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"headline": "Diagnostic sur Membrane basilaire",
"description": "Comment évaluer la fonction de la membrane basilaire ?\nQuels examens sont utilisés pour diagnostiquer des troubles auditifs ?\nQuels signes indiquent un dysfonctionnement de la membrane basilaire ?\nComment les tests de réflexe acoustique aident-ils au diagnostic ?\nQuel rôle joue l'oto-rhino-laryngologiste dans le diagnostic ?",
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"@type": "Question",
"name": "Comment évaluer la fonction de la membrane basilaire ?",
"position": 1,
"acceptedAnswer": {
"@type": "Answer",
"text": "Des tests auditifs comme l'audiométrie peuvent évaluer la fonction de la membrane basilaire."
}
},
{
"@type": "Question",
"name": "Quels examens sont utilisés pour diagnostiquer des troubles auditifs ?",
"position": 2,
"acceptedAnswer": {
"@type": "Answer",
"text": "L'IRM et la tomodensitométrie peuvent aider à diagnostiquer des anomalies de la membrane basilaire."
}
},
{
"@type": "Question",
"name": "Quels signes indiquent un dysfonctionnement de la membrane basilaire ?",
"position": 3,
"acceptedAnswer": {
"@type": "Answer",
"text": "Des signes incluent des pertes auditives, des acouphènes ou des vertiges."
}
},
{
"@type": "Question",
"name": "Comment les tests de réflexe acoustique aident-ils au diagnostic ?",
"position": 4,
"acceptedAnswer": {
"@type": "Answer",
"text": "Ils mesurent la réponse de la membrane basilaire aux sons, indiquant des dysfonctionnements."
}
},
{
"@type": "Question",
"name": "Quel rôle joue l'oto-rhino-laryngologiste dans le diagnostic ?",
"position": 5,
"acceptedAnswer": {
"@type": "Answer",
"text": "L'oto-rhino-laryngologiste évalue les troubles auditifs et examine la membrane basilaire."
}
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{
"@type": "Question",
"name": "Quels symptômes sont associés à des problèmes de membrane basilaire ?",
"position": 6,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les symptômes incluent des pertes auditives, des vertiges et des acouphènes."
}
},
{
"@type": "Question",
"name": "Comment les acouphènes se manifestent-ils ?",
"position": 7,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les acouphènes se manifestent par des bruits perçus sans source externe, souvent liés à des troubles de la membrane basilaire."
}
},
{
"@type": "Question",
"name": "Les vertiges sont-ils un signe de dysfonction de la membrane basilaire ?",
"position": 8,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les vertiges peuvent indiquer une dysfonction de la membrane basilaire ou des structures associées."
}
},
{
"@type": "Question",
"name": "Peut-on ressentir une pression dans l'oreille ?",
"position": 9,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, une pression dans l'oreille peut être liée à des problèmes de membrane basilaire."
}
},
{
"@type": "Question",
"name": "Les changements de l'audition sont-ils fréquents ?",
"position": 10,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des changements d'audition peuvent survenir avec des troubles de la membrane basilaire."
}
},
{
"@type": "Question",
"name": "Comment prévenir les troubles de la membrane basilaire ?",
"position": 11,
"acceptedAnswer": {
"@type": "Answer",
"text": "Éviter l'exposition à des bruits forts et protéger les oreilles peut aider à prévenir ces troubles."
}
},
{
"@type": "Question",
"name": "Les examens auditifs réguliers sont-ils importants ?",
"position": 12,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des examens réguliers peuvent détecter précocement des problèmes liés à la membrane basilaire."
}
},
{
"@type": "Question",
"name": "L'hygiène auditive joue-t-elle un rôle ?",
"position": 13,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, maintenir une bonne hygiène auditive peut prévenir les infections et les troubles associés."
}
},
{
"@type": "Question",
"name": "Les vaccinations peuvent-elles aider à prévenir des infections ?",
"position": 14,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, certaines vaccinations peuvent prévenir des infections qui affectent l'oreille interne."
}
},
{
"@type": "Question",
"name": "Faut-il éviter certains médicaments ?",
"position": 15,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, certains médicaments ototoxiques doivent être évités pour protéger la membrane basilaire."
