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"description": "Comment diagnostique-t-on le syndrome de Job ?\nQuels tests sanguins sont utilisés ?\nLe syndrome de Job est-il héréditaire ?\nQuels signes cliniques indiquent ce syndrome ?\nPeut-on confondre ce syndrome avec d'autres ?",
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"name": "Comment diagnostique-t-on le syndrome de Job ?",
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"acceptedAnswer": {
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"text": "Le diagnostic repose sur l'évaluation clinique, les antécédents médicaux et des tests sanguins pour mesurer les IgE."
}
},
{
"@type": "Question",
"name": "Quels tests sanguins sont utilisés ?",
"position": 2,
"acceptedAnswer": {
"@type": "Answer",
"text": "Des tests mesurant les niveaux d'IgE et des analyses pour détecter des infections sont effectués."
}
},
{
"@type": "Question",
"name": "Le syndrome de Job est-il héréditaire ?",
"position": 3,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, il est souvent héréditaire, lié à des mutations génétiques spécifiques."
}
},
{
"@type": "Question",
"name": "Quels signes cliniques indiquent ce syndrome ?",
"position": 4,
"acceptedAnswer": {
"@type": "Answer",
"text": "Des infections cutanées, des pneumonies récurrentes et des éruptions cutanées sont des signes clés."
}
},
{
"@type": "Question",
"name": "Peut-on confondre ce syndrome avec d'autres ?",
"position": 5,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, il peut être confondu avec d'autres immunodéficiences, nécessitant des tests spécifiques."
}
},
{
"@type": "Question",
"name": "Quels sont les symptômes principaux du syndrome de Job ?",
"position": 6,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les symptômes incluent des infections récurrentes, des éruptions cutanées et des allergies."
}
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{
"@type": "Question",
"name": "Les éruptions cutanées sont-elles fréquentes ?",
"position": 7,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des éruptions cutanées, souvent prurigineuses, sont courantes chez les patients."
}
},
{
"@type": "Question",
"name": "Y a-t-il des symptômes respiratoires associés ?",
"position": 8,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les patients peuvent souffrir de pneumonies et d'autres infections respiratoires fréquentes."
}
},
{
"@type": "Question",
"name": "Le syndrome de Job cause-t-il des problèmes dentaires ?",
"position": 9,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des problèmes dentaires comme des abcès peuvent survenir en raison d'infections fréquentes."
}
},
{
"@type": "Question",
"name": "Les allergies sont-elles fréquentes dans ce syndrome ?",
"position": 10,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les patients présentent souvent des allergies, notamment aux acariens et aux pollens."
}
},
{
"@type": "Question",
"name": "Comment prévenir les infections chez les patients ?",
"position": 11,
"acceptedAnswer": {
"@type": "Answer",
"text": "Il est crucial d'encourager une bonne hygiène, des vaccinations et un suivi médical régulier."
}
},
{
"@type": "Question",
"name": "Les patients doivent-ils éviter certains aliments ?",
"position": 12,
"acceptedAnswer": {
"@type": "Answer",
"text": "Il n'y a pas de restrictions alimentaires spécifiques, mais une alimentation équilibrée est conseillée."
}
},
{
"@type": "Question",
"name": "Les vaccinations sont-elles importantes ?",
"position": 13,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les vaccinations sont essentielles pour prévenir les infections graves chez ces patients."
}
},
{
"@type": "Question",
"name": "Comment gérer les allergies dans ce syndrome ?",
"position": 14,
"acceptedAnswer": {
"@type": "Answer",
"text": "Éviter les allergènes connus et utiliser des antihistaminiques peut aider à gérer les allergies."
}
},
{
"@type": "Question",
"name": "Les soins dentaires sont-ils importants ?",
"position": 15,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des soins dentaires réguliers sont cruciaux pour prévenir les infections buccales."
}
},
{
"@type": "Question",
"name": "Quel est le traitement principal du syndrome de Job ?",
"position": 16,
"acceptedAnswer": {
"@type": "Answer",
"text": "Le traitement inclut des antibiotiques pour les infections et des antihistaminiques pour les allergies."
