US Clinical Practice Experience with Eculizumab in Myasthenia Gravis: Acute Clinical Events and Healthcare Resource Utilization.


Journal

Drugs - real world outcomes
ISSN: 2199-1154
Titre abrégé: Drugs Real World Outcomes
Pays: Switzerland
ID NLM: 101658456

Informations de publication

Date de publication:
29 Oct 2024
Historique:
accepted: 23 09 2024
medline: 29 10 2024
pubmed: 29 10 2024
entrez: 29 10 2024
Statut: aheadofprint

Résumé

The terminal complement inhibitor eculizumab is approved in the USA for the treatment of patients with acetylcholine receptor antibody-positive generalized myasthenia gravis (MG). The ELEVATE study aimed to examine clinical-practice outcome data on eculizumab effectiveness in US adults with MG (generalized or ocular). This paper reports the findings on MG exacerbations and crises and associated healthcare resource utilization, and the use of rescue therapy. A retrospective chart review was conducted of US adults with MG who initiated eculizumab. Outcomes assessed for up to 2 years before and after eculizumab initiation included percentages and rates per patient per year (PPPY) of exacerbations and crises (the latter defined as intubation/impending intubation), healthcare resource utilization, and rescue therapy administration. A total of 119 patients diagnosed with MG were enrolled in the study; 92 patients had ≥ 3 months of data both before and during eculizumab therapy and were included in the analyses. The mean rate of MG exacerbations decreased from 0.385 PPPY before eculizumab initiation to 0.152 PPPY during eculizumab treatment (p = 0.0034); the mean rate of MG crises decreased from 0.411 to 0.056 PPPY (p = 0.0018). Rates of healthcare resource utilization and rescue therapy use also decreased significantly during eculizumab treatment. This retrospective chart review analysis provides evidence for a beneficial impact of eculizumab treatment on the incidence of MG exacerbations and crises and associated healthcare resource utilization in clinical practice, and on rescue therapy use. These data further support the therapeutic benefits of eculizumab in patients with MG.

Sections du résumé

BACKGROUND AND OBJECTIVE OBJECTIVE
The terminal complement inhibitor eculizumab is approved in the USA for the treatment of patients with acetylcholine receptor antibody-positive generalized myasthenia gravis (MG). The ELEVATE study aimed to examine clinical-practice outcome data on eculizumab effectiveness in US adults with MG (generalized or ocular). This paper reports the findings on MG exacerbations and crises and associated healthcare resource utilization, and the use of rescue therapy.
METHODS METHODS
A retrospective chart review was conducted of US adults with MG who initiated eculizumab. Outcomes assessed for up to 2 years before and after eculizumab initiation included percentages and rates per patient per year (PPPY) of exacerbations and crises (the latter defined as intubation/impending intubation), healthcare resource utilization, and rescue therapy administration.
RESULTS RESULTS
A total of 119 patients diagnosed with MG were enrolled in the study; 92 patients had ≥ 3 months of data both before and during eculizumab therapy and were included in the analyses. The mean rate of MG exacerbations decreased from 0.385 PPPY before eculizumab initiation to 0.152 PPPY during eculizumab treatment (p = 0.0034); the mean rate of MG crises decreased from 0.411 to 0.056 PPPY (p = 0.0018). Rates of healthcare resource utilization and rescue therapy use also decreased significantly during eculizumab treatment.
CONCLUSIONS CONCLUSIONS
This retrospective chart review analysis provides evidence for a beneficial impact of eculizumab treatment on the incidence of MG exacerbations and crises and associated healthcare resource utilization in clinical practice, and on rescue therapy use. These data further support the therapeutic benefits of eculizumab in patients with MG.

Identifiants

pubmed: 39470958
doi: 10.1007/s40801-024-00457-8
pii: 10.1007/s40801-024-00457-8
doi:

Types de publication

Journal Article

Langues

eng

Informations de copyright

© 2024. The Author(s).

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Auteurs

Richard J Nowak (RJ)

Yale University School of Medicine, New Haven, CT, USA.

Ali A Habib (AA)

University of California, Irvine, CA, USA.

Andrew J Klink (AJ)

Cardinal Health, Dublin, OH, USA.

Srikanth Muppidi (S)

Stanford Neuroscience Health Center, Palo Alto, CA, USA.

Anju Parthan (A)

Alexion, AstraZeneca Rare Disease, Boston, MA, USA.
FibroGen Inc., San Francisco, CA, USA.

S Chloe Sader (SC)

Alexion, AstraZeneca Rare Disease, Boston, MA, USA.

Alexandrina Balanean (A)

Cardinal Health, Dublin, OH, USA.

Ajeet Gajra (A)

Cardinal Health, Dublin, OH, USA.
Hematology-Oncology Associates of CNY, E. Syracuse, NY, USA.

James F Howard (JF)

Department of Neurology, The University of North Carolina, 170 Manning Drive, CB #7025, Chapel Hill, NC, 27599, USA. howardj@neurology.unc.edu.

Classifications MeSH