}
},
{
"@type": "Question",
"name": "Quels traitements existent pour les troubles de la membrane basilaire ?",
"position": 16,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les traitements incluent des appareils auditifs, des médicaments et parfois la chirurgie."
}
},
{
"@type": "Question",
"name": "Les corticostéroïdes sont-ils efficaces pour traiter ces troubles ?",
"position": 17,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les corticostéroïdes peuvent réduire l'inflammation et améliorer l'audition dans certains cas."
}
},
{
"@type": "Question",
"name": "Quand la chirurgie est-elle envisagée ?",
"position": 18,
"acceptedAnswer": {
"@type": "Answer",
"text": "La chirurgie est envisagée en cas de malformations ou de lésions graves de la membrane basilaire."
}
},
{
"@type": "Question",
"name": "Les thérapies sonores peuvent-elles aider ?",
"position": 19,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les thérapies sonores peuvent aider à gérer les symptômes d'acouphènes liés à la membrane basilaire."
}
},
{
"@type": "Question",
"name": "Comment les appareils auditifs améliorent-ils l'audition ?",
"position": 20,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les appareils auditifs amplifient les sons, aidant à compenser la perte auditive due à des problèmes de membrane basilaire."
}
},
{
"@type": "Question",
"name": "Quelles complications peuvent survenir avec des troubles de la membrane basilaire ?",
"position": 21,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les complications incluent des pertes auditives permanentes et des troubles d'équilibre."
}
},
{
"@type": "Question",
"name": "Les infections de l'oreille peuvent-elles causer des complications ?",
"position": 22,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les infections non traitées peuvent entraîner des complications graves affectant la membrane basilaire."
}
},
{
"@type": "Question",
"name": "Comment les troubles de l'équilibre sont-ils liés à la membrane basilaire ?",
"position": 23,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les troubles de l'équilibre peuvent résulter de dysfonctionnements dans la membrane basilaire et les structures associées."
}
},
{
"@type": "Question",
"name": "Les acouphènes peuvent-ils devenir chroniques ?",
"position": 24,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les acouphènes peuvent devenir chroniques et affecter la qualité de vie si non traités."
}
},
{
"@type": "Question",
"name": "Les troubles auditifs peuvent-ils affecter la santé mentale ?",
"position": 25,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les troubles auditifs peuvent entraîner de l'anxiété et de la dépression chez certains patients."
}
},
{
"@type": "Question",
"name": "Quels sont les facteurs de risque pour les troubles de la membrane basilaire ?",
"position": 26,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les facteurs incluent l'exposition au bruit, l'âge avancé et des antécédents familiaux."
}
},
{
"@type": "Question",
"name": "L'âge est-il un facteur de risque ?",
"position": 27,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, le vieillissement est un facteur de risque majeur pour les troubles auditifs liés à la membrane basilaire."
}
},
{
"@type": "Question",
"name": "Les antécédents médicaux influencent-ils le risque ?",
"position": 28,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des antécédents de maladies de l'oreille ou d'infections augmentent le risque de troubles."
}
},
{
"@type": "Question",
"name": "Le mode de vie peut-il affecter la santé auditive ?",
"position": 29,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, un mode de vie avec exposition fréquente à des bruits forts augmente le risque de troubles auditifs."
}
},
{
"@type": "Question",
"name": "Les maladies systémiques sont-elles un facteur de risque ?",
"position": 30,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, certaines maladies comme le diabète peuvent augmenter le risque de troubles auditifs."
}
}
]
}
]
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Juvenile localized and systemic scleroderma are rare autoimmune diseases which cause significant disability and morbidity in children. The mechanisms driving juvenile scleroderma remain unclear, neces...
Pulmonary Arterial Hypertension (PAH) is a clinical syndrome consisting of physiologic/hemodynamic criteria that are a consequence of several etiologies. Systemic Sclerosis (SSc), one of the most comm...
Enrichment strategies from clinical trials for progressive systemic sclerosis-associated interstitial lung disease (SSc-ILD) have not been tested in a real-life cohort....
Do enrichment strategies for progressive ILD impact efficacy, representativeness, and feasibility in patients with SSc-ILD from the European Scleroderma Trials and Research (EUSTAR) database?...
We applied the inclusion criteria of major recent SSc-ILD trials (Study of the Efficacy and Safety of Tocilizumab in Participants With Systemic Sclerosis [focuSSced], Scleroderma Lung Study II [SLS II...
