Anticorps anti-cytoplasme des polynucléaires neutrophiles : Questions médicales fréquentes
Nom anglais: Antibodies, Antineutrophil Cytoplasmic
Descriptor UI:D019268
Tree Number:D23.101.050
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"name": "Diagnostic",
"headline": "Diagnostic sur Anticorps anti-cytoplasme des polynucléaires neutrophiles",
"description": "Comment diagnostiquer la présence d'ANCA ?\nQuels tests sont utilisés pour les ANCA ?\nLes ANCA sont-ils toujours présents dans les maladies ?\nQuel rôle joue l'historique médical dans le diagnostic ?\nLes ANCA peuvent-ils être détectés chez des personnes saines ?",
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"name": "Symptômes",
"headline": "Symptômes sur Anticorps anti-cytoplasme des polynucléaires neutrophiles",
"description": "Quels sont les symptômes associés aux ANCA ?\nLes ANCA provoquent-ils des symptômes respiratoires ?\nY a-t-il des symptômes cutanés liés aux ANCA ?\nLes ANCA affectent-ils les reins ?\nLes symptômes des ANCA sont-ils similaires à d'autres maladies ?",
"url": "https://questionsmedicales.fr/mesh/D019268?page=17#section-symptômes"
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"name": "Prévention",
"headline": "Prévention sur Anticorps anti-cytoplasme des polynucléaires neutrophiles",
"description": "Peut-on prévenir les maladies liées aux ANCA ?\nLes vaccinations sont-elles recommandées pour les patients ANCA ?\nComment réduire le risque de complications ?\nL'évitement de certains médicaments est-il conseillé ?\nLe stress influence-t-il les maladies ANCA ?",
"url": "https://questionsmedicales.fr/mesh/D019268?page=17#section-prévention"
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"name": "Traitements",
"headline": "Traitements sur Anticorps anti-cytoplasme des polynucléaires neutrophiles",
"description": "Quels traitements sont utilisés pour les ANCA ?\nLes traitements sont-ils personnalisés pour chaque patient ?\nLes ANCA nécessitent-ils un suivi régulier ?\nY a-t-il des effets secondaires aux traitements ?\nLes traitements peuvent-ils guérir les ANCA ?",
"url": "https://questionsmedicales.fr/mesh/D019268?page=17#section-traitements"
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"headline": "Complications sur Anticorps anti-cytoplasme des polynucléaires neutrophiles",
"description": "Quelles sont les complications possibles des ANCA ?\nLes ANCA peuvent-ils entraîner des infections ?\nY a-t-il un risque de cancer associé aux ANCA ?\nLes complications sont-elles réversibles ?\nComment surveiller les complications des ANCA ?",
"url": "https://questionsmedicales.fr/mesh/D019268?page=17#section-complications"
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"name": "Facteurs de risque",
"headline": "Facteurs de risque sur Anticorps anti-cytoplasme des polynucléaires neutrophiles",
"description": "Quels sont les facteurs de risque des ANCA ?\nLe sexe influence-t-il le risque d'ANCA ?\nL'âge joue-t-il un rôle dans le développement des ANCA ?\nCertaines professions augmentent-elles le risque d'ANCA ?\nLes infections antérieures sont-elles un facteur de risque ?",
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"@type": "Question",
"name": "Comment diagnostiquer la présence d'ANCA ?",
"position": 1,
"acceptedAnswer": {
"@type": "Answer",
"text": "Un test sanguin spécifique détecte les ANCA dans le sérum du patient."
}
},
{
"@type": "Question",
"name": "Quels tests sont utilisés pour les ANCA ?",
"position": 2,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les tests ELISA et indirect immunofluorescence sont couramment utilisés."
}
},
{
"@type": "Question",
"name": "Les ANCA sont-ils toujours présents dans les maladies ?",
"position": 3,
"acceptedAnswer": {
"@type": "Answer",
"text": "Non, leur présence varie selon la maladie et le stade de l'inflammation."
