Titre : Leucémie à tricholeucocytes

Leucémie à tricholeucocytes : Questions médicales fréquentes

Termes MeSH sélectionnés :

Scleroderma, Localized
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tricholeucocytes ?\nQuels tests sont utilisés pour confirmer le diagnostic ?\nQuels signes dans le sang indiquent cette leucémie ?\nLa biopsie de la moelle osseuse est-elle toujours nécessaire ?\nQuels symptômes peuvent alerter sur cette maladie ?", "url": "https://questionsmedicales.fr/mesh/D007943?mesh_terms=Scleroderma,+Localized&page=3#section-diagnostic" }, { "@type": "MedicalWebPage", "name": "Symptômes", "headline": "Symptômes sur Leucémie à tricholeucocytes", "description": "Quels sont les symptômes courants de cette leucémie ?\nLa splénomégalie est-elle un symptôme fréquent ?\nPeut-on avoir des saignements avec cette maladie ?\nLes symptômes varient-ils d'un patient à l'autre ?\nY a-t-il des symptômes neurologiques associés ?", "url": "https://questionsmedicales.fr/mesh/D007943?mesh_terms=Scleroderma,+Localized&page=3#section-symptômes" }, { "@type": "MedicalWebPage", "name": "Prévention", "headline": "Prévention sur Leucémie à tricholeucocytes", "description": "Peut-on prévenir la leucémie à tricholeucocytes ?\nY a-t-il des facteurs de risque connus ?\nLe tabagisme influence-t-il le risque ?\nLes infections virales jouent-elles un rôle ?\nDes habitudes de vie saines peuvent-elles aider ?", "url": "https://questionsmedicales.fr/mesh/D007943?mesh_terms=Scleroderma,+Localized&page=3#section-prévention" }, { "@type": "MedicalWebPage", "name": "Traitements", "headline": "Traitements sur Leucémie à tricholeucocytes", "description": "Quels traitements sont disponibles pour cette leucémie ?\nL'interféron est-il efficace pour cette maladie ?\nLa splénectomie est-elle une option de traitement ?\nQuels sont les effets secondaires des traitements ?\nLa radiothérapie est-elle utilisée dans ce cas ?", "url": "https://questionsmedicales.fr/mesh/D007943?mesh_terms=Scleroderma,+Localized&page=3#section-traitements" }, { "@type": "MedicalWebPage", "name": "Complications", "headline": "Complications sur Leucémie à tricholeucocytes", "description": "Quelles complications peuvent survenir avec cette leucémie ?\nLa leucémie à tricholeucocytes peut-elle évoluer ?\nComment les infections sont-elles gérées ?\nY a-t-il un risque de rechute après traitement ?\nLes complications affectent-elles la qualité de vie ?", "url": "https://questionsmedicales.fr/mesh/D007943?mesh_terms=Scleroderma,+Localized&page=3#section-complications" }, { "@type": "MedicalWebPage", "name": "Facteurs de risque", "headline": "Facteurs de risque sur Leucémie à tricholeucocytes", "description": "Quels sont les principaux facteurs de risque ?\nL'âge joue-t-il un rôle dans le risque ?\nLes hommes sont-ils plus touchés que les femmes ?\nY a-t-il un lien avec d'autres maladies ?\nLes antécédents familiaux sont-ils significatifs ?", "url": "https://questionsmedicales.fr/mesh/D007943?mesh_terms=Scleroderma,+Localized&page=3#section-facteurs de risque" } ] }, { "@type": "FAQPage", "mainEntity": [ { "@type": "Question", "name": "Comment diagnostique-t-on la leucémie à tricholeucocytes ?", "position": 1, "acceptedAnswer": { "@type": "Answer", "text": "Le diagnostic repose sur une analyse sanguine et une biopsie de la moelle osseuse." } }, { "@type": "Question", "name": "Quels tests sont utilisés pour confirmer le diagnostic ?", "position": 2, "acceptedAnswer": { "@type": "Answer", "text": "Des tests immunophénotypiques et des analyses cytogénétiques sont souvent réalisés." } }, { "@type": "Question", "name": "Quels signes dans le sang indiquent cette leucémie ?", "position": 3, "acceptedAnswer": { "@type": "Answer", "text": "Une augmentation des lymphocytes atypiques et une thrombopénie sont typiques." } }, { "@type": "Question", "name": "La biopsie de la moelle osseuse est-elle toujours nécessaire ?", "position": 4, "acceptedAnswer": { "@type": "Answer", "text": "Oui, elle est essentielle pour confirmer la présence de cellules tricholeucocytaires." } }, { "@type": "Question", "name": "Quels symptômes peuvent alerter sur cette maladie ?", "position": 5, "acceptedAnswer": { "@type": "Answer", "text": "Fatigue, infections fréquentes et saignements inexpliqués sont des signes d'alerte." } }, { "@type": "Question", "name": "Quels sont les symptômes courants de cette leucémie ?", "position": 6, "acceptedAnswer": { "@type": "Answer", "text": "Les symptômes incluent fatigue, fièvre, infections fréquentes et douleurs abdominales." } }, { "@type": "Question", "name": "La splénomégalie est-elle un symptôme fréquent ?", "position": 7, "acceptedAnswer": { "@type": "Answer", "text": "Oui, l'augmentation de la taille de la rate est un symptôme courant." } }, { "@type": "Question", "name": "Peut-on avoir des saignements avec cette maladie ?", "position": 8, "acceptedAnswer": { "@type": "Answer", "text": "Oui, des saignements inhabituels peuvent survenir en raison de la thrombopénie." } }, { "@type": "Question", "name": "Les symptômes varient-ils d'un patient à l'autre ?", "position": 9, "acceptedAnswer": { "@type": "Answer", "text": "Oui, l'intensité et la combinaison des symptômes peuvent varier considérablement." } }, { "@type": "Question", "name": "Y a-t-il des symptômes neurologiques associés ?", "position": 10, "acceptedAnswer": { "@type": "Answer", "text": "Des symptômes neurologiques peuvent survenir, mais ils sont moins fréquents." } }, { "@type": "Question", "name": "Peut-on prévenir la leucémie à tricholeucocytes ?", "position": 11, "acceptedAnswer": { "@type": "Answer", "text": "Il n'existe pas de méthode de prévention spécifique pour cette maladie." } }, { "@type": "Question", "name": "Y a-t-il des facteurs de risque connus ?", "position": 12, "acceptedAnswer": { "@type": "Answer", "text": "L'exposition à des produits chimiques et des antécédents familiaux peuvent être des facteurs." } }, { "@type": "Question", "name": "Le tabagisme influence-t-il le risque ?", "position": 13, "acceptedAnswer": { "@type": "Answer", "text": "Le tabagisme n'est pas clairement lié à un risque accru de leucémie à tricholeucocytes." } }, { "@type": "Question", "name": "Les infections virales jouent-elles un rôle ?", "position": 14, "acceptedAnswer": { "@type": "Answer", "text": "Certaines infections virales peuvent être associées à un risque accru de leucémie." } }, { "@type": "Question", "name": "Des habitudes de vie saines peuvent-elles aider ?", "position": 15, "acceptedAnswer": { "@type": "Answer", "text": "Adopter un mode de vie sain peut contribuer à réduire le risque de maladies en général." } }, { "@type": "Question", "name": "Quels traitements sont disponibles pour cette leucémie ?", "position": 16, "acceptedAnswer": { "@type": "Answer", "text": "Les traitements incluent la chimiothérapie et l'immunothérapie, comme l'interféron." } }, { "@type": "Question", "name": "L'interféron est-il efficace pour cette maladie ?", "position": 17, "acceptedAnswer": { "@type": "Answer", "text": "Oui, l'interféron peut induire une rémission chez de nombreux patients." } }, { "@type": "Question", "name": "La splénectomie est-elle une option de traitement ?", "position": 18, "acceptedAnswer": { "@type": "Answer", "text": "Oui, la splénectomie peut être envisagée pour soulager les symptômes." } }, { "@type": "Question", "name": "Quels sont les effets secondaires des traitements ?", "position": 19, "acceptedAnswer": { "@type": "Answer", "text": "Les effets secondaires peuvent inclure fatigue, nausées et infections opportunistes." } }, { "@type": "Question", "name": "La radiothérapie est-elle utilisée dans ce cas ?", "position": 20, "acceptedAnswer": { "@type": "Answer", "text": "La radiothérapie est rarement utilisée, sauf dans des cas spécifiques." } }, { "@type": "Question", "name": "Quelles complications peuvent survenir avec cette leucémie ?", "position": 21, "acceptedAnswer": { "@type": "Answer", "text": "Les complications incluent infections graves, hémorragies et insuffisance médullaire." } }, { "@type": "Question", "name": "La leucémie à tricholeucocytes peut-elle évoluer ?", "position": 22, "acceptedAnswer": { "@type": "Answer", "text": "Dans certains cas, elle peut évoluer vers une leucémie aiguë, bien que cela soit rare." } }, { "@type": "Question", "name": "Comment les infections sont-elles gérées ?", "position": 23, "acceptedAnswer": { "@type": "Answer", "text": "Les infections sont traitées rapidement avec des antibiotiques et des soins appropriés." } }, { "@type": "Question", "name": "Y a-t-il un risque de rechute après traitement ?", "position": 24, "acceptedAnswer": { "@type": "Answer", "text": "Oui, des rechutes peuvent survenir, nécessitant un suivi régulier." } }, { "@type": "Question", "name": "Les complications affectent-elles la qualité de vie ?", "position": 25, "acceptedAnswer": { "@type": "Answer", "text": "Oui, les complications peuvent significativement impacter la qualité de vie des patients." } }, { "@type": "Question", "name": "Quels sont les principaux facteurs de risque ?", "position": 26, "acceptedAnswer": { "@type": "Answer", "text": "Les facteurs incluent l'exposition à des produits chimiques et des antécédents familiaux." } }, { "@type": "Question", "name": "L'âge joue-t-il un rôle dans le risque ?", "position": 27, "acceptedAnswer": { "@type": "Answer", "text": "Oui, la leucémie à tricholeucocytes est plus fréquente chez les adultes âgés de 50 à 70 ans." } }, { "@type": "Question", "name": "Les hommes sont-ils plus touchés que les femmes ?", "position": 28, "acceptedAnswer": { "@type": "Answer", "text": "Oui, cette leucémie est plus fréquente chez les hommes que chez les femmes." } }, { "@type": "Question", "name": "Y a-t-il un lien avec d'autres maladies ?", "position": 29, "acceptedAnswer": { "@type": "Answer", "text": "Certaines maladies auto-immunes peuvent augmenter le risque de leucémie à tricholeucocytes." } }, { "@type": "Question", "name": "Les antécédents familiaux sont-ils significatifs ?", "position": 30, "acceptedAnswer": { "@type": "Answer", "text": "Oui, avoir des antécédents familiaux de leucémie peut augmenter le risque." } } ] } ] }

