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Tétrapyrroles
Tétrapyrroles : Questions médicales fréquentes
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"@type": "Question",
"name": "Comment diagnostiquer une carence en tétrapyrroles ?",
"position": 1,
"acceptedAnswer": {
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"text": "Un diagnostic se fait par des tests sanguins mesurant les niveaux de porphyrines."
}
},
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"@type": "Question",
"name": "Quels examens sont utilisés pour évaluer les tétrapyrroles ?",
"position": 2,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les tests de porphyrines urinaires et sanguines sont couramment utilisés."
}
},
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"@type": "Question",
"name": "Quels symptômes indiquent un déséquilibre des tétrapyrroles ?",
"position": 3,
"acceptedAnswer": {
"@type": "Answer",
"text": "Des douleurs abdominales, des troubles neurologiques et des photosensibilités peuvent survenir."
}
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"@type": "Question",
"name": "Les tests génétiques sont-ils utiles pour les tétrapyrroles ?",
"position": 4,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, ils peuvent identifier des mutations liées aux troubles des tétrapyrroles."
}
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"@type": "Question",
"name": "Quelle est l'importance de l'historique médical dans le diagnostic ?",
"position": 5,
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"@type": "Question",
"name": "Quels sont les symptômes courants des troubles des tétrapyrroles ?",
"position": 6,
"acceptedAnswer": {
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"text": "Les symptômes incluent douleurs abdominales, éruptions cutanées et fatigue."
}
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"@type": "Question",
"name": "Comment les tétrapyrroles affectent-ils le système nerveux ?",
"position": 7,
"acceptedAnswer": {
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"text": "Ils peuvent provoquer des neuropathies, des crises et des troubles mentaux."
}
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"@type": "Question",
"name": "Les troubles digestifs sont-ils liés aux tétrapyrroles ?",
"position": 8,
"acceptedAnswer": {
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"text": "Oui, des douleurs abdominales et des nausées sont fréquentes dans ces troubles."
}
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"@type": "Question",
"name": "La photosensibilité est-elle un symptôme des tétrapyrroles ?",
"position": 9,
"acceptedAnswer": {
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"text": "Oui, la photosensibilité est un symptôme courant, provoquant des éruptions cutanées."
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"@type": "Question",
"name": "Les symptômes varient-ils selon le type de tétrapyrroles ?",
"position": 10,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les symptômes peuvent varier selon le type de porphyrie et sa gravité."
}
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"@type": "Question",
"name": "Comment prévenir les crises liées aux tétrapyrroles ?",
"position": 11,
"acceptedAnswer": {
"@type": "Answer",
"text": "Éviter les déclencheurs connus, comme certains médicaments et l'alcool, aide à prévenir."
}
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"@type": "Question",
"name": "Les tests de dépistage sont-ils recommandés ?",
"position": 12,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, le dépistage peut être utile pour les personnes à risque ou avec des antécédents familiaux."
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"@type": "Question",
"name": "L'éducation des patients est-elle importante ?",
"position": 13,
"acceptedAnswer": {
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"text": "Oui, comprendre la maladie aide les patients à gérer leurs symptômes et à éviter les crises."
}
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"@type": "Question",
"name": "Les vaccinations sont-elles nécessaires pour ces patients ?",
"position": 14,
"acceptedAnswer": {
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"text": "Oui, les vaccinations peuvent prévenir des infections qui aggravent les symptômes."
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"name": "La photothérapie est-elle efficace pour les tétrapyrroles ?",
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"text": "Oui, la photothérapie peut aider à réduire les symptômes de photosensibilité."
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"text": "Ils peuvent être nécessaires en cas d'anémie, mais doivent être prescrits par un médecin."
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"name": "Comment la gestion du stress aide-t-elle les patients ?",
"position": 19,
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"@type": "Question",
"name": "Les changements alimentaires sont-ils bénéfiques ?",
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"text": "Oui, un régime équilibré peut aider à gérer les symptômes et améliorer la santé."
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"text": "Les complications incluent des lésions nerveuses, des problèmes hépatiques et des anémies."
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},
{
"@type": "Question",
"name": "Les troubles psychologiques sont-ils des complications ?",
"position": 22,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des troubles comme l'anxiété et la dépression peuvent survenir chez ces patients."
}
},
{
"@type": "Question",
"name": "Comment les tétrapyrroles affectent-ils le foie ?",
"position": 23,
"acceptedAnswer": {
"@type": "Answer",
"text": "Ils peuvent provoquer des lésions hépatiques, entraînant des douleurs et des dysfonctionnements."
}
},
{
"@type": "Question",
"name": "Les complications cardiovasculaires sont-elles possibles ?",
"position": 24,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des problèmes cardiovasculaires peuvent survenir en raison de l'anémie et du stress."
}
},
{
"@type": "Question",
"name": "Les infections sont-elles une complication fréquente ?",
"position": 25,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les infections peuvent survenir, surtout si le système immunitaire est affaibli."
}
},
{
"@type": "Question",
"name": "Quels sont les facteurs de risque des troubles des tétrapyrroles ?",
"position": 26,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les antécédents familiaux, l'exposition à des toxines et certains médicaments augmentent le risque."
}
},
{
"@type": "Question",
"name": "L'alimentation joue-t-elle un rôle dans les tétrapyrroles ?",
"position": 27,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, une alimentation pauvre en nutriments essentiels peut augmenter le risque de troubles."
}
},
{
"@type": "Question",
"name": "Les maladies hépatiques sont-elles un facteur de risque ?",
"position": 28,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les maladies hépatiques préexistantes peuvent exacerber les troubles des tétrapyrroles."