}
},
{
"@type": "Question",
"name": "Des immunothérapies sont-elles recommandées ?",
"position": 17,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, l'immunothérapie peut être envisagée pour gérer les allergies et améliorer la réponse immunitaire."
}
},
{
"@type": "Question",
"name": "Les patients ont-ils besoin de soins réguliers ?",
"position": 18,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, un suivi régulier est essentiel pour surveiller les infections et ajuster le traitement."
}
},
{
"@type": "Question",
"name": "Peut-on guérir le syndrome de Job ?",
"position": 19,
"acceptedAnswer": {
"@type": "Answer",
"text": "Il n'existe pas de cure, mais les traitements peuvent aider à gérer les symptômes et les infections."
}
},
{
"@type": "Question",
"name": "Des traitements préventifs sont-ils disponibles ?",
"position": 20,
"acceptedAnswer": {
"@type": "Answer",
"text": "Des traitements préventifs, comme les vaccins, peuvent aider à réduire les infections."
}
},
{
"@type": "Question",
"name": "Quelles complications peuvent survenir ?",
"position": 21,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les complications incluent des infections graves, des abcès et des problèmes respiratoires chroniques."
}
},
{
"@type": "Question",
"name": "Le syndrome de Job augmente-t-il le risque de cancer ?",
"position": 22,
"acceptedAnswer": {
"@type": "Answer",
"text": "Il existe un risque accru de certains cancers, notamment les lymphomes, chez ces patients."
}
},
{
"@type": "Question",
"name": "Les infections peuvent-elles être mortelles ?",
"position": 23,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des infections graves peuvent être mortelles si elles ne sont pas traitées rapidement."
}
},
{
"@type": "Question",
"name": "Y a-t-il des complications dermatologiques ?",
"position": 24,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des infections cutanées récurrentes et des abcès peuvent survenir fréquemment."
}
},
{
"@type": "Question",
"name": "Les complications respiratoires sont-elles fréquentes ?",
"position": 25,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les patients souffrent souvent de pneumonies et d'autres infections respiratoires."
}
},
{
"@type": "Question",
"name": "Quels sont les facteurs de risque du syndrome de Job ?",
"position": 26,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les facteurs incluent des antécédents familiaux, des mutations génétiques et des infections fréquentes."
}
},
{
"@type": "Question",
"name": "Les enfants sont-ils plus à risque ?",
"position": 27,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, le syndrome de Job se manifeste souvent dans l'enfance, avec des infections récurrentes."
}
},
{
"@type": "Question",
"name": "Les personnes immunodéprimées sont-elles plus à risque ?",
"position": 28,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les personnes immunodéprimées peuvent avoir un risque accru de développer ce syndrome."
}
},
{
"@type": "Question",
"name": "Les allergies augmentent-elles le risque ?",
"position": 29,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les antécédents d'allergies peuvent être un facteur de risque pour le syndrome de Job."
}
},
{
"@type": "Question",
"name": "Les infections fréquentes sont-elles un indicateur ?",
"position": 30,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des infections fréquentes peuvent indiquer un risque accru de syndrome de Job."
}
}
]
}
]
}
To compare clinical visual field outputs in glaucoma and healthy patients returned by the Humphrey Field Analyzer (HFA) and virtual reality (Virtual Field, VF) perimetry....
One eye of 54 glaucoma patients and 41 healthy subjects was prospectively tested (three times each in random order) using the HFA and VF perimeters (24-2 test grids). We extracted and compared global ...
The VF test was shorter (by 76 s) and had lower fixation losses (by 0.08) and false-positive rate (by 0.01) compared to the HFA (all p < 0.0001). Intraclass correlations were 0.86, 0.82 and 0.47 for M...
Virtual Field returns global results that are correlated with the HFA, but pointwise sensitivities were more variable. Differences in test-retest variability and defect detection by its current normat...
Intraocular pressure is currently the only known reliable, modifiable risk factor for the development and progression of glaucoma. Other risk factors for glaucoma include increasing age, myopia, decre...
Neuroanatomical variations across the visual field of human observers go along with corresponding variations of the perceived coarseness of visual stimuli. Here we show that horizontal gratings are pe...
