Titre : Syndrome de Budd-Chiari

Syndrome de Budd-Chiari : Questions médicales fréquentes

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"2025-05-02", "inLanguage": "fr", "hasPart": [ { "@type": "MedicalWebPage", "name": "Diagnostic", "headline": "Diagnostic sur Syndrome de Budd-Chiari", "description": "Comment diagnostiquer le syndrome de Budd-Chiari ?\nQuels tests sanguins sont utiles ?\nQuels signes cliniques indiquent ce syndrome ?\nL'échographie Doppler est-elle utile ?\nQuand envisager une biopsie hépatique ?", "url": "https://questionsmedicales.fr/mesh/D006502?page=2#section-diagnostic" }, { "@type": "MedicalWebPage", "name": "Symptômes", "headline": "Symptômes sur Syndrome de Budd-Chiari", "description": "Quels sont les symptômes courants ?\nLa douleur abdominale est-elle fréquente ?\nQu'est-ce que l'ascite ?\nLa jaunisse est-elle un symptôme ?\nPeut-on avoir des symptômes asymptomatiques ?", "url": "https://questionsmedicales.fr/mesh/D006502?page=2#section-symptômes" }, { "@type": "MedicalWebPage", "name": "Prévention", "headline": "Prévention sur Syndrome de Budd-Chiari", "description": "Comment prévenir le syndrome de Budd-Chiari ?\nLes anticoagulants peuvent-ils prévenir ce syndrome ?\nQuelles habitudes de vie adopter ?\nLes vaccinations sont-elles importantes ?\nFaut-il surveiller les maladies hépatiques ?", "url": "https://questionsmedicales.fr/mesh/D006502?page=2#section-prévention" }, { "@type": "MedicalWebPage", "name": "Traitements", "headline": "Traitements sur Syndrome de Budd-Chiari", "description": "Quels traitements sont disponibles ?\nQuand utiliser des anticoagulants ?\nQu'est-ce qu'une procédure endovasculaire ?\nQuand envisager une transplantation hépatique ?\nY a-t-il des traitements symptomatiques ?", "url": "https://questionsmedicales.fr/mesh/D006502?page=2#section-traitements" }, { "@type": "MedicalWebPage", "name": "Complications", "headline": "Complications sur Syndrome de Budd-Chiari", "description": "Quelles sont les complications possibles ?\nL'insuffisance hépatique est-elle fréquente ?\nQu'est-ce que l'hypertension portale ?\nPeut-on avoir des complications à long terme ?\nLes complications peuvent-elles être évitées ?", "url": "https://questionsmedicales.fr/mesh/D006502?page=2#section-complications" }, { "@type": "MedicalWebPage", "name": "Facteurs de risque", "headline": "Facteurs de risque sur Syndrome de Budd-Chiari", "description": "Quels sont les principaux facteurs de risque ?\nL'obésité augmente-t-elle le risque ?\nLes maladies hépatiques sont-elles un risque ?\nLes contraceptifs oraux sont-ils un facteur ?\nLe tabagisme influence-t-il le risque ?", "url": "https://questionsmedicales.fr/mesh/D006502?page=2#section-facteurs de risque" } ] }, { "@type": "FAQPage", "mainEntity": [ { "@type": "Question", "name": "Comment diagnostiquer le syndrome de Budd-Chiari ?", "position": 1, "acceptedAnswer": { "@type": "Answer", "text": "Le diagnostic repose sur l'échographie, l'IRM et des tests sanguins pour évaluer la fonction hépatique." } }, { "@type": "Question", "name": "Quels tests sanguins sont utiles ?", "position": 2, "acceptedAnswer": { "@type": "Answer", "text": "Les tests incluent les marqueurs de la fonction hépatique et les tests de coagulation." } }, { "@type": "Question", "name": "Quels signes cliniques indiquent ce syndrome ?", "position": 