Oui, les AVC sont une complication fréquente et peuvent survenir à tout moment.
Accident vasculaire cérébralComplicationsMaladie de Moya-Moya
#3
Y a-t-il des risques de récidive d'AVC ?
Oui, les patients ont un risque accru de récidive d'AVC même après un traitement.
RécidiveAccident vasculaire cérébralMaladie de Moya-Moya
#4
Les complications peuvent-elles affecter la qualité de vie ?
Oui, les complications neurologiques peuvent significativement altérer la qualité de vie des patients.
Qualité de vieComplicationsMaladie de Moya-Moya
#5
Comment les complications sont-elles gérées ?
Les complications sont gérées par des soins médicaux appropriés et une réhabilitation ciblée.
Gestion des complicationsRéhabilitationMaladie de Moya-Moya
Facteurs de risque
5
#1
Quels sont les principaux facteurs de risque de Moya-Moya ?
Les antécédents familiaux, les maladies auto-immunes et certaines conditions génétiques sont des facteurs de risque.
Antécédents familiauxMaladies auto-immunesFacteurs de risque
#2
La race influence-t-elle le risque de Moya-Moya ?
Oui, la maladie est plus fréquente chez les personnes d'origine asiatique, notamment au Japon.
Origine ethniqueMaladie de Moya-MoyaFacteurs de risque
#3
L'âge joue-t-il un rôle dans le risque ?
Oui, la maladie de Moya-Moya est souvent diagnostiquée chez les enfants et les jeunes adultes.
ÂgeMaladie de Moya-MoyaFacteurs de risque
#4
Les maladies cardiovasculaires augmentent-elles le risque ?
Oui, les maladies cardiovasculaires peuvent augmenter le risque d'accidents vasculaires cérébraux associés.
Maladies cardiovasculairesAccident vasculaire cérébralMaladie de Moya-Moya
#5
Le tabagisme est-il un facteur de risque ?
Oui, le tabagisme est un facteur de risque connu qui peut aggraver la santé vasculaire.
TabagismeSanté vasculaireFacteurs de risque
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"@type": "Question",
"name": "Quels tests sont utilisés pour confirmer le diagnostic ?",
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"@type": "Question",
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"@type": "Question",
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"@type": "Question",
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"acceptedAnswer": {
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"@type": "Question",
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"position": 15,
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"@type": "Question",
"name": "Quels traitements sont disponibles pour Moya-Moya ?",
"position": 16,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les traitements incluent la chirurgie de dérivation et des médicaments pour gérer les symptômes."
}
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"@type": "Question",
"name": "La chirurgie est-elle toujours nécessaire ?",
"position": 17,
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}
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{
"@type": "Question",
"name": "Quels médicaments sont utilisés pour traiter Moya-Moya ?",
"position": 18,
"acceptedAnswer": {
"@type": "Answer",
"text": "Des anticoagulants et des antiplaquettaires sont souvent prescrits pour prévenir les AVC."
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"@type": "Question",
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"acceptedAnswer": {
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"@type": "Question",
"name": "Quelles sont les complications possibles de Moya-Moya ?",
"position": 21,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les complications incluent des AVC, des troubles cognitifs et des déficits neurologiques permanents."
}
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"@type": "Question",
"name": "Les AVC sont-ils fréquents chez les patients ?",
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"@type": "Question",
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"acceptedAnswer": {
"@type": "Answer",
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}
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"@type": "Question",
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"name": "Le tabagisme est-il un facteur de risque ?",
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Moyamoya disease (MMD), also known as abnormal cerebral vascular network disease, is characterized by progressive occlusion or stenosis of the internal carotid and cerebral arteries, as well as the fo...
Moyamoya disease (MMD) is a rare steno-occlusive disease of the bilateral internal carotid arteries that predominantly occurs in East Asia. Since the first description of the MMD by Suzuki and Takaku ...
Long-term outcomes are unknown in patients with asymptomatic moyamoya disease. In this report, we aimed to clarify their 5-year risk of stroke and its predictors....
We are conducting a multicenter, prospective cohort study (Asymptomatic Moyamoya Registry) in Japan. Participants were eligible if they were 20 to 70 years, had bilateral or unilateral moyamoya diseas...
Between 2012 and 2015, we enrolled 109 patients, of whom 103 patients with 182 involved hemispheres completed the 5-year follow-up. According to the findings on DSA and MRA, 143 hemispheres were judge...
