Titre : Uroporphyrines

Uroporphyrines : Questions médicales fréquentes

Termes MeSH sélectionnés :

Diffusion Tensor Imaging
{ "@context": "https://schema.org", "@graph": [ { "@type": "MedicalWebPage", "name": "Uroporphyrines : Questions médicales les plus fréquentes", "headline": "Uroporphyrines : Comprendre les symptômes, diagnostics et traitements", "description": "Guide complet et accessible sur les Uroporphyrines : explications, diagnostics, traitements et prévention. Information médicale validée destinée aux patients.", "datePublished": "2024-01-01", "dateModified": "2025-03-26", "inLanguage": "fr", "medicalAudience": [ { "@type": "MedicalAudience", "name": "Grand public", "audienceType": "Patient", "healthCondition": { "@type": "MedicalCondition", "name": "Uroporphyrines" }, "suggestedMinAge": 18, "suggestedGender": "unisex" }, { "@type": "MedicalAudience", "name": "Médecins", "audienceType": "Physician", "geographicArea": { "@type": "AdministrativeArea", "name": "France" } }, { "@type": "MedicalAudience", "name": "Chercheurs", "audienceType": "Researcher", "geographicArea": { "@type": "AdministrativeArea", "name": "International" } } ], "reviewedBy": { "@type": "Person", "name": "Dr Olivier Menir", "jobTitle": "Expert en Médecine", "description": "Expert en Médecine, Optimisation des Parcours de Soins et Révision Médicale", "url": "/static/pages/docteur-olivier-menir.html", "alumniOf": { "@type": "EducationalOrganization", "name": "Université Paris Descartes" } }, "isPartOf": { "@type": "MedicalWebPage", "name": "Porphyrines", "url": "https://questionsmedicales.fr/mesh/D011166", "about": { "@type": "MedicalCondition", "name": "Porphyrines", "code": { "@type": "MedicalCode", "code": "D011166", "codingSystem": "MeSH" }, "identifier": { "@type": "PropertyValue", "propertyID": "MeSH Tree", "value": "D23.767.727" } } }, "about": { "@type": "MedicalCondition", "name": "Uroporphyrines", "alternateName": "Uroporphyrins", "code": { "@type": "MedicalCode", "code": "D014578", "codingSystem": "MeSH" } }, "author": [ { "@type": "Person", "name": "Juliana Bragazzi Cunha", "url": "https://questionsmedicales.fr/author/Juliana%20Bragazzi%20Cunha", "affiliation": { "@type": "Organization", "name": "Center for Advanced Biotechnology and Medicine, Rutgers University, Piscataway, 08854, USA. bragazzi@umich.edu." } }, { "@type": "Person", "name": "Jared S Elenbaas", "url": "https://questionsmedicales.fr/author/Jared%20S%20Elenbaas", "affiliation": { "@type": "Organization", "name": "Medical Scientist Training Program, Washington University, Saint Louis, 63110, USA." } }, { "@type": "Person", "name": "Dhiman Maitra", "url": "https://questionsmedicales.fr/author/Dhiman%20Maitra", "affiliation": { "@type": "Organization", "name": "Center for Advanced Biotechnology and Medicine, Rutgers University, Piscataway, 08854, USA." } }, { "@type": "Person", "name": "Ning Kuo", "url": "https://questionsmedicales.fr/author/Ning%20Kuo", "affiliation": { "@type": "Organization", "name": "Center for Advanced Biotechnology and Medicine, Rutgers University, Piscataway, 08854, USA." } }, { "@type": "Person", "name": "Rodrigo Azuero-Dajud", "url": "https://questionsmedicales.fr/author/Rodrigo%20Azuero-Dajud", "affiliation": { "@type": "Organization", "name": "Center for Advanced Biotechnology and Medicine, Rutgers University, Piscataway, 08854, USA." } } ], "citation": [ { "@type": "ScholarlyArticle", "name": "Diffusion-tensor MR imaging of optic pathway in idiopathic intracranial hypertension.", "datePublished": "2023-07-04", "url": "https://questionsmedicales.fr/article/37401887", "identifier": { "@type": "PropertyValue", "propertyID": "DOI", "value": "10.1177/19714009231187346" } }, { "@type": "ScholarlyArticle", "name": "Analysis of changes in brain morphological structure of taekwondo athletes by diffusion tensor imaging.", "datePublished": "2023-02-13", "url": "https://questionsmedicales.fr/article/36791923", "identifier": { "@type": "PropertyValue", "propertyID": "DOI", "value": "10.1016/j.jchemneu.2023.102250" } }, { "@type": "ScholarlyArticle", "name": "Probabilistic tractography of the extracranial branches of the trigeminal nerve using diffusion tensor imaging.", "datePublished": "2023-06-22", "url": "https://questionsmedicales.fr/article/37347460", "identifier": { "@type": "PropertyValue", "propertyID": "DOI", "value": "10.1007/s00234-023-03184-z" } }, { "@type": "ScholarlyArticle", "name": "Chronic Cocaine Use and White Matter Coherence: A Diffusion Tensor Imaging Study.", "datePublished": "2023-02-22", "url": "https://questionsmedicales.fr/article/36971714", "identifier": { "@type": "PropertyValue", "propertyID": "DOI", "value": "10.15288/jsad.21-00410" } }, { "@type": "ScholarlyArticle", "name": "Test-retest reliability of diffusion tensor imaging scalars in 5-year-olds.", "datePublished": "2022-09-13", "url": "https://questionsmedicales.fr/article/36098477", "identifier": { "@type": "PropertyValue", "propertyID": "DOI", "value": "10.1002/hbm.26064" } } ], "breadcrumb": { "@type": "BreadcrumbList", "itemListElement": [ { "@type": "ListItem", "position": 1, "name": "questionsmedicales.fr", "item": "https://questionsmedicales.fr" }, { "@type": "ListItem", "position": 2, "name": "Facteurs biologiques", "item": "https://questionsmedicales.fr/mesh/D001685" }, { "@type": "ListItem", "position": 3, "name": "Pigments biologiques", "item": "https://questionsmedicales.fr/mesh/D010860" }, { "@type": "ListItem", "position": 4, "name": "Porphyrines", "item": "https://questionsmedicales.fr/mesh/D011166" }, { "@type": "ListItem", "position": 5, "name": "Uroporphyrines", "item": "https://questionsmedicales.fr/mesh/D014578" } ] } }, { "@type": "MedicalWebPage", "name": "Article complet : Uroporphyrines - Questions et réponses", "headline": "Questions et réponses médicales fréquentes sur Uroporphyrines", "description": "Une compilation de questions et réponses structurées, validées par des experts médicaux.", "datePublished": "2025-05-13", "inLanguage": "fr", "hasPart": [ { "@type": "MedicalWebPage", "name": "Diagnostic", "headline": "Diagnostic sur Uroporphyrines", "description": "Comment diagnostiquer une accumulation d'uroporphyrines ?\nQuels tests sont utilisés pour évaluer les uroporphyrines ?\nQuels symptômes peuvent indiquer un excès d'uroporphyrines ?\nLes tests génétiques sont-ils nécessaires pour le diagnostic ?\nQuelle est l'importance de l'historique médical dans le diagnostic ?", "url": "https://questionsmedicales.fr/mesh/D014578?mesh_terms=Diffusion+Tensor+Imaging&page=3#section-diagnostic" }, { "@type": "MedicalWebPage", "name": "Symptômes", "headline": "Symptômes sur Uroporphyrines", "description": "Quels sont les symptômes courants des troubles liés aux uroporphyrines ?