}
},
{
"@type": "Question",
"name": "Quel rôle joue l'historique médical dans le diagnostic ?",
"position": 4,
"acceptedAnswer": {
"@type": "Answer",
"text": "L'historique aide à identifier les symptômes et les antécédents de maladies auto-immunes."
}
},
{
"@type": "Question",
"name": "Les ANCA peuvent-ils être détectés chez des personnes saines ?",
"position": 5,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des ANCA peuvent être présents à faible niveau chez des individus sains."
}
},
{
"@type": "Question",
"name": "Quels sont les symptômes associés aux ANCA ?",
"position": 6,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les symptômes incluent fatigue, fièvre, perte de poids et douleurs articulaires."
}
},
{
"@type": "Question",
"name": "Les ANCA provoquent-ils des symptômes respiratoires ?",
"position": 7,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, ils peuvent causer des symptômes respiratoires comme la toux et l'essoufflement."
}
},
{
"@type": "Question",
"name": "Y a-t-il des symptômes cutanés liés aux ANCA ?",
"position": 8,
"acceptedAnswer": {
"@type": "Answer",
"text": "Des éruptions cutanées et des lésions peuvent apparaître chez certains patients."
}
},
{
"@type": "Question",
"name": "Les ANCA affectent-ils les reins ?",
"position": 9,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, ils peuvent entraîner des atteintes rénales, comme la glomérulonéphrite."
}
},
{
"@type": "Question",
"name": "Les symptômes des ANCA sont-ils similaires à d'autres maladies ?",
"position": 10,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, ils peuvent être confondus avec d'autres maladies auto-immunes ou inflammatoires."
}
},
{
"@type": "Question",
"name": "Peut-on prévenir les maladies liées aux ANCA ?",
"position": 11,
"acceptedAnswer": {
"@type": "Answer",
"text": "Il n'existe pas de méthode de prévention spécifique, mais un mode de vie sain aide."
}
},
{
"@type": "Question",
"name": "Les vaccinations sont-elles recommandées pour les patients ANCA ?",
"position": 12,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les vaccinations peuvent être recommandées pour prévenir les infections."
}
},
{
"@type": "Question",
"name": "Comment réduire le risque de complications ?",
"position": 13,
"acceptedAnswer": {
"@type": "Answer",
"text": "Un suivi médical régulier et une gestion proactive des symptômes sont essentiels."
}
},
{
"@type": "Question",
"name": "L'évitement de certains médicaments est-il conseillé ?",
"position": 14,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, certains médicaments peuvent aggraver les symptômes et doivent être évités."
}
},
{
"@type": "Question",
"name": "Le stress influence-t-il les maladies ANCA ?",
"position": 15,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, le stress peut aggraver les symptômes et doit être géré efficacement."
}
},
{
"@type": "Question",
"name": "Quels traitements sont utilisés pour les ANCA ?",
"position": 16,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les corticostéroïdes et les immunosuppresseurs sont souvent prescrits."
}
},
{
"@type": "Question",
"name": "Les traitements sont-ils personnalisés pour chaque patient ?",
"position": 17,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, le traitement est adapté en fonction de la gravité et des symptômes du patient."
}
},
{
"@type": "Question",
"name": "Les ANCA nécessitent-ils un suivi régulier ?",
"position": 18,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, un suivi régulier est essentiel pour ajuster le traitement et surveiller l'évolution."
}
},
{
"@type": "Question",
"name": "Y a-t-il des effets secondaires aux traitements ?",
"position": 19,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les traitements peuvent avoir des effets secondaires comme l'infection ou l'ostéoporose."
}
},
{
"@type": "Question",
"name": "Les traitements peuvent-ils guérir les ANCA ?",
"position": 20,
"acceptedAnswer": {
"@type": "Answer",
"text": "Il n'existe pas de cure, mais les traitements peuvent contrôler les symptômes et la progression."
}
},
{
"@type": "Question",
"name": "Quelles sont les complications possibles des ANCA ?",
"position": 21,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les complications incluent des atteintes rénales, pulmonaires et cardiovasculaires."
}
},
{
"@type": "Question",
"name": "Les ANCA peuvent-ils entraîner des infections ?",
"position": 22,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les traitements immunosuppresseurs augmentent le risque d'infections."