}
},
{
"@type": "Question",
"name": "Le stress peut-il aggraver les symptômes ?",
"position": 29,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, le stress est un facteur déclenchant connu pour les crises liées aux tétrapyrroles."
}
},
{
"@type": "Question",
"name": "Les infections antérieures influencent-elles le risque ?",
"position": 30,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, certaines infections peuvent déclencher ou aggraver les troubles des tétrapyrroles."
}
}
]
}
]
}
Upper limb dysfunction after stroke seriously affects quality of life. Bilateral training has proven helpful in recovery of upper limb motor function in these patients. However, studies evaluating the...
24 stroke patients with hemiplegia were randomly divided into a conventional training (CT, n = 12) group or a bilateral upper limb robot-assisted training (BRT, n = 12) group. All patients received 60...
Significant (p < 0.05) within-group differences were found in FMA-UE and MBI scores for both groups after treatment. A between-group comparison indicated the MBI score of the BRT group was significant...
BRT outperformed CT in improving ADL in stroke patients within three months, and BRT facilitates the recovery of upper limb function by enhancing functional connectivity of the bilateral cerebral hemi...
Retromuscular sublay (RMS) technique for repair of ventral hernias has gained popularity due to lower risk of recurrence and wound complications. Robotic approaches to RMS have been shown to decrease ...
A retrospective review of elective robotic and open RMS repairs in the ACHQC database was performed. Patients deemed to be high-risk for wound complications were included: adult patients with BMI grea...
A total of 917 patients met inclusion criteria. After propensity score matching, 211 patients matched for each approach. There was no difference in overall SSO (18% for Open vs 23% for Robotic, p = 0....
In this analysis, a robotic approach was associated with decreased rates of SSI and SSOPI in obese patients who were either current smokers or diabetics. In effort to reduce wound morbidity and the as...
This paper formulates an innovative model-free self-organizing weight adaptation that strengthens the robustness of a Linear Quadratic Regulator (LQR) for inverted pendulum-like mechatronic systems ag...
More recently, soft actuators have evoked great interest in the next generation of soft robots. Despite significant progress, the majority of current soft actuators suffer from the lack of real-time s...
Renal cell carcinoma (RCC) is an adenocarcinoma of the renal cortex. Radical nephrectomy remains the standard of care for managing massive renal tumours. Robotic-assisted radical nephrectomy is an inc...
To investigate preoperative patient factors that may predict the occurrence of perioperative complications following robot-assisted radical cystectomy at a single center in Japan....
From 2013 to 2022, 103 patients underwent RARC at our institution. Complications within 90 days after surgery were assessed using the Clavien-Dindo classification. Preoperative characteristics and sur...
Overall, 27% of patients (27/103) experienced grade 3 or higher complications. The cohort that developed complications ≥grade 3 exhibited significantly higher Charlson comorbidity index (p = 0.046) an...
Our results suggest that the Charlson comorbidity index and preoperative estimated glomerular filtration rate may be predictors of perioperative complications. It is important to evaluate the patient'...
Minimally invasive liver resections (MILR) offer potential benefits such as reduced blood loss and morbidity compared with open liver resections. Several studies have suggested that the impact of cirr...
A total of 2534 patients undergoing minimally invasive major hepatectomies (MIMH) for primary malignancies across 58 centers worldwide were retrospectively reviewed. Propensity score (PSM) and coarsen...
A total of 1353 patients (53%) had no cirrhosis, 1065 (42%) had Child-Pugh A and 116 (4%) had Child-Pugh B cirrhosis. Matched comparison between non-cirrhotics vs Child-Pugh A cirrhosis demonstrated c...
The presence and severity of cirrhosis affected the difficulty and impacted the outcomes of MIMH, resulting in higher blood transfusion rates, increased postoperative morbidity, and longer hospitaliza...
The surgical resection of rectal carcinoma is associated with a high risk of permanent stoma rate. Primary anastomosis rate is suggested to be higher in robot-assisted and transanal total mesorectal e...
Patients undergoing total mesorectal excision for MRI-defined rectal cancer between 2015 and 2017 in 11 centers highly experienced in laparoscopic, robot-assisted or transanal total mesorectal excisio...
In total, 1198 patients were included. Permanent stoma rate after low anterior resection (with anastomosis or with an end colostomy) was 40.1% in patients undergoing laparoscopic surgery, 21.3% in pat...
The robot-assisted and transanal techniques are associated with a lower permanent stoma rate in patients who underwent a low anterior resection....
Children with cerebral palsy (CP) classified as gross motor function classification system (GMFCS) levels III-IV demonstrate impaired sitting and reaching control abilities that hamper their overall f...
We will recruit 82 participants with CP, GMFCS III-IV, and aged 6-17 years. Randomisation using concealed allocation to either the TruST-support or static trunk-support intervention will be conducted ...
The study was approved by the Columbia University Institutional Review Board (AAAS7804). This study is funded by the National Institutes of Health (1R01HD101903-01) and is registered at clinicaltrials...
NCT04897347; clinicaltrials.gov....
Robotic-assisted minimally invasive esophagectomy (RAMIE) was first introduced in 2003 and has since then shown to significantly improve the postoperative course. Previous studies have shown that a st...
All patients undergoing RAMIE performed by two experienced surgeons for esophageal cancer since the introduction of the robotic technique in 2017 was included in this analysis. Intraoperative outcomes...
From 06/2017 to 03/2022, a total of 154 patients underwent RAMIE at our facility and were included in the analysis. An advancement in performance level was observed for total operating time after 70 c...
Our data and analysis showed the progression from proficient to expert performance levels during the implementation of RAMIE at a European high-volume center. Further analysis of surgeons, especially ...