\nLes uroporphyrines provoquent-elles des problèmes cutanés ?\nY a-t-il des symptômes psychologiques associés ?\nLes douleurs abdominales sont-elles fréquentes ?\nComment les symptômes varient-ils selon les individus ?", "url": "https://questionsmedicales.fr/mesh/D014578?mesh_terms=Diffusion+Tensor+Imaging&page=3#section-symptômes" }, { "@type": "MedicalWebPage", "name": "Prévention", "headline": "Prévention sur Uroporphyrines", "description": "Comment prévenir les troubles liés aux uroporphyrines ?\nUne alimentation spécifique peut-elle aider ?\nLes examens réguliers sont-ils nécessaires ?\nLe stress influence-t-il les troubles des uroporphyrines ?\nLes vaccinations sont-elles importantes pour ces patients ?", "url": "https://questionsmedicales.fr/mesh/D014578?mesh_terms=Diffusion+Tensor+Imaging&page=3#section-prévention" }, { "@type": "MedicalWebPage", "name": "Traitements", "headline": "Traitements sur Uroporphyrines", "description": "Quels traitements sont disponibles pour les troubles des uroporphyrines ?\nLes transfusions sanguines sont-elles une option de traitement ?\nLa photothérapie est-elle efficace pour ces troubles ?\nLes médicaments peuvent-ils réduire les niveaux d'uroporphyrines ?\nY a-t-il des traitements alternatifs recommandés ?", "url": "https://questionsmedicales.fr/mesh/D014578?mesh_terms=Diffusion+Tensor+Imaging&page=3#section-traitements" }, { "@type": "MedicalWebPage", "name": "Complications", "headline": "Complications sur Uroporphyrines", "description": "Quelles complications peuvent survenir avec les uroporphyrines ?\nLes troubles hépatiques sont-ils une complication possible ?\nComment les complications affectent-elles la qualité de vie ?\nLes complications sont-elles réversibles ?\nLes complications psychologiques sont-elles fréquentes ?", "url": "https://questionsmedicales.fr/mesh/D014578?mesh_terms=Diffusion+Tensor+Imaging&page=3#section-complications" }, { "@type": "MedicalWebPage", "name": "Facteurs de risque", "headline": "Facteurs de risque sur Uroporphyrines", "description": "Quels sont les principaux facteurs de risque des troubles des uroporphyrines ?\nL'alcoolisme est-il un facteur de risque ?\nLes médicaments peuvent-ils augmenter le risque ?\nLes infections sont-elles un facteur de risque ?\nLe sexe influence-t-il le risque de troubles ?", "url": "https://questionsmedicales.fr/mesh/D014578?mesh_terms=Diffusion+Tensor+Imaging&page=3#section-facteurs de risque" } ] }, { "@type": "FAQPage", "mainEntity": [ { "@type": "Question", "name": "Comment diagnostiquer une accumulation d'uroporphyrines ?", "position": 1, "acceptedAnswer": { "@type": "Answer", "text": "Un diagnostic se fait par analyse d'urine pour mesurer les niveaux d'uroporphyrines." } }, { "@type": "Question", "name": "Quels tests sont utilisés pour évaluer les uroporphyrines ?", "position": 2, "acceptedAnswer": { "@type": "Answer", "text": "Des tests de laboratoire, comme l'électrophorèse, sont utilisés pour évaluer les uroporphyrines." } }, { "@type": "Question", "name": "Quels symptômes peuvent indiquer un excès d'uroporphyrines ?", "position": 3, "acceptedAnswer": { "@type": "Answer", "text": "Des symptômes comme des douleurs abdominales et des troubles cutanés peuvent indiquer un excès." } }, { "@type": "Question", "name": "Les tests génétiques sont-ils nécessaires pour le diagnostic ?", "position": 4, "acceptedAnswer": { "@type": "Answer", "text": "Oui, des