Sources (10000 au total)

Management Options for Linear Scleroderma ("En Coup de Sabre").

En coup de sabre (ECDS) is a form of linear-scleroderma, primarily affecting the face. Despite effectiveness of pharmacological interventions in the management of lesions, sequelae of cutaneous deform... Review the existing surgical tools for the correction of "en coup de sabre" ECDS lesions and facial deformities.... The authors conducted a literature search for reports on surgical interventions for ECDS deformations, in the electronic databases of PubMed, Scopus, and Cochrane Library Databases.... Twenty-six publications reporting 39 patients were found in the literature. The average age of patients was 25 ± 4.7 years. Thirty-one of the patients were females. Six methods were found in the liter... Different surgical and minimally invasive options exist in the armamentarium of clinicians correcting ECDS deformities. Tailoring the method of correction to patient's needs and expectation is crucial...

Scleroderma cardiac crisis: A-life-threatening but reversible complication of systemic sclerosis.

To describe systemic sclerosis (SSc) heart involvement in the ICU.... We retrospectively studied patients with previous diagnosis of SSc admitted to the ICU for acute cardiac dysfunction between 2012 and mid-2021.... 9 female patients were included, mainly with diffuse SSc (n = 7, 78%). Six (67%) had digital ulcers. All but one patient complained about physical cardiac symptoms (n = 8, 89%), 5 (56%) had electrocar... We report an uncommon and specific severe acute life-threatening cardiac dysfunction in SSc patients, which can be reversible but remains associated with a poor long-term prognosis, which can be rever...

Exploring metabolism in scleroderma reveals opportunities for pharmacological intervention for therapy in fibrosis.

