Uncovering Deletion/Insertion Mutations in Veno-Occlusive Disease with Immunodeficiency Syndrome in An Iranian Family: A Case Report.

Bioinformatics Mutation SP110 Protein Veno-occlusive disease with immunodeficiency syndrome Whole-exome sequencing

Journal

Cell journal
ISSN: 2228-5806
Titre abrégé: Cell J
Pays: Iran
ID NLM: 101566618

Informations de publication

Date de publication:
07 Oct 2024
Historique:
received: 19 02 2024
medline: 9 10 2024
pubmed: 9 10 2024
entrez: 9 10 2024
Statut: epublish

Résumé

Veno-occlusive disease with immunodeficiency (VODI) syndrome is a rare genetic disorder characterized by immune system irregularities and a significant mortality rate, despite its infrequency.

Identifiants

pubmed: 39380482
doi: 10.22074/cellj.2024.2023359.1514
pii:
doi:

Types de publication

Case Reports Journal Article

Langues

eng

Pagination

515-522

Auteurs

Parastoo Mohammadi (P)

Department of Biology, Damghan Branch, Islamic Azad University, Damghan, Iran.

Mehrdad Noruzinia (M)

Department of Medical Genetics, Faculty of Medicine, Tarbiat Modares University, Tehran, Iran. Email: Noruzinia@modares.ac.ir.

Mostafa Ebadi (M)

Department of Biology, Damghan Branch, Islamic Azad University, Damghan, Iran.

Pegah Ghoraeian (P)

Department of Genetics, Faculty of Advanced Science and Technology, Tehran Medical Sciences, Islamic Azad University, Tehran, Iran.

Classifications MeSH