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"description": "Comment diagnostique-t-on le syndrome de Job ?\nQuels tests sanguins sont utilisés ?\nLe syndrome de Job est-il héréditaire ?\nQuels signes cliniques indiquent ce syndrome ?\nPeut-on confondre ce syndrome avec d'autres ?",
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"name": "Comment diagnostique-t-on le syndrome de Job ?",
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"text": "Le diagnostic repose sur l'évaluation clinique, les antécédents médicaux et des tests sanguins pour mesurer les IgE."
}
},
{
"@type": "Question",
"name": "Quels tests sanguins sont utilisés ?",
"position": 2,
"acceptedAnswer": {
"@type": "Answer",
"text": "Des tests mesurant les niveaux d'IgE et des analyses pour détecter des infections sont effectués."
}
},
{
"@type": "Question",
"name": "Le syndrome de Job est-il héréditaire ?",
"position": 3,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, il est souvent héréditaire, lié à des mutations génétiques spécifiques."
}
},
{
"@type": "Question",
"name": "Quels signes cliniques indiquent ce syndrome ?",
"position": 4,
"acceptedAnswer": {
"@type": "Answer",
"text": "Des infections cutanées, des pneumonies récurrentes et des éruptions cutanées sont des signes clés."
}
},
{
"@type": "Question",
"name": "Peut-on confondre ce syndrome avec d'autres ?",
"position": 5,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, il peut être confondu avec d'autres immunodéficiences, nécessitant des tests spécifiques."
}
},
{
"@type": "Question",
"name": "Quels sont les symptômes principaux du syndrome de Job ?",
"position": 6,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les symptômes incluent des infections récurrentes, des éruptions cutanées et des allergies."
}
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{
"@type": "Question",
"name": "Les éruptions cutanées sont-elles fréquentes ?",
"position": 7,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des éruptions cutanées, souvent prurigineuses, sont courantes chez les patients."
}
},
{
"@type": "Question",
"name": "Y a-t-il des symptômes respiratoires associés ?",
"position": 8,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les patients peuvent souffrir de pneumonies et d'autres infections respiratoires fréquentes."
}
},
{
"@type": "Question",
"name": "Le syndrome de Job cause-t-il des problèmes dentaires ?",
"position": 9,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des problèmes dentaires comme des abcès peuvent survenir en raison d'infections fréquentes."
}
},
{
"@type": "Question",
"name": "Les allergies sont-elles fréquentes dans ce syndrome ?",
"position": 10,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les patients présentent souvent des allergies, notamment aux acariens et aux pollens."
}
},
{
"@type": "Question",
"name": "Comment prévenir les infections chez les patients ?",
"position": 11,
"acceptedAnswer": {
"@type": "Answer",
"text": "Il est crucial d'encourager une bonne hygiène, des vaccinations et un suivi médical régulier."
}
},
{
"@type": "Question",
"name": "Les patients doivent-ils éviter certains aliments ?",
"position": 12,
"acceptedAnswer": {
"@type": "Answer",
"text": "Il n'y a pas de restrictions alimentaires spécifiques, mais une alimentation équilibrée est conseillée."
}
},
{
"@type": "Question",
"name": "Les vaccinations sont-elles importantes ?",
"position": 13,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les vaccinations sont essentielles pour prévenir les infections graves chez ces patients."
}
},
{
"@type": "Question",
"name": "Comment gérer les allergies dans ce syndrome ?",
"position": 14,
"acceptedAnswer": {
"@type": "Answer",
"text": "Éviter les allergènes connus et utiliser des antihistaminiques peut aider à gérer les allergies."
}
},
{
"@type": "Question",
"name": "Les soins dentaires sont-ils importants ?",
"position": 15,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des soins dentaires réguliers sont cruciaux pour prévenir les infections buccales."
}
},
{
"@type": "Question",
"name": "Quel est le traitement principal du syndrome de Job ?",
"position": 16,
"acceptedAnswer": {
"@type": "Answer",
"text": "Le traitement inclut des antibiotiques pour les infections et des antihistaminiques pour les allergies."