3, "acceptedAnswer": { "@type": "Answer", "text": "Les signes incluent l'ascite, la douleur abdominale et l'hypertrophie du foie." } }, { "@type": "Question", "name": "L'échographie Doppler est-elle utile ?", "position": 4, "acceptedAnswer": { "@type": "Answer", "text": "Oui, elle permet d'évaluer le flux sanguin dans les veines hépatiques et de détecter des obstructions." } }, { "@type": "Question", "name": "Quand envisager une biopsie hépatique ?", "position": 5, "acceptedAnswer": { "@type": "Answer", "text": "Une biopsie peut être envisagée si le diagnostic est incertain ou pour évaluer des lésions hépatiques." } }, { "@type": "Question", "name": "Quels sont les symptômes courants ?", "position": 6, "acceptedAnswer": { "@type": "Answer", "text": "Les symptômes incluent fatigue, douleur abdominale, jaunisse et ascite." } }, { "@type": "Question", "name": "La douleur abdominale est-elle fréquente ?", "position": 7, "acceptedAnswer": { "@type": "Answer", "text": "Oui, la douleur abdominale est un symptôme fréquent, souvent localisée dans la partie supérieure droite." } }, { "@type": "Question", "name": "Qu'est-ce que l'ascite ?", "position": 8, "acceptedAnswer": { "@type": "Answer", "text": "L'ascite est l'accumulation de liquide dans la cavité abdominale, souvent causée par une hypertension portale." } }, { "@type": "Question", "name": "La jaunisse est-elle un symptôme ?", "position": 9, "acceptedAnswer": { "@type": "Answer", "text": "Oui, la jaunisse, due à une accumulation de bilirubine, est un symptôme courant du syndrome." } }, { "@type": "Question", "name": "Peut-on avoir des symptômes asymptomatiques ?", "position": 10, "acceptedAnswer": { "@type": "Answer", "text": "Oui, certains patients peuvent être asymptomatiques, surtout dans les formes chroniques." } }, { "@type": "Question", "name": "Comment prévenir le syndrome de Budd-Chiari ?", "position": 11, "acceptedAnswer": { "@type": "Answer", "text": "La prévention inclut la gestion des facteurs de risque comme les troubles de la coagulation et l'obésité." } }, { "@type": "Question", "name": "Les anticoagulants peuvent-ils prévenir ce syndrome ?", "position": 12, "acceptedAnswer": { "@type": "Answer", "text": "Oui, les anticoagulants peuvent prévenir les thromboses chez les patients à risque." } }, { "@type": "Question", "name": "Quelles habitudes de vie adopter ?", "position": 13, "acceptedAnswer": { "@type": "Answer", "text": "Adopter une alimentation équilibrée, faire de l'exercice et éviter le tabac sont bénéfiques." } }, { "@type": "Question", "name": "Les vaccinations sont-elles importantes ?", "position": 14, "acceptedAnswer": { "@type": "Answer", "text": "Oui, se faire vacciner contre l'hépatite peut réduire le risque de complications hépatiques." } }, { "@type": "Question", "name": "Faut-il surveiller les maladies hépatiques ?", "position": 15, "acceptedAnswer": { "@type": "Answer", "text": "Oui, surveiller les maladies hépatiques et les troubles de la coagulation est crucial pour la prévention." } }, { "@type": "Question", "name": "Quels traitements sont disponibles ?", "position": 16, "acceptedAnswer": { "@type": "Answer", "text": "Les traitements incluent des anticoagulants, des procédures endovasculaires et, dans certains cas, une transplantation hépatique." } }, { "@type": "Question", "name": "Quand utiliser des anticoagulants ?", "position": 17, "acceptedAnswer": { "@type": "Answer", "text": "Les anticoagulants sont utilisés pour traiter les thromboses veineuses hépatiques et prévenir les complications." } }, { "@type": "Question", "name": "Qu'est-ce qu'une procédure endovasculaire ?", "position": 18, "acceptedAnswer": { "@type": "Answer", "text": "C'est une intervention pour débloquer les veines hépatiques, souvent par angioplastie ou stenting." } }, { "@type": "Question", "name": "Quand envisager une transplantation hépatique ?", "position": 19, "acceptedAnswer": { "@type": "Answer", "text": "La transplantation est envisagée en cas d'insuffisance hépatique sévère ou de complications irréversibles." } }, { "@type": "Question", "name": "Y a-t-il des traitements symptomatiques ?", "position": 20, "acceptedAnswer": { "@type": "Answer", "text": "Oui, des traitements symptomatiques comme les diurétiques peuvent aider à gérer l'ascite." } }, { "@type": "Question", "name": "Quelles sont les complications possibles ?", "position": 21, "acceptedAnswer": { "@type": "Answer", "text": "Les complications incluent l'insuffisance hépatique, la thrombose et l'hypertension portale." } }, { "@type": "Question", "name": "L'insuffisance hépatique est-elle fréquente ?", "position": 22, "acceptedAnswer": { "@type": "Answer", "text": "Oui, l'insuffisance hépatique est une complication grave pouvant survenir dans ce syndrome." } }, { "@type": "Question", "name": "Qu'est-ce que l'hypertension portale ?", "position": 23, "acceptedAnswer": { "@type": "Answer", "text": "L'hypertension portale est une augmentation de la pression dans la veine porte, causée par l'obstruction." } }, { "@type": "Question", "name": "Peut-on avoir des complications à long terme ?", "position": 24, "acceptedAnswer": { "@type": "Answer", "text": "Oui, des complications à long terme comme la cirrhose peuvent se développer si non traitées." } }, { "@type": "Question", "name": "Les complications peuvent-elles être évitées ?", "position": 25, "acceptedAnswer": { "@type": "Answer", "text": "Certaines complications peuvent être évitées par un traitement précoce et une surveillance régulière." } }, { "@type": "Question", "name": "Quels sont les principaux facteurs de risque ?", "position": 26, "acceptedAnswer": { "@type": "Answer", "text": "Les facteurs incluent les troubles de la coagulation, l'obésité, et certaines maladies hépatiques." } }, { "@type": "Question", "name": "L'obésité augmente-t-elle le risque ?", "position": 27, "acceptedAnswer": { "@type": "Answer", "text": "Oui, l'obésité est un facteur de risque connu pour le syndrome de Budd-Chiari." } }, { "@type": "Question", "name": "Les maladies hépatiques sont-elles un risque ?", "position": 28, "acceptedAnswer": { "@type": "Answer", "text": "Oui, certaines maladies hépatiques, comme la cirrhose, augmentent le risque de ce syndrome." } }, { "@type": "Question", "name": "Les contraceptifs oraux sont-ils un facteur ?", "position": 29, "acceptedAnswer": { "@type": "Answer", "text": "Oui, l'utilisation prolongée de contraceptifs oraux peut augmenter le risque de thrombose." } }, { "@type": "Question", "name": "Le tabagisme influence-t-il le risque ?", "position": 30, "acceptedAnswer": { "@type": "Answer", "text": "Oui, le tabagisme peut contribuer à des problèmes vasculaires, augmentant le risque de thrombose." } } ] } ] }