In total, 2,258 patients with SSc-ILD were included: 31.2% of the patients met SENSCIS criteria; 5.8% of the patients met SLS II criteria; 1.6% of the patients met focuSSced criteria, and 67.7% (1,529...
The application of enrichment criteria from previous clinical trials showed enrichment for progression with variable success, which led to selected patient populations reducing feasibility of recruitm...
Patients with systemic sclerosis (SSc) are at increased risk of cancer, a growing cause of non-SSc-related death among these patients. We analyzed the increased cancer risk among Spanish patients with...
Spanish Scleroderma Registry data were analyzed to determine the demographic characteristics of patients with SSc, and logistic regression was used to identify cancer risk factors. SIRs with 95% confi...
Of 1930 patients with SSc, 206 had cancer, most commonly breast, lung, hematological, and colorectal cancers. Patients with SSc had increased risks of overall cancer (SIR 1.48, 95% CI 1.36-1.60; P < 0...
Spanish patients with SSc had an increased cancer risk compared with the general population. Some characteristics, including specific autoantibodies, may be related to this increased risk....
One of the key clinical challenges of systemic sclerosis (SSc) is diversity in clinical presentation, organ involvement and disease progression. Antinuclear autoantibodies (ANA) are central to the dia...
There has been further development in delineating clinical patterns in ANA, genetic susceptibility and antigen triggers predisposing to ANA subtypes. Sub-group analysis of recent clinical trials shows...
ANA subtyping is likely to be firmly embedded into future classification systems. Beyond informing current management and monitoring of scleroderma patients, ANA subsets have implication on future res...
The mechanisms of systemic autoimmune diseases (ADs) are still not clearly understood. Understanding the etiology of systemic ADs and identifying new therapeutic targets require a systems science appr...
People with systemic sclerosis (SSc) are vulnerable in COVID-19 and face challenges related to shifting COVID-19 risk and protective restrictions. We evaluated mental health symptom trajectories in pe...
The longitudinal Scleroderma Patient-centred Intervention Network (SPIN) COVID-19 cohort was launched in April 2020 and included participants from the ongoing SPIN Cohort and external enrolees. Analys...
Anxiety symptoms increased in early 2020 but returned to pre-COVID-19 levels by mid-2020 and remained stable through March 2022. Depression symptoms did not initially change but were slightly lower by...
People with SSc continue to face COVID-19 challenges related to ongoing risk, the opening of societies, and removal of protective restrictions. People with SSc, in aggregate, appear to be weathering t...
Systemic sclerosis (SSc) is a rare auto-immune disease, affecting principally women between 40 and 60 years old. It is caracterised by a cutaneous and visceral fibrosis, an alteration of the microvasc...
We have analysed the data of a retrospective and bicentrique cohort, from the internal medicine unit of Hôpital Nord in Marseille and from the internal medicine unit of the Hôpital Sainte-Anne in Toul...
The cohort included 151 patients including 134 limited cutaneous SSc. Fifty-two (34.4%) patients presented at least one associated auto-immune or inflammatory disease. The association of two connectiv...
SSc is often associated with other autoimmune diseases. This interrelation between associated pathologies and SSc, modifying sometimes the evolution of SSc, enhances the need of a personalized follow-...
Systemic sclerosis (SSc) represents extremely rare disease with majority of data coming from adults. Studies comparing juvenile- (jSSc) and adult-onset (aSSc) patients are limited. We aimed to compare...
A retrospective study among pediatric and adult Scl patients has been performed. Demographic characteristics, clinical features, autoantibody profiles, and treatment data were retrieved from the datab...
A total of 158 adults and 58 juvenile Scl patients were identified. The mean age at the disease onset was 37±14.7 vs. 8.8 ± 4.1 years, mean age at diagnosis 42±15.2 vs. 10.4 ± 3.8 years and mean follo...
Juvenile and adult-onset Scl represent rarely seen conditions with different clinical phenotypes. Pediatric patients with LS are more commonly seen by pediatric rheumatologists, in contrary to adults....
Systemic sclerosis (SSc), also known as scleroderma, is a chronic autoimmune connective tissue disease and is associated with a significant economic burden resulting from health care utilization costs...