Titre : Anticorps anti-cytoplasme des polynucléaires neutrophiles

Anticorps anti-cytoplasme des polynucléaires neutrophiles : Questions médicales fréquentes

Termes MeSH sélectionnés :

Myotonic Dystrophy
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sur Anticorps anti-cytoplasme des polynucléaires neutrophiles", "description": "Quels sont les symptômes associés aux ANCA ?\nLes ANCA provoquent-ils des symptômes respiratoires ?\nY a-t-il des symptômes cutanés liés aux ANCA ?\nLes ANCA affectent-ils les reins ?\nLes symptômes des ANCA sont-ils similaires à d'autres maladies ?", "url": "https://questionsmedicales.fr/mesh/D019268?mesh_terms=Myotonic+Dystrophy&page=3#section-symptômes" }, { "@type": "MedicalWebPage", "name": "Prévention", "headline": "Prévention sur Anticorps anti-cytoplasme des polynucléaires neutrophiles", "description": "Peut-on prévenir les maladies liées aux ANCA ?\nLes vaccinations sont-elles recommandées pour les patients ANCA ?\nComment réduire le risque de complications ?\nL'évitement de certains médicaments est-il conseillé ?\nLe stress influence-t-il les maladies ANCA ?", "url": "https://questionsmedicales.fr/mesh/D019268?mesh_terms=Myotonic+Dystrophy&page=3#section-prévention" }, { "@type": "MedicalWebPage", "name": "Traitements", "headline": "Traitements sur Anticorps anti-cytoplasme des polynucléaires neutrophiles", "description": "Quels traitements sont utilisés pour les ANCA ?\nLes traitements sont-ils personnalisés pour chaque patient ?\nLes ANCA nécessitent-ils un suivi régulier ?\nY a-t-il des effets secondaires aux traitements ?\nLes traitements peuvent-ils guérir les ANCA ?", "url": "https://questionsmedicales.fr/mesh/D019268?mesh_terms=Myotonic+Dystrophy&page=3#section-traitements" }, { "@type": "MedicalWebPage", "name": "Complications", "headline": "Complications sur Anticorps anti-cytoplasme des polynucléaires neutrophiles", "description": "Quelles sont les complications possibles des ANCA ?\nLes ANCA peuvent-ils entraîner des infections ?\nY a-t-il un risque de cancer associé aux ANCA ?\nLes complications sont-elles réversibles ?\nComment surveiller les complications des ANCA ?", "url": "https://questionsmedicales.fr/mesh/D019268?mesh_terms=Myotonic+Dystrophy&page=3#section-complications" }, { "@type": "MedicalWebPage", "name": "Facteurs de risque", "headline": "Facteurs de risque sur Anticorps anti-cytoplasme des polynucléaires neutrophiles", "description": "Quels sont les facteurs de risque des ANCA ?\nLe sexe influence-t-il le risque d'ANCA ?\nL'âge joue-t-il un rôle dans le développement des ANCA ?\nCertaines professions augmentent-elles le risque d'ANCA ?\nLes infections antérieures sont-elles un facteur de risque ?", "url": "https://questionsmedicales.fr/mesh/D019268?mesh_terms=Myotonic+Dystrophy&page=3#section-facteurs de risque" } ] }, { "@type": "FAQPage", "mainEntity": [ { "@type": "Question", "name": "Comment diagnostiquer la présence d'ANCA ?", "position": 1, "acceptedAnswer": { "@type": "Answer", "text": "Un test sanguin spécifique détecte les ANCA dans le sérum du patient." } }, { "@type": "Question", "name": "Quels tests sont utilisés pour les ANCA ?", "position": 2, "acceptedAnswer": { "@type": "Answer", "text": "Les tests ELISA et indirect immunofluorescence sont couramment utilisés." } }, { "@type": "Question", "name": "Les ANCA sont-ils toujours présents dans les maladies ?", "position": 3, "acceptedAnswer": { "@type": "Answer", "text": "Non, leur présence varie selon la maladie et le stade de l'inflammation." } }, { "@type": "Question", "name": "Quel rôle joue l'historique médical dans le diagnostic ?", "position": 4, "acceptedAnswer": { "@type": "Answer", "text": "L'historique aide à identifier les symptômes et les antécédents de maladies auto-immunes." } }, { "@type": "Question", "name": "Les ANCA peuvent-ils être détectés chez des personnes saines ?", "position": 5, "acceptedAnswer": { "@type": "Answer", "text": "Oui, des ANCA peuvent être présents à faible niveau chez des individus sains." } }, { "@type": "Question", "name": "Quels sont les symptômes associés aux ANCA ?", "position": 6, "acceptedAnswer": { "@type": "Answer", "text": "Les symptômes incluent fatigue, fièvre, perte de poids et douleurs articulaires." } }, { "@type": "Question", "name": "Les ANCA provoquent-ils des symptômes respiratoires ?", "position": 7, "acceptedAnswer": { "@type": "Answer", "text": "Oui, ils peuvent causer des symptômes respiratoires comme la toux et l'essoufflement." } }, { "@type": "Question", "name": "Y a-t-il des symptômes cutanés liés aux ANCA ?", "position": 8, "acceptedAnswer": { "@type": "Answer", "text": "Des éruptions cutanées et des lésions peuvent apparaître chez certains patients." } }, { "@type": "Question", "name": "Les ANCA affectent-ils les reins ?", "position": 9, "acceptedAnswer": { "@type": "Answer", "text": "Oui, ils peuvent entraîner des atteintes rénales, comme la glomérulonéphrite." } }, { "@type": "Question", "name": "Les