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Tétrapyrroles
Tétrapyrroles : Questions médicales fréquentes
Termes MeSH sélectionnés :
Ventricular Function, Left
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"@type": "Question",
"name": "Comment diagnostiquer une carence en tétrapyrroles ?",
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"text": "Un diagnostic se fait par des tests sanguins mesurant les niveaux de porphyrines."
}
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"@type": "Question",
"name": "Quels examens sont utilisés pour évaluer les tétrapyrroles ?",
"position": 2,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les tests de porphyrines urinaires et sanguines sont couramment utilisés."
}
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"@type": "Question",
"name": "Quels symptômes indiquent un déséquilibre des tétrapyrroles ?",
"position": 3,
"acceptedAnswer": {
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"text": "Des douleurs abdominales, des troubles neurologiques et des photosensibilités peuvent survenir."
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"@type": "Question",
"name": "Les tests génétiques sont-ils utiles pour les tétrapyrroles ?",
"position": 4,
"acceptedAnswer": {
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"text": "Oui, ils peuvent identifier des mutations liées aux troubles des tétrapyrroles."
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"@type": "Question",
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"@type": "Question",
"name": "Quels sont les symptômes courants des troubles des tétrapyrroles ?",
"position": 6,
"acceptedAnswer": {
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"text": "Les symptômes incluent douleurs abdominales, éruptions cutanées et fatigue."
}
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"name": "Comment les tétrapyrroles affectent-ils le système nerveux ?",
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"text": "Ils peuvent provoquer des neuropathies, des crises et des troubles mentaux."
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"name": "Les troubles digestifs sont-ils liés aux tétrapyrroles ?",
"position": 8,
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"text": "Oui, des douleurs abdominales et des nausées sont fréquentes dans ces troubles."
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"name": "La photosensibilité est-elle un symptôme des tétrapyrroles ?",
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"text": "Oui, la photosensibilité est un symptôme courant, provoquant des éruptions cutanées."
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"name": "Les symptômes varient-ils selon le type de tétrapyrroles ?",
"position": 10,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les symptômes peuvent varier selon le type de porphyrie et sa gravité."
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"@type": "Question",
"name": "Comment prévenir les crises liées aux tétrapyrroles ?",
"position": 11,
"acceptedAnswer": {
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"text": "Éviter les déclencheurs connus, comme certains médicaments et l'alcool, aide à prévenir."
}
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"@type": "Question",
"name": "Les tests de dépistage sont-ils recommandés ?",
"position": 12,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, le dépistage peut être utile pour les personnes à risque ou avec des antécédents familiaux."
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"@type": "Question",
"name": "L'éducation des patients est-elle importante ?",
"position": 13,
"acceptedAnswer": {
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"text": "Oui, comprendre la maladie aide les patients à gérer leurs symptômes et à éviter les crises."
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"@type": "Question",
"name": "Les vaccinations sont-elles nécessaires pour ces patients ?",
"position": 14,
"acceptedAnswer": {
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"text": "Oui, les vaccinations peuvent prévenir des infections qui aggravent les symptômes."
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"name": "La photothérapie est-elle efficace pour les tétrapyrroles ?",
"position": 17,
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"text": "Oui, la photothérapie peut aider à réduire les symptômes de photosensibilité."
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"name": "Les suppléments de fer sont-ils recommandés ?",
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"text": "Ils peuvent être nécessaires en cas d'anémie, mais doivent être prescrits par un médecin."
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"@type": "Question",
"name": "Comment la gestion du stress aide-t-elle les patients ?",
"position": 19,
"acceptedAnswer": {
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"@type": "Question",
"name": "Les changements alimentaires sont-ils bénéfiques ?",
"position": 20,
"acceptedAnswer": {
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"text": "Oui, un régime équilibré peut aider à gérer les symptômes et améliorer la santé."
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"name": "Quelles sont les complications possibles des tétrapyrroles ?",
"position": 21,
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"text": "Les complications incluent des lésions nerveuses, des problèmes hépatiques et des anémies."
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"@type": "Question",
"name": "Les troubles psychologiques sont-ils des complications ?",
"position": 22,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des troubles comme l'anxiété et la dépression peuvent survenir chez ces patients."
}
},
{
"@type": "Question",
"name": "Comment les tétrapyrroles affectent-ils le foie ?",
"position": 23,
"acceptedAnswer": {
"@type": "Answer",
"text": "Ils peuvent provoquer des lésions hépatiques, entraînant des douleurs et des dysfonctionnements."
}
},
{
"@type": "Question",
"name": "Les complications cardiovasculaires sont-elles possibles ?",
"position": 24,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des problèmes cardiovasculaires peuvent survenir en raison de l'anémie et du stress."
}
},
{
"@type": "Question",
"name": "Les infections sont-elles une complication fréquente ?",
"position": 25,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les infections peuvent survenir, surtout si le système immunitaire est affaibli."
}
},
{
"@type": "Question",
"name": "Quels sont les facteurs de risque des troubles des tétrapyrroles ?",
"position": 26,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les antécédents familiaux, l'exposition à des toxines et certains médicaments augmentent le risque."
}
},
{
"@type": "Question",
"name": "L'alimentation joue-t-elle un rôle dans les tétrapyrroles ?",
"position": 27,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, une alimentation pauvre en nutriments essentiels peut augmenter le risque de troubles."
}
},
{
"@type": "Question",
"name": "Les maladies hépatiques sont-elles un facteur de risque ?",
"position": 28,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les maladies hépatiques préexistantes peuvent exacerber les troubles des tétrapyrroles."