tests génétiques peuvent être nécessaires pour confirmer des troubles héréditaires." } }, { "@type": "Question", "name": "Quelle est l'importance de l'historique médical dans le diagnostic ?", "position": 5, "acceptedAnswer": { "@type": "Answer", "text": "L'historique médical aide à identifier des facteurs de risque et des antécédents familiaux." } }, { "@type": "Question", "name": "Quels sont les symptômes courants des troubles liés aux uroporphyrines ?", "position": 6, "acceptedAnswer": { "@type": "Answer", "text": "Les symptômes incluent douleurs abdominales, photosensibilité et troubles neurologiques." } }, { "@type": "Question", "name": "Les uroporphyrines provoquent-elles des problèmes cutanés ?", "position": 7, "acceptedAnswer": { "@type": "Answer", "text": "Oui, elles peuvent causer des éruptions cutanées et une sensibilité accrue au soleil." } }, { "@type": "Question", "name": "Y a-t-il des symptômes psychologiques associés ?", "position": 8, "acceptedAnswer": { "@type": "Answer", "text": "Des symptômes comme l'anxiété et la dépression peuvent être associés à ces troubles." } }, { "@type": "Question", "name": "Les douleurs abdominales sont-elles fréquentes ?", "position": 9, "acceptedAnswer": { "@type": "Answer", "text": "Oui, les douleurs abdominales sont un symptôme fréquent des troubles des uroporphyrines." } }, { "@type": "Question", "name": "Comment les symptômes varient-ils selon les individus ?", "position": 10, "acceptedAnswer": { "@type": "Answer", "text": "Les symptômes peuvent varier en fonction de la gravité et du type de trouble métabolique." } }, { "@type": "Question", "name": "Comment prévenir les troubles liés aux uroporphyrines ?", "position": 11, "acceptedAnswer": { "@type": "Answer", "text": "Éviter les déclencheurs comme l'alcool et certains médicaments peut aider à prévenir les crises." } }, { "@type": "Question", "name": "Une alimentation spécifique peut-elle aider ?", "position": 12, "acceptedAnswer": { "@type": "Answer", "text": "Oui, une alimentation riche en glucides et faible en graisses peut aider à prévenir les symptômes." } }, { "@type": "Question", "name": "Les examens réguliers sont-ils nécessaires ?", "position": 13, "acceptedAnswer": { "@type": "Answer", "text": "Oui, des examens réguliers peuvent aider à surveiller les niveaux d'uroporphyrines et prévenir les complications." } }, { "@type": "Question", "name": "Le stress influence-t-il les troubles des uroporphyrines ?", "position": 14, "acceptedAnswer": { "@type": "Answer", "text": "Oui, le stress peut aggraver les symptômes et déclencher des crises chez certains patients." } }, { "@type": "Question", "name": "Les vaccinations sont-elles importantes pour ces patients ?", "position": 15, "acceptedAnswer": { "@type": "Answer", "text": "Oui, les vaccinations peuvent prévenir des infections qui pourraient aggraver l'état de santé." } }, { "@type": "Question", "name": "Quels traitements sont disponibles pour les troubles des uroporphyrines ?", "position": 16, "acceptedAnswer": { "@type": "Answer", "text": "Les traitements incluent des modifications diététiques et des médicaments pour gérer les symptômes." } }, { "@type": "Question", "name": "Les transfusions sanguines sont-elles une option de traitement ?", "position": 17, "acceptedAnswer": { "@type": "Answer", "text": "Oui, les transfusions peuvent être utilisées dans