}
},
{
"@type": "Question",
"name": "Des immunothérapies sont-elles recommandées ?",
"position": 17,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, l'immunothérapie peut être envisagée pour gérer les allergies et améliorer la réponse immunitaire."
}
},
{
"@type": "Question",
"name": "Les patients ont-ils besoin de soins réguliers ?",
"position": 18,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, un suivi régulier est essentiel pour surveiller les infections et ajuster le traitement."
}
},
{
"@type": "Question",
"name": "Peut-on guérir le syndrome de Job ?",
"position": 19,
"acceptedAnswer": {
"@type": "Answer",
"text": "Il n'existe pas de cure, mais les traitements peuvent aider à gérer les symptômes et les infections."
}
},
{
"@type": "Question",
"name": "Des traitements préventifs sont-ils disponibles ?",
"position": 20,
"acceptedAnswer": {
"@type": "Answer",
"text": "Des traitements préventifs, comme les vaccins, peuvent aider à réduire les infections."
}
},
{
"@type": "Question",
"name": "Quelles complications peuvent survenir ?",
"position": 21,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les complications incluent des infections graves, des abcès et des problèmes respiratoires chroniques."
}
},
{
"@type": "Question",
"name": "Le syndrome de Job augmente-t-il le risque de cancer ?",
"position": 22,
"acceptedAnswer": {
"@type": "Answer",
"text": "Il existe un risque accru de certains cancers, notamment les lymphomes, chez ces patients."
}
},
{
"@type": "Question",
"name": "Les infections peuvent-elles être mortelles ?",
"position": 23,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des infections graves peuvent être mortelles si elles ne sont pas traitées rapidement."
}
},
{
"@type": "Question",
"name": "Y a-t-il des complications dermatologiques ?",
"position": 24,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des infections cutanées récurrentes et des abcès peuvent survenir fréquemment."
}
},
{
"@type": "Question",
"name": "Les complications respiratoires sont-elles fréquentes ?",
"position": 25,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les patients souffrent souvent de pneumonies et d'autres infections respiratoires."
}
},
{
"@type": "Question",
"name": "Quels sont les facteurs de risque du syndrome de Job ?",
"position": 26,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les facteurs incluent des antécédents familiaux, des mutations génétiques et des infections fréquentes."
}
},
{
"@type": "Question",
"name": "Les enfants sont-ils plus à risque ?",
"position": 27,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, le syndrome de Job se manifeste souvent dans l'enfance, avec des infections récurrentes."
}
},
{
"@type": "Question",
"name": "Les personnes immunodéprimées sont-elles plus à risque ?",
"position": 28,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les personnes immunodéprimées peuvent avoir un risque accru de développer ce syndrome."
}
},
{
"@type": "Question",
"name": "Les allergies augmentent-elles le risque ?",
"position": 29,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les antécédents d'allergies peuvent être un facteur de risque pour le syndrome de Job."
}
},
{
"@type": "Question",
"name": "Les infections fréquentes sont-elles un indicateur ?",
"position": 30,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des infections fréquentes peuvent indiquer un risque accru de syndrome de Job."
}
}
]
}
]
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Tablet-based perimetry could be used to test for glaucomatous visual field defects in settings without easy access to perimeters, although few studies have assessed diagnostic accuracy of tablet-based...
This was a prospective, cross-sectional study of patients undergoing their first Humphrey Field Analyser (HFA) visual field test at a glaucoma clinic in India. Participants underwent 24-2 SITA Standar...
203 eyes from 115 participants were included, with 82 eyes classified as moderate or worse glaucoma. iPad perimetry had an area under the receiver operating characteristic (AUROC) curve of 0.64 (95% C...
iPad perimetry using the visualFields Easy application had inadequate diagnostic accuracy to be used as a screening tool for glaucoma in this South Indian population....
The benefit of protective headgear for recreational skiers is an ongoing debate in the snow sports industry, and there are a lot of opposing opinions. Due to the dynamic conditions in which winter spo...
To determine the horizontal extent of the binocular visual field (BVF) in subjects with horizontal strabismus and whether the BVF falls below the driving standard....