}
},
{
"@type": "Question",
"name": "Y a-t-il un risque de cancer associé aux ANCA ?",
"position": 23,
"acceptedAnswer": {
"@type": "Answer",
"text": "Certaines études suggèrent un risque accru de certains cancers chez les patients ANCA."
}
},
{
"@type": "Question",
"name": "Les complications sont-elles réversibles ?",
"position": 24,
"acceptedAnswer": {
"@type": "Answer",
"text": "Certaines complications peuvent être réversibles avec un traitement approprié."
}
},
{
"@type": "Question",
"name": "Comment surveiller les complications des ANCA ?",
"position": 25,
"acceptedAnswer": {
"@type": "Answer",
"text": "Des examens réguliers et des tests sanguins aident à surveiller les complications."
}
},
{
"@type": "Question",
"name": "Quels sont les facteurs de risque des ANCA ?",
"position": 26,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les facteurs incluent des antécédents familiaux, le tabagisme et certaines infections."
}
},
{
"@type": "Question",
"name": "Le sexe influence-t-il le risque d'ANCA ?",
"position": 27,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les femmes sont plus souvent touchées par les maladies associées aux ANCA."
}
},
{
"@type": "Question",
"name": "L'âge joue-t-il un rôle dans le développement des ANCA ?",
"position": 28,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les ANCA apparaissent généralement chez les adultes jeunes à moyens d'âge."
}
},
{
"@type": "Question",
"name": "Certaines professions augmentent-elles le risque d'ANCA ?",
"position": 29,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les professions exposant à des produits chimiques peuvent augmenter le risque."
}
},
{
"@type": "Question",
"name": "Les infections antérieures sont-elles un facteur de risque ?",
"position": 30,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, certaines infections peuvent déclencher la production d'ANCA chez des individus prédisposés."
}
}
]
}
]
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To evaluate the association between health-related quality of life (HRQoL) and mortality in patients with antineutrophil cytoplasmic antibody-associated vasculitis (AAV)....
We searched patients with AAV assessed for HRQoL at initial diagnosis using Short Form 36 (SF-36). Relationships between SF-36 physical component summary (PCS) and mental component summary (MCS) scale...
The median SF-36 PCS and MCS values of the 189 patients were 47.5 and 53.3, respectively, and 21 (11.1%) patients (microscopic polyangiitis [MPA], n=15; granulomatosis with polyangiitis [GPA], n=6) di...
Poor baseline physical functioning associated with premature death in patients with MPA and GPA. HRQoL assessment during initial diagnosis may provide clinical insights for this population....
The life prognosis of elderly patients with myeloperoxidase-anti-neutrophil cytoplasmic antibodies-associated vasculitis (MPO-AAV) has been improved by reducing the corticosteroid or cyclophosphamide ...
Patients with MPO-AAV who reached complete or incomplete remission after induction therapy were prospectively and randomly divided into mizoribine (MZR; n = 25) and control (n = 28) groups. The primar...
Fifty-eight MPO-AAV patients from 16 hospitals in Japan were enrolled. Ten patients relapsed (MZR group, n = 6; control group, n = 4; a nonsignificant between-group difference). Changes in the serum M...
There was no significant difference in the recurrence rate of MPO-AAV between treatment with versus without MZR....
Positive antineutrophil cytoplasmic antibodies (ANCAs) may occur in the setting of interstitial lung disease (ILD), with or without ANCA-associated vasculitis (AAV). We aim to compare the characterist...
We performed a single-center retrospective cohort study from 2018 to 2021. All patients with ILD and ANCA testing were included. Patient characteristics (symptoms, dyspnea scale, and systemic AAV), te...
A total of 265 patients with ILD were included. The mean follow-up duration was 69.3 months, 26 patients (9.8%) were ANCA positive, and 69.2% of those with ANCA-ILD had another autoantibody. AAV occur...
Routine ANCA testing should be considered in patients with ILD. Patients with ANCA-ILD are at risk for AAV. More research is required to better understand and manage patients with ANCA-ILD....