Recent evidence has indicated that alterations in energy metabolism play a critical role in the pathogenesis of fibrotic diseases. Studies have suggested that 'metabolic reprogramming' involving the g... Dermal fibroblasts were isolated from five SSc patients and five healthy donors. Cells were cultured in medium with/without TGF-β1 and with/without ALK5, pan-PIM or ATM kinase inhibitors. Extracellula... Enhanced mitochondrial respiration coupled to ATP production was observed in SSc fibroblasts at the expense of spare respiratory capacity. Although no difference was found in glycolysis when comparing... Our data provide evidence for a novel mechanism(s) by which SSc fibroblasts exhibit altered metabolic programs and highlight changes in respiration and dysregulated mitochondrial morphology and functi...

Three Distinct Transcriptional Profiles of Monocytes Associate with Disease Activity in Scleroderma Patients.

Patients with diffuse cutaneous systemic sclerosis (dcSSc) display a complex clinical phenotype. Transcriptional profiling of whole blood or tissue from patients are affected by changes in cellular co... SSc patients were recruited from the Prospective Registry for Early Systemic Sclerosis. Clinical data were collected, as well as peripheral blood for isolation of CMs and NCMs. Age-, sex-, and race-ma... We used an unbiased approach to cluster patients into 3 groups (groups A-C) based on the transcriptional signatures of CMs relative to controls. Each group maintained their characteristic transcriptio... We are the first to show that transcriptional signatures of CMs and NCMs can be used to unbiasedly stratify SSc patients and correlate with disease activity outcome measures....

Association of Race and Risk of Future Scleroderma Renal Crisis at Systemic Sclerosis Diagnosis.

Scleroderma renal crisis (SRC) is a rare and severe manifestation of systemic sclerosis (SSc). Although it is well documented that Black patients with SSc have worse morbidity and mortality than non-B... Using the electronic health record of the US Military Health System, we conducted a comprehensive chart review of each patient with SSc from 2005 to 2016. The final study cohort was comprised of 31 SR... Of 353 patients, 294 had identifiable race (79 Black, 215 non-Black). Thirteen of 79 Black patients (16.5%) versus 16 of 215 (7.4%) non-Black patients developed SRC (P = 0.02). On adjusted analysis, B... Black race was independently associated with a higher risk of future SRC. Further studies are needed to elucidate the mechanisms that underlie this important association....

[Role of cardiopulmonary exercise test in early diagnosis of pulmonary hypertension in scleroderma patients].

Pulmonary arterial hypertension (PAH) is a severe, high mortality and progressive disease. Early diagnosis and treatment improves the prognosis. Patients with scleroderma disease presents high risk of... Prospective study of 52 consecutive patients diagnosed of scleroderma in our health area, during 2 years (2018 and 2019). All of them undergo CPET, in addition to the annual systematic screening. Sens... Fifty-two CPET were performed, of which 16 suggested PAH. Resting RHC confirmed PAH in 5 patients and exercise RHC in 7 (diagnostic sensitivity of CPET together with rest and exercise catheterization ... CPET and exercise RHC could detect PAH earlier than established screening in patients with scleroderma disease, allowing early diagnosis....

Scleroderma-specific autoantibodies: Should they be included in the diagnostic work-up for Sjögren's syndrome?

Sicca complaints are a frequent reason for rheumatologic consultation. Testing for specific antibodies against Ro/SSA and La/SSB antigens and minor salivary gland (MSG) biopsy are among the main tools... Demographic, clinico-pathological, and laboratory data were recorded in 216 consecutive patients with sicca complaints. All study participants were tested for SSc-specific autoantibodies (against CENP... SSc-specific autoantibodies were detected in 41.7% (90/216) patients evaluated (19% at strong, 22.7% at medium titers) without significant differences between anti-Ro/SSA positive and negative groups.... SSc-specific autoantibodies are frequently detected among patients presenting with sicca complaints and at strong but not medium titers are independently associated with MSG biopsy positivity. Taken t...

Periostin overexpression in scleroderma cardiac tissue and its utility as a marker for disease complications.

To evaluate the levels of periostin in patients with systemic sclerosis (SSc) and their association with features of systemic sclerosis.... The levels of periostin were assessed in the serum of 106 SSc patients and 22 healthy controls and by immunofluorescence staining in cardiac tissue from 4 SSc patients and 4 controls. Serum periostin ... Periostin levels were higher in patients with SSc compared to controls and directly correlated to modified Rodnan skin score and echocardiography parameters of left ventricular measurements. Immunoflu... Periostin is elevated in SSc cardiac tissue in vivo and circulating levels of periostin are increased in SSc, correlating with the extent of disease duration, degree of skin fibrosis, and left ventric...