Adults with congenital esotropia and infantile exotropia ≤45 Prism Dioptres (PD), and subjects with orthotropia were recruited. The manifest angle of deviation was measured using a simultaneous prism ...
Forty-nine subjects were included: 10 with orthotropia, 20 with exotropia and 19 with esotropia. The horizontal extent of BVF (degrees) was significantly smaller in esotropes (122.8 ± 18.8) than in or...
The horizontal extent of BVF is significantly smaller and more variable in adults with congenital esotropia and may fall below the driving standard....
Largest study on visual fields in subjects with horizontal strabismus including an orthotropic control group who do not have diplopia and who would otherwise meet the driving standard. Visual field qu...
The findings of this study would suggest that people with an esotropia should be offered the opportunity to have a binocular visual field test before applying for a driving license. The DVLA may want ...
Visual abilities tend to vary predictably across the visual field-for simple low-level stimuli, visibility is better along the horizontal vs. vertical meridian and in the lower vs. upper visual field....
In natural environments, head movements are required to search for objects outside the field of view (FoV). Here we investigate the power of a salient target in an extended visual search array to faci...
Optic disc drusen (ODD) are calcified deposits in the prelaminar portion of the optic nerve head. Although often asymptomatic, these deposits can cause progressive visual field defects and vision loss...
This was a retrospective cohort study including 65 eyes of 43 patients with ODD from the Duke Ophthalmic Registry. All eyes had at least 12 months of follow-up and at least 3 reliable standard automat...
Subjects were followed for an average of 7.6 ± 5.3 years. The mean rate of SAP MD change was -0.23 ± 0.26 dB/year, ranging from -1.19 to 0.13 dB/year. Fifty-seven eyes (87.7%) had slow progression (sl...
Most eyes with ODD had slow rates of visual field loss over time. Age and baseline severity were significantly associated with faster rates of visual field loss....
To evaluate the association between baseline severity of visual field (VF) damage and the initial rates of VF progression with quality of life (QOL) outcomes over an extended follow-up in glaucoma....
Retrospective cohort study....
Both eyes of 167 glaucoma or suspected glaucoma patients were followed for 10.0±0.3 years. The National Eye Institute Visual Function Questionnaire (NEI-VFQ)-25 was performed at the end of the follow-...
All models demonstrated association of worse baseline severity of VF damage with worse subsequent NEI-VFQ-25 scores. Faster rates of decline in VF mean deviation of the better eye and the mean sensiti...
Baseline severity and initial rates of change of VF damage are associated with QOL outcomes over an extended follow-up. Assessment of longitudinal VF changes, especially in better eye, provides progno...
To investigate the intereye correlations between and differences in the rates of visual field (VF) progression in eyes with bilateral open-angle glaucoma....
Retrospective, longitudinal, observational study....
Patients with bilateral open-angle glaucoma with 8 or more reliable 30 - 2 standard automated perimetry tests over a period of more than 2 years were enrolled. The rate of change of the MD (MD slope) ...
One hundred eighty-eight eyes from 94 patients (56 women) were enrolled. A significant intereye correlation of the rates of visual field progression (P = .002) was found. The mean ± standard deviation...
A significant intereye correlation in the rate of VF progression was found in eyes with bilateral open-angle glaucoma. We showed the distributions and associated factors of intereye differences in VF ...
To investigate the influence of peripapillary retinoschisis (PRS) on visual field (VF) test results in patients with primary open angle glaucoma (POAG)....
Thirty eyes of 30 patients with POAG who had PRS at least once were included. All eyes were followed-up for a minimum 5 years at 4-6-month intervals. The occurrence of PRS was determined by circumpapi...
Global MD (p=0.345) and regional VF deviations (p=0.255) did not differ significantly between immediately after and just prior to PRS formation. Global MD (p=0.846) and regional VF deviations (p=0.758...
PRS has no short-term effect on the VF sensitivity. Therefore, VF test can still be useful for evaluating glaucomatous damage even in the presence of PRS compared with OCT....
Visual input is not equally processed over space. In recent years, a right visual field advantage during free walking and standing in orientation discrimination and contrast detection task was reporte...