Hemiconvulsion-Hemiplegia-Epilepsy syndrome in a 3-year-old girl: A case report and literature review.

Epilepsy Hemiconvulsion Hemiplegia MRI Status epilepticus

Journal

Radiology case reports
ISSN: 1930-0433
Titre abrégé: Radiol Case Rep
Pays: Netherlands
ID NLM: 101467888

Informations de publication

Date de publication:
Dec 2024
Historique:
received: 27 08 2024
accepted: 15 09 2024
medline: 11 10 2024
pubmed: 11 10 2024
entrez: 11 10 2024
Statut: epublish

Résumé

Hemiconvulsion-hemiplegia-epilepsy syndrome is a rare and severe neurological condition that results from prolonged status epilepticus in infancy and early childhood. This syndrome is characterized by unilateral prolonged seizures, primarily clonic in nature, which are followed by transient or permanent ipsilateral hemiplegia. In this report, we present the case of a 3-year-old girl who exhibited persistent left hemiparesis after experiencing an episode of prolonged focal seizures at the age of 2 years. Comprehensive neurological evaluation and brain MRI conducted in our department confirmed the diagnosis of hemiconvulsion-hemiplegia-epilepsy syndrome in its chronic phase.

Identifiants

pubmed: 39391028
doi: 10.1016/j.radcr.2024.09.076
pii: S1930-0433(24)01024-0
pmc: PMC11465060
doi:

Types de publication

Case Reports Journal Article

Langues

eng

Pagination

6574-6577

Informations de copyright

© 2024 The Authors. Published by Elsevier Inc. on behalf of University of Washington.

Auteurs

Sara Essetti (S)

Department of Neuroradiology, Specialty Hospital, CHU Ibn Sina, Mohamed V University, Rabat, Morocco.

Meriem Zhim (M)

Department of Neuroradiology, Specialty Hospital, CHU Ibn Sina, Mohamed V University, Rabat, Morocco.

Chaymae Faraj (C)

Department of Neuroradiology, Specialty Hospital, CHU Ibn Sina, Mohamed V University, Rabat, Morocco.

Asmae Guennouni (A)

Department of Neuroradiology, Specialty Hospital, CHU Ibn Sina, Mohamed V University, Rabat, Morocco.

Najwa Ech-Cherif El Kettani (NE)

Department of Neuroradiology, Specialty Hospital, CHU Ibn Sina, Mohamed V University, Rabat, Morocco.

Meriem Fikri (M)

Department of Neuroradiology, Specialty Hospital, CHU Ibn Sina, Mohamed V University, Rabat, Morocco.

Firdaous Touarsa (F)

Department of Neuroradiology, Specialty Hospital, CHU Ibn Sina, Mohamed V University, Rabat, Morocco.

Mohamed Jiddane (M)

Department of Neuroradiology, Specialty Hospital, CHU Ibn Sina, Mohamed V University, Rabat, Morocco.

Classifications MeSH