certains cas pour traiter les complications." } }, { "@type": "Question", "name": "La photothérapie est-elle efficace pour ces troubles ?", "position": 18, "acceptedAnswer": { "@type": "Answer", "text": "La photothérapie peut aider à réduire les symptômes cutanés liés à la photosensibilité." } }, { "@type": "Question", "name": "Les médicaments peuvent-ils réduire les niveaux d'uroporphyrines ?", "position": 19, "acceptedAnswer": { "@type": "Answer", "text": "Oui, certains médicaments peuvent aider à réduire les niveaux d'uroporphyrines dans le corps." } }, { "@type": "Question", "name": "Y a-t-il des traitements alternatifs recommandés ?", "position": 20, "acceptedAnswer": { "@type": "Answer", "text": "Des traitements alternatifs comme l'acupuncture peuvent être envisagés pour soulager les symptômes." } }, { "@type": "Question", "name": "Quelles complications peuvent survenir avec les uroporphyrines ?", "position": 21, "acceptedAnswer": { "@type": "Answer", "text": "Les complications incluent des lésions cutanées, des douleurs chroniques et des troubles neurologiques." } }, { "@type": "Question", "name": "Les troubles hépatiques sont-ils une complication possible ?", "position": 22, "acceptedAnswer": { "@type": "Answer", "text": "Oui, des troubles hépatiques peuvent survenir en raison de l'accumulation d'uroporphyrines." } }, { "@type": "Question", "name": "Comment les complications affectent-elles la qualité de vie ?", "position": 23, "acceptedAnswer": { "@type": "Answer", "text": "Les complications peuvent réduire la qualité de vie en provoquant douleur et incapacité fonctionnelle." } }, { "@type": "Question", "name": "Les complications sont-elles réversibles ?", "position": 24, "acceptedAnswer": { "@type": "Answer", "text": "Certaines complications peuvent être réversibles avec un traitement approprié, d'autres non." } }, { "@type": "Question", "name": "Les complications psychologiques sont-elles fréquentes ?", "position": 25, "acceptedAnswer": { "@type": "Answer", "text": "Oui, des complications psychologiques comme l'anxiété peuvent survenir en raison de la maladie." } }, { "@type": "Question", "name": "Quels sont les principaux facteurs de risque des troubles des uroporphyrines ?", "position": 26, "acceptedAnswer": { "@type": "Answer", "text": "Les facteurs incluent des antécédents familiaux, des maladies hépatiques et des expositions environnementales." } }, { "@type": "Question", "name": "L'alcoolisme est-il un facteur de risque ?", "position": 27, "acceptedAnswer": { "@type": "Answer", "text": "Oui, l'alcoolisme peut aggraver les symptômes et augmenter le risque de complications." } }, { "@type": "Question", "name": "Les médicaments peuvent-ils augmenter le risque ?", "position": 28, "acceptedAnswer": { "@type": "Answer", "text": "Oui, certains médicaments peuvent déclencher des crises chez les personnes sensibles." } }, { "@type": "Question", "name": "Les infections sont-elles un facteur de risque ?", "position": 29, "acceptedAnswer": { "@type": "Answer", "text": "Oui, certaines infections peuvent exacerber les symptômes et augmenter le risque de complications." } }, { "@type": "Question", "name": "Le sexe influence-t-il le risque de troubles ?", "position": 30, "acceptedAnswer": { "@type": "Answer", "text": "Oui, certains troubles des uroporphyrines sont plus fréquents chez les femmes que chez les hommes." } } ] } ] }