Human visual performance changes dramatically both across (eccentricity) and around (polar angle) the visual field. Performance is better at the fovea, decreases with eccentricity, and is better along...
The earlier a person quits smoking the more likely is the optic nerve be spared from damage....
To investigate the effect of smoking cessation on visual field (VF) progression in glaucoma....
Primary open angle glaucoma patients with a minimum of 3 years follow-up and 5 VFs were included. Linear mixed models were used to investigate the effects of smoking on the rates of 24-2 VF mean devia...
Five hundred eleven eyes of 354 patients were included over the mean follow-up of 12.4 years. Mean baseline age (95% confidence interval) was 62.3 (61.2, 63.4) years. One hundred forty nine (42.1%) pa...
After ≥25 years of smoking cessation, the risk of VF progression in former heavy smokers becomes similar to never smokers. Long-term smoking cessation may be associated with lower VF progression in gl...
Previous studies have suggested behavioral patterns, such as visual attention and eye movements, relate to individual personality traits. However, these studies mainly focused on free visual tasks, an...
Despite, the potential clinical utility of 60-4 visual fields, they are not frequently used in clinical practice partly, due to the purported impact of facial contour on field defects. The purpose of ...
Subjects with no ocular pathology were included. Participants were subject to optical coherence tomography, 60-4 Swedish interactive thresholding algorithm visual field tests and photography. The pred...
30 healthy were enrolled. Three-dimensional facial reconstruction using a convolution neural network (CNN) was able to predict facial contour-dependent 60-4 visual field defects in 30 subjects without...
This pilot study reports the development of a CNN-enhanced platform capable of predicting 60-4 visual field defects in healthy controls based on facial contour. Further study with this platform may en...
To measure visual field (VF) rates of change after Ahmed Glaucoma Valve (AGV) implantation and to investigate risk factors for progression....
Retrospective, clinical cohort study....
Patients who underwent AGV implantation with at least 4 eligible postoperative VFs and 2 years of follow-up were included. Baseline, intraoperative, and postoperative data were collected. VF progressi...
A total of 173 eyes were included. The intraocular pressure (IOP) and number of glaucoma medications were significantly reduced from a median (interquartile range [IQR]) of 23.5 (12.1) mm Hg at baseli...
To our knowledge, this is the largest published series reporting long-term VF outcomes after glaucoma drainage device implantation. There is a continued, significant rate of VF decline after AGV surge...
To evaluate the relationship between interocular asymmetries of corneal hysteresis (CH) and visual field defects in Korean patients with glaucoma....
A total of 444 eyes from 222 participants with glaucoma in at least one eye were enrolled. CH was measured using an ocular response analyzer (Reichert Technologies Inc). Eyes of each participant were ...
Median (interquartile range) MD value was -3.71 dB (-6.87 to -1.30 dB) in the better eye and -10.20 dB (-16.32 to -5.62 dB) in the worse eye. When the correlation between the asymmetry of the MD value...
The interocular asymmetry of CH was significantly correlated with the interocular asymmetry of visual field defects in glaucoma....
To compare the accuracy of detecting moderate and rapid rates of glaucoma worsening over a 2-year period with different numbers of OCT scans and visual field (VF) tests in a large sample of glaucoma a...
Descriptive and simulation study....
The OCT sample comprised 12 150 eyes from 7392 adults with glaucoma or glaucoma suspect status followed up at the Wilmer Eye Institute from 2013 through 2021. The VF sample comprised 20 583 eyes from ...
Within-eye rates of change in retinal nerve fiber layer (RNFL) thickness and mean deviation (MD) were measured using linear regression. For each measured rate, simulated measurements of RNFL thickness...
The accuracy of diagnosing moderate and rapid rates of glaucoma worsening for different numbers of OCT scans and VF tests over a 2-year period....
Accuracy was less than 50% for both OCT and VF when diagnosing worsening after a 2-year period. OCT accuracy was 5 to 10 percentage points higher than VF accuracy at detecting moderate worsening and 1...
More frequent OCT scans and VF tests are needed to improve the accuracy of diagnosing glaucoma worsening. Accuracy greatly increases when relying on both OCT and VF to detect worsening....
The author(s) have no proprietary or commercial interest in any materials discussed in this article....