Sources (10000 au total)

Living Donor Liver Transplantation for Budd-Chiari Syndrome: A Propensity Score-Matched Analysis.

There are unique technical and management challenges associated with living donor liver transplantation (LDLT) for Budd-Chiari Syndrome (BCS). The outcomes of LDLT for BCS in comparison to other indic... Data of 24 BCS patients who underwent LDLT between January 2012 and June 2019 were analyzed. There were 20 adults and 4 children. The early and long-term outcomes of adult LDLT BCS patients were compa... Primary BCS was observed in 18 (90%) patients. Caval replacement was performed in 7 (35%) patients. Early and late hepatic venous outflow tract (HVOT) complications were seen in 1 (5%) and 3 (15%) pat... LDLT is a good option for symptomatic BCS who have failed non-transplant interventions. The clinical and risk factor profile of BCS recipients is distinct from non-BCS recipients. By following an algo...

Evaluation of outcome from endovascular therapy for Budd-Chiari syndrome: a systematic review and meta-analysis.

This study was performed to evaluate the outcome of endovascular intervention therapy for Budd-Chiari syndrome (BCS) and compare recanalization, transjugular intrahepatic portosystemic shunt (TIPS)/di...

Outcome of Budd-Chiari Syndrome Patients Treated With Direct Oral Anticoagulants: An Austrian Multicenter Study.

Direct oral anticoagulants (DOACs) may simplify management of Budd-Chiari syndrome (BCS). Here, we report our experience with off-label use of DOACs for anticoagulation in BCS.... The safety of DOAC vs vitamin K antagonist treatment as well as associated clinical outcomes were retrospectively assessed in 47 BCS patients treated at 6 Austrian centers.... Mean age at study inclusion was 37.9 ± 14.0 years and mean Model for End-Stage Liver Disease was 13.1 ± 5.1. Overall, 63.8% (n = 30) of patients had decompensated liver disease, and 87.2% (n = 41) sho... DOACs seem to be effective and safe for long-term anticoagulation in patients with BCS, but confirmation by larger prospective studies is needed....

Secondary Budd-Chiari syndrome occurred after adjuvant radiotherapy for perihilar cholangiocarcinoma: a case report.

Budd-Chiari syndrome (BCS) is a rare vascular disorder of the liver, and acute and secondary BCS is even rarer.... A 62-year-old man with perihilar cholangiocarcinoma of Bismuth type IIIa underwent right hemi-hepatectomy with caudate lobectomy and pancreatoduodenectomy. Adjuvant chemoradiotherapy was performed due... Although no case of BCS caused by radiotherapy has yet been reported, the present case showed that late side effect of radiotherapy can cause hepatic vein stenosis and secondary BCS....

Percutaneous recanalization in hepatic vein-type Budd-Chiari syndrome: hepatic or accessory hepatic vein.

This study was designed to assess the clinical efficiency and long-term outcomes of hepatic vein (HV) and accessory hepatic vein (AHV) recanalization in patients with HV-type Budd-Chiari syndrome (BCS... A total of 27 patients with HV-type BCS underwent AHV recanalization and 94 patients had HV recanalization at our center from January 2012 to December 2019. The treatment effectiveness and long-term o... Technical success was accomplished in all patients, without any procedure-related complications. The clinical success rates were 96.3% (26/27) and 95.7% (90/94) (... Our findings suggest that AHV could be employed as a replacement for HV, as a hepatic drainage vein, in HV-type BCS patients....

Prothrombotic states in portal vein thrombosis and Budd-Chiari syndrome in India: A systematic review and meta-analysis.

Both Budd-Chiari syndrome (BCS) and portal vein thrombosis (PVT) have been linked to various prothrombotic (PT) conditions. The PT profile in Asians is different from the west and there are no nationw... A comprehensive literature search of Embase, Medline and Scopus was conducted from January 2000 to February 2022 for studies evaluating the prevalence of various PT conditions in Indian patients with ... Thirty-five studies with 1005 PVT patients and 1391 BCS patients were included in the meta-analysis. At least one PT condition was seen in 46.2% (28.7-63.7) of the PVT patients and 44.9% (37.3-60.7) o... The PT profile in Indian patients with abdominal vein thrombosis is different from that of the western data with a lower prevalence of PT conditions in patients with BCS....

Efficacy and Safety of Transjugular Intrahepatic Portosystemic Shunt Creation for Budd-Chiari Syndrome: A Systematic Review and Meta-Analysis.

To assess the critical role of transjugular intrahepatic portosystemic shunt (TIPS) in the management of Budd-Chiari syndrome (BCS), as the data with respect to the safety and outcome of TIPS in patie... A comprehensive search of literature of various databases from 2000 to October 2021 was conducted for studies evaluating the outcome of TIPS in patients with BCS. The primary outcomes of the analysis ... A total of 33 studies (1,395 patients) were included in this meta-analysis. The pooled rates and 95% confidence intervals of various outcomes were 98.6% (97.6-99.7) for technical success, 90.3% (86.0-... The existing literature supports the feasibility, safety, and efficacy of TIPS in the treatment of BCS. Deciding the optimal timing of TIPS in BCS needs further studies....