céline Garrec (C)
Marion Gauthier-Villars (M)
Marion Gerard (M)
Brigitte Gilbert-Dussardier (B)
Irina Giurgea (I)
Elodie Haser (E)
Marion Imbert-Bouteille (M)
Bertrand Isidor (B)
Valerie Layet (V)
Sophie Lejeune (S)
Dominique Leroux (D)
Lyonnet Stanislas (L)
Dominique Martin Coignard (DM)
Tanguy Martin-Denavit (T)
Christine Maugard (C)
Nicolas Molko (N)
Gilles Morin (G)
Sylviane Olschwang (S)
Olivier Patat (O)
Laurine Perrin (L)
Jean-Philippe Peyrat (JP)
Anne Philippe (A)
Lucile Pinson (L)
Fabienne Prieur (F)
Massimiliano Rossi (M)
Jean-Christophe Saurin (JC)
Hélène Schuster (H)
Nicolas Taris (N)
Marianne Till (M)
Lionel Van Maldergem (LV)
Dominique Vaur (D)
Laurence Venat (L)
Marie Vincent (M)

Informations de copyright

© Author(s) (or their employer(s)) 2024. No commercial re-use. See rights and permissions. Published by BMJ.

Déclaration de conflit d'intérêts

Competing interests: None declared.

Auteurs

Henri Margot (H)

Medical Genetics Departement, CHU de Bordeaux, Bordeaux, Nouvelle-Aquitaine, France.

Natalie Jones (N)

Cancer Genetics Unit, Institut Bergonié, Bordeaux, Aquitaine, France.

Thibaut Matis (T)

Cancer Genetics Unit, Institut Bergonié, Bordeaux, Aquitaine, France.

Dominique Bonneau (D)

U771-CNRS6214, UMR INSERM, Angers, France.
School of Medicine, University of Angers, Angers, France.

Tiffany Busa (T)

Medical Genetics Departement, Marseille Public University Hospital System, Marseille, France.

Françoise Bonnet (F)

Cancer Genetics Unit, Institut Bergonié, Bordeaux, Aquitaine, France.

Solene Conrad (S)

Medical Genetics Departement, University Hospital Centre Nantes, Nantes, Pays de la Loire, France.

Louise Crivelli (L)

Department of Oncogenetics, Centre Eugene Marquis, Rennes, Bretagne, France.

Pauline Monin (P)

Medical Genetics Departement, Centre Hospitalier Universitaire de Lyon, Lyon, Rhône-Alpes, France.

Sandra Fert-Ferrer (S)

Medical Genetics Departement, Centre Hospitalier Métropole Savoie, Chambery, France.

Isabelle Mortemousque (I)

Cancer Genetics Unit, Centre Hospitalier Régional Universitaire de Tours, Tours, Centre-Val de Loire, France.

Sabine Raad (S)

Cancer Genetics Unit, Institut Bergonié, Bordeaux, Aquitaine, France.

Didier Lacombe (D)

Department of Medical Genetics, CHU Bordeaux GH Pellegrin, Bordeaux, Aquitaine, France.
MRGM INSERM U1211, Universite de Bordeaux College Sciences de la Sante, Bordeaux, Nouvelle-Aquitaine, France.

Frédéric Caux (F)

Hospital Avicenne Internal Medicine Service, Bobigny, Île-de-France, France.

Nicolas Sevenet (N)

Cancer Genetics Unit, Institut Bergonié, Bordeaux, Aquitaine, France.
UMR1312, INSERM, BoRdeaux Institute of onCology, Bordeaux, France.

Virginie Bubien (V)

Cancer Genetics Unit, Institut Bergonié, Bordeaux, Aquitaine, France v.bubien@bordeaux.unicancer.fr.

Michel Longy (M)

Cancer Genetics Unit, Institut Bergonié, Bordeaux, Aquitaine, France.
UMR1312, INSERM, BoRdeaux Institute of onCology, Bordeaux, France.

Classifications MeSH