Polyarteritis nodosa mimics Kawasaki disease.


Journal

BMJ case reports
ISSN: 1757-790X
Titre abrégé: BMJ Case Rep
Pays: England
ID NLM: 101526291

Informations de publication

Date de publication:
21 Oct 2024
Historique:
medline: 22 10 2024
pubmed: 22 10 2024
entrez: 21 10 2024
Statut: epublish

Résumé

Polyarteritis nodosa (PAN) is a rarely seen vasculitis that often affects small-sized and medium-sized arteries. PAN can present with diverse clinical features depending on the organs involved, including potential cardiac involvement. Typical cardiac manifestations of PAN in the paediatric age group include pericarditis, valvular heart disease and coronary artery aneurysms. In contrast to PAN, Kawasaki disease (KD) is often associated with coronary artery abnormalities. Herein, we report a case of a young boy presented with KD-like features, including a coronary artery aneurysm confirmed by an echocardiogram (ECHO) and eventually diagnosed as PAN. The patient was treated with steroids, methotrexate and tocilizumab with improvement of the symptoms. Repeated ECHO revealed the resolution of the coronary artery aneurysms. Our paper highlights a rare presentation of PAN mimicking KD presentation. Physicians should consider PAN in chronic or severe courses of KD or coronary artery aneurysms.

Identifiants

pubmed: 39433394
pii: 17/10/e260544
doi: 10.1136/bcr-2024-260544
pii:
doi:

Substances chimiques

Methotrexate YL5FZ2Y5U1
tocilizumab I031V2H011
Antibodies, Monoclonal, Humanized 0

Types de publication

Case Reports Journal Article

Langues

eng

Sous-ensembles de citation

IM

Informations de copyright

© BMJ Publishing Group Limited 2024. No commercial re-use. See rights and permissions. Published by BMJ.

Déclaration de conflit d'intérêts

Competing interests: None declared.

Auteurs

Ibrahim Alibrahim (I)

Umm Al-Qura University College of Medicine, Makkah, Saudi Arabia.

Aisha Mirza (A)

Pediatrics, Maternity and Children Hospital, Makkah, Saudi Arabia.

Amer Khojah (A)

Pediatrics, Umm Al-Qura University College of Medicine, Makkah, Saudi Arabia amkhojah@uqu.edu.sa.

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Classifications MeSH