}
},
{
"@type": "Question",
"name": "Le stress peut-il aggraver les symptômes ?",
"position": 29,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, le stress est un facteur déclenchant connu pour les crises liées aux tétrapyrroles."
}
},
{
"@type": "Question",
"name": "Les infections antérieures influencent-elles le risque ?",
"position": 30,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, certaines infections peuvent déclencher ou aggraver les troubles des tétrapyrroles."
}
}
]
}
]
}
The Simpson's method is the standard technique to determine left ventricular (LV) ejection fraction (EF) on echocardiography. The large inter-observer variability of measuring LVEF is well documented ...
Tortuosity in the coronary arteries is a very common entity encountered during angiography. The effect of coronary artery tortuosity (CAT) on the myocardium has not been completely investigated. The a...
Seventy-five patients with CAT and 80 age- and gender-matched controls who proved to have normal coronary angiograms (CAG) were enrolled into the study. Following CAG, the 2D images were obtained firs...
The LAS-r, LAS-active, and LV-GLS were significantly depressed in the CAT (+) group (p < .001, p < .001, p = .012, respectively). The multivariate regression models demonstrated that LAS-r (p < .001),...
The current study is the first to focus on the assessing both LA and LV myocardial dynamics in CAT (+) patients by strain echocardiography. The results of our study support the patients with CAT may h...
Background and Objectives: Increasing reluctance to perform surgical mitral valve repair or replacement particularly in high-risk patients with poor left-ventricular function is trending. These patien...
The 2016 American Society of Echocardiography guidelines have been widely used to assess left ventricular diastolic function. However, limitations are present in the current classification system. The...
Baseline demographics, heart failure hospitalization, and all-cause mortality data were obtained for all adult patients who underwent transthoracic echocardiography at Mayo Clinic Rochester in 2015. P...
Among 24,414 patients (mean age, 63.6 ± 16.2 years), all-cause mortality occurred in 4,612 patients (18.9%) during a median follow-up period of 3.1 years. The algorithm determined three clusters with ...
Unsupervised machine learning identified physiologically and prognostically distinct clusters on the basis of nine diastolic function Doppler variables. The clusters can be potentially applied in echo...
Type 2 diabetes (T2D) and obesity induce left ventricular (LV) dysfunction. The underlying pathophysiological mechanisms remain unclear, but myocardial triglyceride content (MTGC) could be involved....
This study aimed to determine which clinical and biological factors are associated with increased MTGC and to establish whether MTGC is associated with early changes in LV function....
A retrospective study was conducted using five previous prospective cohorts, leading to 338 subjects studied, including 208 well-phenotyped healthy volunteers and 130 subjects living with T2D and/or o...
MTGC content increased with age, body mass index (BMI), waist circumference, T2D, obesity, hypertension, and dyslipidemia, but the only independent correlate found in multivariate analysis was BMI (p=...
Predicting MTGC remains a challenge in routine clinical practice, as only BMI independently correlates with increased MTGC. MTGC may play a role in LV dysfunction but does not appear to be involved in...
Tachycardia-induced cardiomyopathy (TCM) represents a partially reversible type of cardiomyopathy (CM) that is often underdiagnosed and cardiac chamber remodelling in TCM remains incompletely understo...
We identified patients with reduced ejection fraction (≤50%) and/or atrial fibrillation or flutter with a left ventricular ejection fraction that improved from baseline (≥15% in left ventricular eject...
TCM patients have a specific pattern of functional recovery with persistent remodelling of the left atria and left ventricle. Several echocardiographic parameters might help identify TCM before treatm...
Cardiovascular mortality is significantly higher in patients with primary hyperparathyroidism (PHPT) compared to the general population. The role of the renin-angiotensin-aldosterone system (RAAS) as ...
In 45 consecutive, hypercalcemic PHPT patients (91% female, 20 normotensive, mean age 54.6 ± 14.6), laboratory examinations, and 24 h ambulatory blood pressure monitoring (ABPM) were performed before,...
Both in patients with normotension (NT) and HT, lower calcemia and parathyroid hormone (PTH) as well as higher phosphatemia were observed on follow-up, while B-type natriuretic peptide, aldosterone, p...
PTX was shown to significantly reduce BP, LV hypertrophy and diastolic dysfunction parameters in PHPT patients with HT, and improve systolic function in all PHPT patients....
Mitral regurgitation (MR) burdens the left and right ventricles with a volume or pressure overload that leads to a series of compensatory adaptations that eventually lead to ventricular dysfunction, a...
Evaluate whether rheumatic etiology is associated with ventricular dysfunction in patients with chronic MR....
The study population comprised patients aged 18 years or older included in the registry who had echocardiography performed at the National Cardiovascular Center Harapan Kita in Indonesia during the st...
The current study included 1,130 patients with significant isolated degenerative MR and 276 patients with rheumatic MR. Patients with rheumatic MR were younger and had a higher prevalence of atrial fi...
Rheumatic etiology was independently associated with more impaired left ventricular function; however, rheumatic etiology was not associated with reduced right ventricular systolic function in a patie...
Background Diabetes and hypertension have been associated with adverse left ventricular (LV) remodeling. While they often occur concurrently, their individual effects are understudied. We aimed to ass...
Aldosterone has hypertrophic and profibrotic effects on the heart. This study aims to determine the relationship between serum aldosterone concentration (SAC) and aldosterone-to-renin ratio (ARR) with...