symptômes des ANCA sont-ils similaires à d'autres maladies ?", "position": 10, "acceptedAnswer": { "@type": "Answer", "text": "Oui, ils peuvent être confondus avec d'autres maladies auto-immunes ou inflammatoires." } }, { "@type": "Question", "name": "Peut-on prévenir les maladies liées aux ANCA ?", "position": 11, "acceptedAnswer": { "@type": "Answer", "text": "Il n'existe pas de méthode de prévention spécifique, mais un mode de vie sain aide." } }, { "@type": "Question", "name": "Les vaccinations sont-elles recommandées pour les patients ANCA ?", "position": 12, "acceptedAnswer": { "@type": "Answer", "text": "Oui, les vaccinations peuvent être recommandées pour prévenir les infections." } }, { "@type": "Question", "name": "Comment réduire le risque de complications ?", "position": 13, "acceptedAnswer": { "@type": "Answer", "text": "Un suivi médical régulier et une gestion proactive des symptômes sont essentiels." } }, { "@type": "Question", "name": "L'évitement de certains médicaments est-il conseillé ?", "position": 14, "acceptedAnswer": { "@type": "Answer", "text": "Oui, certains médicaments peuvent aggraver les symptômes et doivent être évités." } }, { "@type": "Question", "name": "Le stress influence-t-il les maladies ANCA ?", "position": 15, "acceptedAnswer": { "@type": "Answer", "text": "Oui, le stress peut aggraver les symptômes et doit être géré efficacement." } }, { "@type": "Question", "name": "Quels traitements sont utilisés pour les ANCA ?", "position": 16, "acceptedAnswer": { "@type": "Answer", "text": "Les corticostéroïdes et les immunosuppresseurs sont souvent prescrits." } }, { "@type": "Question", "name": "Les traitements sont-ils personnalisés pour chaque patient ?", "position": 17, "acceptedAnswer": { "@type": "Answer", "text": "Oui, le traitement est adapté en fonction de la gravité et des symptômes du patient." } }, { "@type": "Question", "name": "Les ANCA nécessitent-ils un suivi régulier ?", "position": 18, "acceptedAnswer": { "@type": "Answer", "text": "Oui, un suivi régulier est essentiel pour ajuster le traitement et surveiller l'évolution." } }, { "@type": "Question", "name": "Y a-t-il des effets secondaires aux traitements ?", "position": 19, "acceptedAnswer": { "@type": "Answer", "text": "Oui, les traitements peuvent avoir des effets secondaires comme l'infection ou l'ostéoporose." } }, { "@type": "Question", "name": "Les traitements peuvent-ils guérir les ANCA ?", "position": 20, "acceptedAnswer": { "@type": "Answer", "text": "Il n'existe pas de cure, mais les traitements peuvent contrôler les symptômes et la progression." } }, { "@type": "Question", "name": "Quelles sont les complications possibles des ANCA ?", "position": 21, "acceptedAnswer": { "@type": "Answer", "text": "Les complications incluent des atteintes rénales, pulmonaires et cardiovasculaires." } }, { "@type": "Question", "name": "Les ANCA peuvent-ils entraîner des infections ?", "position": 22, "acceptedAnswer": { "@type": "Answer", "text": "Oui, les traitements immunosuppresseurs augmentent le risque d'infections." } }, { "@type": "Question", "name": "Y a-t-il un risque de cancer associé aux ANCA ?", "position": 23, "acceptedAnswer": { "@type": "Answer", "text": "Certaines études suggèrent un risque accru de certains cancers chez les patients ANCA." } }, { "@type": "Question", "name": "Les complications sont-elles réversibles ?", "position": 24, "acceptedAnswer": { "@type": "Answer", "text": "Certaines complications peuvent être réversibles avec un traitement approprié." } }, { "@type": "Question", "name": "Comment surveiller les complications des ANCA ?", "position": 25, "acceptedAnswer": { "@type": "Answer", "text": "Des examens réguliers et des tests sanguins aident à surveiller les complications." } }, { "@type": "Question", "name": "Quels sont les facteurs de risque des ANCA ?", "position": 26, "acceptedAnswer": { "@type": "Answer", "text": "Les facteurs incluent des antécédents familiaux, le tabagisme et certaines infections." } }, { "@type": "Question", "name": "Le sexe influence-t-il le risque d'ANCA ?", "position": 27, "acceptedAnswer": { "@type": "Answer", "text": "Oui, les femmes sont plus souvent touchées par les maladies associées aux ANCA." } }, { "@type": "Question", "name": "L'âge joue-t-il un rôle dans le développement des ANCA ?", "position": 28, "acceptedAnswer": { "@type": "Answer", "text": "Oui, les ANCA apparaissent généralement chez les adultes jeunes à moyens d'âge." } }, { "@type": "Question", "name": "Certaines professions augmentent-elles le risque d'ANCA ?", "position": 29, "acceptedAnswer": { "@type": "Answer", "text": "Oui, les professions exposant à des produits chimiques peuvent augmenter le risque." } }, { "@type": "Question", "name": "Les infections antérieures sont-elles un facteur de risque ?", "position": 30, "acceptedAnswer": { "@type": "Answer", "text": "Oui, certaines infections peuvent déclencher la production d'ANCA chez des individus prédisposés." } } ] } ] }