The hemispheres with asymptomatic moyamoya disease may carry a 1.0% annual risk of stroke during the first 5 years, the majority of which are hemorrhagic stroke. Grade-2 choroidal anastomosis may pred...
URL: https://www....
gov; Unique identifier: UMIN000006640....
Moyamoya disease (MMD) is a rare chronic cerebrovascular disease, and the outcomes of bypass management in adult patients remain controversial....
To categorize adult MMD based on asymptomatic, ischemic, and hemorrhagic onset and compare the outcomes (death, hemorrhagic stroke [HS], and ischemic stroke [IS]) of bypass surgery (direct or indirect...
This retrospective, nationwide, population-based longitudinal cohort study used Korean National Health Insurance Research data to identify adults (aged ≥15 years) with MMD who were diagnosed between J...
Bypass surgery and conservative management....
Death constituted the primary outcome; secondary outcomes consisted of HS or IS. Kaplan-Meier survival curve and Cox proportional hazards regression analysis were applied. The propensity score-matchin...
A total of 19 700 patients (mean [SD] age, 45.43 [14.98] years; 12 766 [64.8%] female) were included. Compared with conservative management, bypass was associated with a reduced risk of death (adjuste...
The findings of this cohort study of bypass outcomes for patients with MMD emphasize the importance of tailoring management strategies in adult patients based on onset types....
Moyamoya disease (MMD) is a cerebrovascular narrowing and occlusive condition characterized by progressive stenosis of the terminal portion of the internal carotid artery and the formation of an abnor...
This study investigated the effect of indirect revascularization surgery in adult patients with moyamoya disease (MMD) complicated with hyperhomocysteinemia (HHcy), and the effect of HHcy on the progr...
A retrospective case-control study was conducted in patients with MMD, with or without HHcy (n = 123). Postoperative collateral angiogenesis was evaluated using the Matsushima grading system and disea...
There was no significant difference in the Suzuki stage composition ratios between the HHcy group and the non-HHcy group before and after surgery. Non-HHcy patients were more likely to grow new collat...
HHcy level may be a specific predictor of adverse clinical outcomes after EDAS in patients with MMD and a risk factor for poor collateral circulation and poor prognosis. Patients with MMD complicated ...
To explore the applicability of CT perfusion-derived parameters and collateral index in prediction of functional and clinical outcomes in patients with Moyamoya disease (MMD) who have not been treated...
All hemispheres were categorized into four groups: those with ischemic (IS) lesions, hemorrhagic (HE) lesions, subarachnoid hemorrhage (SAH) and normal hemisphere (NH). The clinical review included pr...
Between December 2020 and December 2021, 21 MMD patients (15 bilateral cases and 6 unilateral cases, for a total of 36 hemispheres) were retrospectively included. Compared with the NH group, the IS gr...
Among different imaging types, IS hemispheres were characterized by distinct changes of hemodynamic parameters. Collateral index of HIR could be considered a clinically accessible and promising indict...
Moyamoya disease (MMD) is an idiopathic occlusive cerebrovascular disorder. The development of collateral circulation originates from the dural and pial collaterals. Currently, the clinical significan...
Data from MMD patients were collected at Xiangya Hospital from January 2016 to April 2022. A collateral circulation grading system with scores was established, the dominant side of transdural collater...
A total of 102 patients were recruited. Results of digital subtraction angiography showed that 74 (72.5%) patients had transdural collaterals. The transdural collaterals were more common in patients w...
Transdural collateral circulation was common in MMD patients. The transdural collaterals were associated with the occurrence of infarction. Transdural collaterals were well established on the cerebral...
Eventually, 108 consecutive patients received 174 surgeries were enrolled, experienced new or expanded infarction occured in 13 (7.47%) surgeries, which showed higher Suzuki stage on the non-operative...
Revascularization was a safe option for patients with MMD, higher Suzuki stage on the non-operative side, PCA involvement, and intraoperative hypotension might be the risk factors for new or expanded ...
When it comes to the onset of moyamoya disease (MMD), environmental variables are crucial. Furthermore, there is confusion about the relationship between the gut microbiome, an environmental variable,...
A prospective case-control investigation was performed from June 2021 to May 2022. The fecal samples of patients with MMD and HC were obtained. Typically, 16S rRNA sequencing was employed to examine t...
This investigation involved a total of 60 MMD patients and 60 HC. The MMD group's Shannon and Chao 1 indices were substantially lower than those of the HC cohort. β-diversity was significantly differe...
The gut microbiota was altered in individuals with MMD, and was characterized by increased abundance of...