Pediatric antineutrophil cytoplasmic antibody-associated vasculitis (AAV) is a life-threatening systemic vasculitis featured by liability to renal involvement. However, there are few studies on the ri...
Data from 179 AAV children in multiple centers between January 2012 and March 2020 were collected retrospectively. The risk factors and predictive model of end-stage renal disease (ESRD) in AAV were e...
Renal involvement was the most typical manifestation (95.5%), and the crescent was the predominant pathological lesion (84.9%). The estimated glomerular filtration rate (eGFR) was evaluated in 114 pat...
Renal involvement is the most common manifestation of pediatric AAV in China, of which more than half deteriorates into ESRD. The predictive model based on eGFR at renal biopsy and the pGGS may be sta...
This study aims to compare the prognostic values of two histopathological classification, Berden's classification versus renal risk score (RRS) by Brix et al. for predicting renal survival in Chinese ...
The medical records of 225 patients with MPO-AAGN diagnosed in our centre between February 2004 and December 2020 were retrospectively analysed. The predictive model of Berden's classification or RRS ...
After a median follow up of 38.99 months, 32.44% of patients developed end-stage renal disease (ESRD). In the Kaplan-Meier analysis, there were significant differences in renal survival among groups a...
The model based on RRS has better predictive value for renal survival than Berden's classification in aspect of discrimination and clinical decision from 0.5- to 3-year renal survival....
Spontaneous renal hemorrhage (SRH) in ANCA-associated vasculitis (AAV) is rare but fatal. We aimed to characterize clinical manifestations and managements of AAV patients with SRH....
Hospitalized AAV patients were screened from January 2000 to April 2021, at Peking Union Medical College Hospital (PUMCH). Also, a systematic review was based on retrieving all the relevant literature...
In PUMCH, four out of 1640 AAV patients with SRH were included in our study; three had granulomatosis with polyangiitis (GPA) and one had microscopic polyangiitis (MPA). The ratio of men to women was ...
This is the first summary of clinical features and treatments of SRH in AAV. Patients with AAV in early stage and with high disease activity appeared to be more likely to develop SRH. Key Points • Thi...
Vasculitis, or inflammation of blood vessels, is commonly seen with severe acute respiratory syndrome Coronavirus disease 2 (SARS-CoV-2). It is usually triggered by an autoimmune response induced by t...
This study applied the 2022 American College of Rheumatology (ACR)/European Alliance of Associations for Rheumatology (EULAR) criteria for antineutrophil cytoplasmic antibody (ANCA)-associated vasculi...
Among the 232 patients diagnosed with SSc, 105 with signs suggestive of small- or medium-vessel vasculitis, which were defined as the present of interstitial lung disease (ILD), peripheral neuropathy,...
Among the 105 SSc patients, the detection rate of ANCA was 19.0%. When the 2022 ACR/EULAR criteria were applied, the frequency of SSc-AAV-OS was 20.0%, which was much higher than 1.7% reported with pr...
The frequency of SSc-AAV-OS in SSc patients with signs suggestive of small- or medium-vessel vasculitis at diagnosis was 20.0%. Therefore, we suggest that physicians should perform ANCA tests in SSc p...
Antineutrophil cytoplasmic antibody (ANCA)-associated vasculitis (AAV) presents a significant medical challenge, with an annual incidence of 2.4 to 4.1 cases per 100,000 individuals and a prevalence o...
Antineutrophil cytoplasmic antibody (ANCA)-associated vasculitis (AAV) includes granulomatosis with polyangiitis (GPA), microscopic polyangiitis (MPA), and eosinophilic granulomatosis with polyangiiti...
Critical research was performed in the electronic archive (PUBMED, UpToDate, Google Scholar, ResearchGate), supplemented with manual research. We searched in these databases for articles published unt...
The search identified 102 unique search results. After the evaluation, eight articles were selected for further study. The literature reported that capillaroscopy investigations documented non-specifi...
Microvascular nailfold changes, observed in patients affected by vasculitis, may correlate with the outcome of these patients. However, these non-specific abnormalities may help in the diagnosis of va...