Sources (10000 au total)

Diffusion-tensor MR imaging of optic pathway in idiopathic intracranial hypertension.

To investigate the role of diffusion tensor imaging (DTI) of optic pathway in patients with idiopathic intracranial hypertension (IIH).... This study included 41 IIH patients and 22 controls. They underwent DTI of the optic nerve (ON) and optic radiation (OR). Their fractional anostrophy (FA) and mean diffusivity (MD) were calculated by ... The optic nerve mean FA and MD of patients for reviewer-1 were 0.21 ± 0.047 and 2.189 ± 0.52 ×10... Our findings suggest that, IIH is associated mainly with pre-chiasmatic or ON involvement rather than post-chiasmatic parenchymal or OR involvement. DTI MD and FA parameters of the ON may be a reliabl...

Analysis of changes in brain morphological structure of taekwondo athletes by diffusion tensor imaging.

Taekwondo, which is the most preferred sport among the martial arts, is known to improve individuals physically, spiritually and mentally. The aim of this study is to reveal the effect of teakwondo sp... Total brain volume and volumes of white matter, gray matter, frontal lobe, precentral gyrus, corticospinal tract, basal nuclei, postcentral gyrus, hippocampus and amigdala and the ratio of these volum... An increase in total brain volume, gray matter, frontal lobe and precentral gyrus volume in athletes was associated with taekwondo training. When the ratio of brain parts to total brain volume was exa... The increase in the volume of gray matter, frontal lobe, postcentral gyrus and corticospinal tract together with the brain volume shows that taekwondo exercise contributes to physical, spiritual and m...

Probabilistic tractography of the extracranial branches of the trigeminal nerve using diffusion tensor imaging.

The peripheral course of the trigeminal nerves is complex and spans multiple bony foramen and tissue compartments throughout the face. Diffusion tensor imaging of these nerves is difficult due to the ... We prospectively acquired imaging data from six healthy adult participants with a 3.0-Tesla system, including T2-weighted short tau inversion recovery with variable flip angle (T2-STIR-SPACE) and read... All nerves in all subjects were tracked beyond the trigeminal ganglion. Tracts in the inferior alveolar and ophthalmic nerve exhibited the strongest signal and most consistently reached the most dista... This work demonstrates a method for consistently identifying and tracking the major nerve branches of the trigeminal nerve with diffusion tensor imaging....

Chronic Cocaine Use and White Matter Coherence: A Diffusion Tensor Imaging Study.

Chronic substance use and its effects on brain function and structure has long been of interest to clinicians and researchers. Prior cross-sectional comparisons of diffusion tensor imaging (DTI) metri... A total of 46 participants (21 healthy controls, 25 chronic cocaine users) were recruited from the Richmond, Virginia metropolitan area. Information regarding past and current substance use was collec... Consistent with previous DTI studies, significant differences were found between fractional anisotropy (FA) and axial diffusivity (AD) CocUD and controls, with CocUD showing lower FA and AD in the rig... These data align with previously reported declines in white matter coherence in chronic cocaine users. However, it is less clear whether comorbid alcohol consumption results in an additive deleterious...

Validation of Presurgical Simulation of White Matter Damage Using Diffusion Tensor Imaging.

The understanding of white matter (WM) was revolutionized by the emergence of tractography based on diffusion tensor imaging (DTI). Currently, DTI simulations are implemented in preoperative planning ... WM surgical damage was preoperatively simulated by creating a 3-dimensional volume representing the endoscope or the surgical trajectory. This volume was used as an additional region of interest in th... The preoperative and postoperative DTI studies of 30 patients undergoing various neurosurgical approaches were processed. The correlation between simulated injuries and postoperative studies was high ... Presurgical simulation of WM fascicles based on DTI is consistent with postoperative DTI studies. These findings require further validation by neurophysiological and clinical correlation....

Simultaneous Acquisition of Diffusion Tensor and Dynamic Diffusion MRI.

Dynamic diffusion magnetic resonance imaging (ddMRI) metrics can assess transient microstructural alterations in tissue diffusivity but requires additional scan time hindering its clinical application... To determine whether a diffusion gradient table can simultaneously acquire data to estimate dynamic and diffusion tensor imaging (DTI) metrics.... Prospective.... Seven healthy subjects, 39 epilepsy patients (15 female, 31 male, age ± 15).... Two-dimensional diffusion MRI (b = 1000 s/mm... Fifteen direction DTI was repeated twice for within-session test-retest measurements in healthy subjects. Bland-Altman analysis computed bias and limits of agreement for DTI metrics using test-retest ... Bland-Altman and ICC analysis using a P-value of 0.05 for statistical significance.... Correlations of mean diffusivity (MD), axial diffusivity (AD), and radial diffusivity (RD) were strong and significant in gray (ICC > 0.95) and white matter (ICC > 0.95) between standard vs. nested cu... A nested cubes diffusion gradient table produces tensor-based and dynamic diffusion measurements in a single acquisition.... 2 TECHNICAL EFFICACY: Stage 1....