Sources (1547 au total)

Milestones of progression in myotonic dystrophy type 1 and type 2.

Disease progression in myotonic dystrophy (DM) is marked by milestone events when functional thresholds are crossed. DM type 2 (DM2) is considered less severe than DM type 1 (DM1), but it is unknown w... We studied a large cohort of adult participants in a national registry of DM1 and DM2. Using annual surveys from participants, we ascertained milestone events for motor involvement (use of cane, walke... Mean follow-up of registry participants (929 DM1 and 222 DM2 patients) was 7 years. Disability and motor milestones occurred at earlier ages in DM1 than in DM2. In contrast, the risk of diabetes was h... Milestone events recorded through registries can be used to assess long-term impact of DM in large cohorts. Except for diabetes, the age-related risk of milestone events is greater in DM1 than in DM2....

Cardiac magnetic resonance findings and prognosis in type 1 myotonic dystrophy.

Cardiac involvement is a major determinant of prognosis in type 1 myotonic dystrophy (DM1), but limited information is available about myocardial remodeling and tissue changes. The aim of the study wa... We retrospectively identified all DM1 patients referred from a neurology unit to our CMR laboratory from 2009 to 2020.... Thirty-four patients were included (aged 45 ± 12, 62% male individuals) and compared with 68 age-matched and gender-matched healthy volunteers (43 male individuals, age 48 ± 15 years). At CMR, biventr... DM1 patients display structural and functional cardiac abnormalities, with variable degrees of cardiac muscle hypotrophy, fibrosis, and fatty infiltration. Such changes, as evaluated by CMR, seem to b...

Frequency and type of cancers in myotonic dystrophy: A retrospective cross-sectional study.

Myotonic dystrophies (DMs) are autosomal dominant diseases in which expression of a mutant expanded repeat mRNA leads to abnormal splicing of downstream effector genes thought to be responsible for th... A retrospective, cross-sectional study was carried out on patients with genetically confirmed DM1, DM2, facioscapulohumeral muscular dystrophy (FSHD), and oculopharyngeal muscular dystrophy (OPMD) at ... One hundred eighty-five DM1, 67 DM2, 187 FSHD, and 109 OPMD patients were included. Relative to non-DM, DM patients had an increased cancer risk that was independent of age and sex. Specifically, an i... In addition to current consensus-based care recommendations, our findings prompt consideration of screening for skin, urological, and hematological cancers in DM2 patients, and screening of ovarian ma...

microRNA-mRNA expression profiles in the skeletal muscle of myotonic dystrophy type 1.

Myotonic dystrophy type 1 (DM1) is the most common muscular dystrophy in adults, yet there are currently no disease-modifying treatments. Disrupted miRNA expressions may lead to dysregulation of targe... We used microarray platforms to examine the miRNA/mRNA expression profiles in skeletal muscle biopsies derived from DM1 patients and matched controls. Bioinformatics analysis and dual-luciferase repor... Twenty-three differentially expressed miRNAs and 135 differentially expressed genes were identified. qPCR confirmed that miR-3201, myogenic factor 5 (MYF5), myogenic differentiation 1 (MYOD1), CUGBP, ... Those results implied that the observed miRNA/mRNA dysregulation could contribute to specific functions and pathways related to DM1 pathogenesis, highlighting the dysfunction of miR-196a and CELF2....

Cognitive phenotype of childhood myotonic dystrophy type 1: A multicenter pooled analysis.

There is clear evidence for brain involvement in childhood myotonic dystrophy type 1 (DM1) from imaging studies and the prevalence of intellectual impairment and neurodevelopmental disorders. The cogn... Neuropsychological examination reports of 45 children aged 2-17 y were analyzed. All cognitive subtests used in this cohort were pooled in 10 cognitive domains. For every patient a composite z-score w... The nature and extent of neuropsychological examinations differed between centers and patients. The domains with the highest frequency of major cognitive impairment were social cognition (4/9 children... Children with DM1 may have specific cognitive deficits, most frequently affecting working memory, attention, and visuospatial functions, in addition to the previously described global intellectual imp...